2024 ICD-10-CM Diagnosis Code Q82.3
The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:
- Incontinentia pigmenti achromians syndrome
- Incontinentia pigmenti syndrome
Clinical Category is Other specified and unspecified congenital anomalies
- CCSR Category Code: MAL010
- Inpatient Default CCSR: Y - Yes, default inpatient assignment for principal diagnosis or first-listed diagnosis.
- Outpatient Default CCSR: Y - Yes, default outpatient assignment for principal diagnosis or first-listed diagnosis.
Incontinentia Pigmentia genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. hyperpigmentation is bizarre and irregular. sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.
Pigmentation Disordersdiseases affecting pigmentation, including skin pigmentation.
Index to Diseases and Injuries References
The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).
- - Bloch-Sulzberger disease or syndrome - Q82.3
- - Incontinentia pigmenti - Q82.3
Present on Admission (POA)
CMS POA Indicator Options and Definitions
|Reason for Code
|CMS will pay the CC/MCC DRG?
|Diagnosis was present at time of inpatient admission.
|Diagnosis was not present at time of inpatient admission.
|Documentation insufficient to determine if the condition was present at the time of inpatient admission.
|Clinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.
|Unreported/Not used - Exempt from POA reporting.
What does your skin do?
Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:
- Holds body fluids in, which helps prevent you from getting dehydrated
- Keeps out harmful germs, which helps prevent infections
- Helps you feel things like heat, cold, and pain
- Helps control your body temperature
- Makes vitamin D when the sun shines on it
- Shields your body against heat and light
What problems and conditions can affect your skin?
There are many different problems and conditions which can affect your skin. Some of them can cause uncomfortable symptoms, such as itching, burning, redness, and rashes. They might also affect your appearance. Some of the more common skin conditions include:
- Acne, which causes pimples when hair follicles under your skin get clogged up
- Cuts and scrapes
- Dandruff, flaking of the skin on your scalp (the top of your head)
- Eczema (atopic dermatitis), which causes inflammation, redness, and irritation of the skin
- Hives, which are red and sometimes itchy bumps on your skin
- Insect bites
- Psoriasis, which causes itchy, scaly red patches
- Skin cancer
- Skin infections
How can I keep my skin healthy?
Since your skin protects your body in many ways, it's important to try to keep your skin healthy. For example, you can:
- Wear the right protective equipment, like gloves, long sleeves, knee and elbow pads, or helmets to protect against cuts, bumps and scrapes.
- If you do get a cut or scrape, clean it right away with soap and warm water. Put on a bandage to protect it while it heals.
- When you are spending time outdoors, wear long sleeves and pants and use insect repellant to prevent insect bites.
- Prevent sunburn by covering up and using sunscreen when outdoors.
- Wash your hands often with soap and water.
- When you take a shower or bath, use warm (not hot) water. Use mild cleansers and wash gently (don't scrub).
- Use moisturizers, like lotions, creams, or ointments, to prevent dry skin.
NIH: National Institute of Arthritis and Musculoskeletal and Skin Diseases
[Learn More in MedlinePlus]
Incontinentia pigmenti is a condition that can affect many body systems, particularly the skin. This condition occurs much more often in females than in males.
Incontinentia pigmenti is characterized by skin abnormalities that typically evolve throughout childhood and young adulthood. Many affected infants have a blistering rash at birth and in early infancy. Though this blistering heals spontaneously, it can recur during illnesses with high fever. This blistering stage is followed by the development of wart-like (verrucous) lesions that also heal spontaneously. The blisters and wart-like lesions primarily occur on the arms and legs.
In infancy and early childhood, the skin develops grey or brown patches (hyperpigmentation) that occur in a swirled pattern. These patches, which can occur anywhere on the body, fade with time. Adults with incontinentia pigmenti usually have lines of unusually light-colored skin (hypopigmentation) on their arms and legs. These markings follow the paths along which cells migrate as the skin develops before birth (called the lines of Blaschko).
Individuals with incontinentia pigmenti are at risk of stroke and vision loss, especially within the first year of life. These risks are due to abnormalities in blood vessels in the brain and in the light-sensitive tissue that lines the back of the eye (retina). Affected individuals at risk often have developmental delays, intellectual disabilities, seizures, or other neurological problems. In the absence of stroke or another brain abnormality, most people with incontinentia pigmenti have normal intelligence.
Other signs and symptoms of incontinentia pigmenti can include hair loss (alopecia) on the scalp and other parts of the body, dental abnormalities (such as small teeth or few teeth), and lined or pitted fingernails and toenails. The features of incontinentia pigmenti may be mild or gone by the time affected individuals reach adulthood.
[Learn More in MedlinePlus]
- FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
- FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
- FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
- FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
- FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
- FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
- FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
- FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
- FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.
 Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.