2027 ICD-10-CM Diagnosis Code Q82.0Hereditary lymphedema
ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q82
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q82.0 is a billable ICD-10-CM diagnosis code for hereditary lymphedema. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 606 through 607. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q82.0 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations (Q80-Q89).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Accessory eyelid
- Anhidrotic ectodermal dysplasia, immunodeficiency, osteopetrosis, lymphedema syndrome
- CELSR1-related late-onset primary lymphedema
- Cerebral arteriovenous malformation
- Choanal atresia
- Congenital cutaneous lymphangiectasia
- Congenital distichiasis
- Congenital elephantiasis
- Congenital lymphangiectasia
- Congenital lymphangiectasia with chylous reflux
- Congenital malformation of lymphatic vessel of skin
- Congenital primary lymphedema of Gordon
- Constricting band of extremity
- Constriction ring of lower limb with lymphedema
- Constriction ring of upper limb with lymphedema
- Constriction ring syndrome
- Constriction ring syndrome of lower limb
- Constriction ring syndrome of upper limb
- Distichiasis
- Distichiasis-lymphedema syndrome
- Ectopic cilia of eyelid
- Edema of foot
- EPHB4-related lymphatic-related hydrops fetalis
- GJC2-related late-onset primary lymphedema
- Hereditary disorder of lymphatic system
- Hereditary lymphedema
- Hereditary lymphedema and yellow nails
- Hereditary lymphedema type I
- Hereditary lymphedema type II
- Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome
- Lymphedema and cerebral arteriovenous anomaly syndrome
- Lymphedema of lower extremity
- Lymphedema of upper limb
- Lymphedema, posterior choanal atresia syndrome
- Macrothrombocytopenia, lymphedema, developmental delay, facial dysmorphism, camptodactyly syndrome
- Megakaryocytic thrombocytopenia
- Microcephalus, lymphedema, chorioretinopathy syndrome
- PIEZO1-related generalized lymphatic dysplasia with non-immune hydrops fetalis
- Primary lymphedema tardum
- Progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like syndrome
- Warts, immunodeficiency, lymphedema, anogenital dysplasia syndrome
- Yellow nails
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q82.0: its own notes plus those printed at Q82 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q82.0, its category, or a range that includes it.
Excludes1 3
These codes carry an Excludes1 note naming Q82.0: they are not reported together with it, unless the two conditions are unrelated.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Disease, diseased See Also: Syndrome;
Edema, edematous (infectious) (pitting) (toxic) R60.9
chronic hereditary Q82.0
familial, hereditary Q82.0
hereditary Q82.0
hereditary Q82.0
Milroy's Q82.0
Lymphedema (acquired) See Also: Elephantiasis;
congenital Q82.0
Meige's syndrome Q82.0
Nonne-Milroy syndrome Q82.0
Syndrome See Also: Disease;
Nonne-Milroy-Meige Q82.0
Tropholymphedema Q82.0
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Meige Syndrome
a syndrome characterized by orofacial dystonia; including blepharospasm; forceful jaw opening; lip retraction; platysma muscle spasm; and tongue protrusion. it primarily affects older adults, with an incidence peak in the seventh decade of life. (from adams et al., principles of neurology, 6th ed, p108)
Patient EducationClinical
Skin Conditions
Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:
The full article covers:
- What does your skin do?
- What problems and conditions can affect your skin?
- How can I keep my skin healthy?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q82.0 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q82.0Overview
What is the ICD-10 code for hereditary lymphedema?
The ICD-10-CM code for hereditary lymphedema is Q82.0 (sometimes written as Q820). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q82.0 (Other congenital malformations of skin) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report hereditary lymphedema on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q82.0 group to?
When hereditary lymphedema is the principal diagnosis on an inpatient stay, it groups to MS-DRG 607, 606, with relative weights from 0.8772 to 1.5721 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q82.0 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for hereditary lymphedema on inpatient claims. The code appears in the Other congenital malformations (Q80-Q89) range of the CMS exempt list.
Can Q82.0 be reported with E83.2?
Not as a rule. The Excludes1 note at Q82, which applies to Q82.0, lists "acrodermatitis enteropathica (E83.2)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
