2026 ICD-10-CM Diagnosis Code Q82.0Hereditary lymphedema

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q82

ICD-10-CM Q82.0
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q82.0 is a billable ICD-10-CM diagnosis code for hereditary lymphedema. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 606 through 607. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q82.0
Billable Status
Yes — Valid for Submission
Code Describes
Hereditary lymphedema
Short Description
Hereditary lymphedema
Same as the full description in the CMS dataset.
Parent Code
Q82
Other congenital malformations of skin

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ82Other congenital malformations of skin
This CodeQ82.0Hereditary lymphedema

Present on Admission (POA)Billing

Q82.0 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Accessory eyelid
  • Anhidrotic ectodermal dysplasia, immunodeficiency, osteopetrosis, lymphedema syndrome
  • CELSR1-related late-onset primary lymphedema
  • Cerebral arteriovenous malformation
  • Choanal atresia
  • Congenital cutaneous lymphangiectasia
  • Congenital distichiasis
  • Congenital elephantiasis
  • Congenital lymphangiectasia
  • Congenital lymphangiectasia with chylous reflux
  • Congenital malformation of lymphatic vessel of skin
  • Congenital primary lymphedema of Gordon
  • Constricting band of extremity
  • Constriction ring of lower limb with lymphedema
  • Constriction ring of upper limb with lymphedema
  • Constriction ring syndrome
  • Constriction ring syndrome of lower limb
  • Constriction ring syndrome of upper limb
  • Distichiasis
  • Distichiasis-lymphedema syndrome
  • Ectopic cilia of eyelid
  • Edema of foot
  • EPHB4-related lymphatic-related hydrops fetalis
  • GJC2-related late-onset primary lymphedema
  • Hereditary disorder of lymphatic system
  • Hereditary lymphedema
  • Hereditary lymphedema and yellow nails
  • Hereditary lymphedema type I
  • Hereditary lymphedema type II
  • Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome
  • Lymphedema and cerebral arteriovenous anomaly syndrome
  • Lymphedema of lower extremity
  • Lymphedema of upper limb
  • Lymphedema, posterior choanal atresia syndrome
  • Macrothrombocytopenia, lymphedema, developmental delay, facial dysmorphism, camptodactyly syndrome
  • Megakaryocytic thrombocytopenia
  • Microcephalus, lymphedema, chorioretinopathy syndrome
  • PIEZO1-related generalized lymphatic dysplasia with non-immune hydrops fetalis
  • Primary lymphedema tardum
  • Progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like syndrome
  • Warts, immunodeficiency, lymphedema, anogenital dysplasia syndrome
  • Yellow nails

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Disease, diseased
      • Meige's (chronic hereditary edema)
    • Disease, diseased
      • Milroy's (chronic hereditary edema)
    • Disease, diseased
      • Nonne-Milroy-Meige (chronic hereditary edema)
    • Edema, edematous(infectious) (pitting) (toxic)
      • chronic hereditary
    • Edema, edematous(infectious) (pitting) (toxic)
      • familial, hereditary
    • Edema, edematous(infectious) (pitting) (toxic)
      • hereditary
    • Edema, edematous(infectious) (pitting) (toxic)
      • legs
        • hereditary
    • Edema, edematous(infectious) (pitting) (toxic)
      • Milroy's
    • Elephantiasis(nonfilarial)
      • congenital (any site) (hereditary)
    • Lymphedema(acquired)
      • congenital
    • Lymphedema(acquired)
      • hereditary (chronic) (idiopathic)
    • Meige-Milroy disease(chronic hereditary edema)
    • Meige's syndrome
    • Milroy's disease(chronic hereditary edema)
    • Nonne-Milroy syndrome
    • Pseudoelephantiasis neuroarthritica
    • Syndrome
      • Nonne-Milroy-Meige
    • Trophedema(congenital) (hereditary)
    • Tropholymphedema

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Choanal Atresia

    a congenital abnormality that is characterized by a blocked choanae, the opening between the nose and the nasopharynx. blockage can be unilateral or bilateral; bony or membranous.

Patient EducationClinical

Skin Conditions

Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:

The full article covers:

  • What does your skin do?
  • What problems and conditions can affect your skin?
  • How can I keep my skin healthy?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q82.0 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
757.0 Hereditary edema of legs
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q82.0Overview

Is Q82.0 (Other congenital malformations of skin) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report hereditary lymphedema on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q82.0 group to?

When hereditary lymphedema is the principal diagnosis on an inpatient stay, it groups to MS-DRG 606, 607, with relative weights from 0.9064 to 1.5132 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q82.0 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for hereditary lymphedema on inpatient claims.

What is the ICD-9 equivalent of Q82.0?

Under the General Equivalence Mappings, hereditary lymphedema converts to ICD-9-CM 757.0 (hereditary edema of legs). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.