ICD-10-CM Code Q81.8

Other epidermolysis bullosa

Version 2020 Billable Code POA Exempt

Valid for Submission

Q81.8 is a billable code used to specify a medical diagnosis of other epidermolysis bullosa. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code Q81.8 might also be used to specify conditions or terms like abnormal granulation tissue, aplasia cutis congenita in association with epidermolysis bullosa , cicatricial junctional epidermolysis bullosa, congenital junctional epidermolysis bullosa, congenital junctional epidermolysis bullosa-pyloric atresia syndrome, epidermolysis bullosa pruriginosa, etc The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Short Description:Other epidermolysis bullosa
Long Description:Other epidermolysis bullosa

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code Q81.8 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Abnormal granulation tissue
  • Aplasia cutis congenita in association with epidermolysis bullosa
  • Cicatricial junctional epidermolysis bullosa
  • Congenital junctional epidermolysis bullosa
  • Congenital junctional epidermolysis bullosa-pyloric atresia syndrome
  • Epidermolysis bullosa pruriginosa
  • Gastric atresia
  • Generalized dystrophic epidermolysis bullosa
  • Generalized junctional epidermolysis bullosa
  • Inverse junctional epidermolysis bullosa
  • Junctional epidermolysis bullosa
  • Junctional epidermolysis bullosa mitis
  • Junctional epidermolysis bullosa non-Herlitz type
  • Laryngo-onycho-cutaneous syndrome
  • Late-onset junctional epidermolysis bullosa
  • Late-onset localized junctional epidermolysis bullosa, intellectual disability syndrome
  • Localized junctional epidermolysis bullosa
  • Progressive junctional epidermolysis bullosa
  • Pyloric atresia
  • Weber-Cockayne syndrome

Clinical Information

  • EPIDERMOLYSIS BULLOSA-. group of genetically determined disorders characterized by the blistering of skin and mucosae. there are four major forms: acquired simple junctional and dystrophic. each of the latter three has several varieties.
  • EPIDERMOLYSIS BULLOSA ACQUISITA-. form of epidermolysis bullosa characterized by trauma induced subepidermal blistering with no family history of the disease. direct immunofluorescence shows immunoglobulin g deposited at the dermo epidermal junction.
  • EPIDERMOLYSIS BULLOSA DYSTROPHICA-. form of epidermolysis bullosa characterized by atrophy of blistered areas severe scarring and nail changes. it is most often present at birth or in early infancy and occurs in both autosomal dominant and recessive forms. all forms of dystrophic epidermolysis bullosa result from mutations in collagen type vii a major component fibrils of basement membrane and epidermis.
  • EPIDERMOLYSIS BULLOSA JUNCTIONAL-. form of epidermolysis bullosa having onset at birth or during the neonatal period and transmitted through autosomal recessive inheritance. it is characterized by generalized blister formation extensive denudation and separation and cleavage of the basal cell plasma membranes from the basement membrane.
  • EPIDERMOLYSIS BULLOSA SIMPLEX-. a form of epidermolysis bullosa characterized by serous bullae that heal without scarring. mutations in the genes that encode keratin 5 and keratin 14 have been associated with several subtypes of epidermolysis bullosa simplex.

Diagnostic Related Groups

The ICD-10 code Q81.8 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.


Present on Admission (POA)

Q81.8 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here .

CMS POA Indicator Options and Definitions
POA Indicator CodePOA Reason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q81.8 to ICD-9

  • 757.39 - Skin anomaly NEC (Approximate Flag)

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Epidermolysis bullosa (Q81)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Skin Conditions

Your skin is your body's largest organ. It covers and protects your body. Your skin

  • Holds body fluids in, preventing dehydration
  • Keeps harmful microbes out, preventing infections
  • Helps you feel things like heat, cold, and pain
  • Keeps your body temperature even
  • Makes vitamin D when the sun shines on it

Anything that irritates, clogs, or inflames your skin can cause symptoms such as redness, swelling, burning, and itching. Allergies, irritants, your genetic makeup, and certain diseases and immune system problems can cause rashes, hives, and other skin conditions. Many skin problems, such as acne, also affect your appearance.

NIH: National Institute of Arthritis and Musculoskeletal and Skin Diseases

[Learn More]

Junctional epidermolysis bullosa Junctional epidermolysis bullosa (JEB) is a major form of epidermolysis bullosa, a group of genetic conditions that cause the skin to be very fragile and to blister easily. Blisters and areas of skin loss (erosions) form in response to minor injury or friction, such as rubbing or scratching. Researchers classify junctional epidermolysis bullosa into two main types: JEB generalized severe (formerly known as Herlitz JEB) and JEB generalized intermediate (formerly known as non-Herlitz JEB). Although the types differ in severity, their features overlap significantly, and they can be caused by mutations in the same genes.JEB generalized severe is the more serious form of the condition. From birth or early infancy, affected individuals have blistering over large regions of the body. Blistering also affects the mucous membranes, such as the moist lining of the mouth and digestive tract, which can make it difficult to eat and digest food. As a result, many affected children are undernourished and grow slowly. The extensive blistering leads to scarring and the formation of red, bumpy patches called granulation tissue. Granulation tissue bleeds easily and profusely, making affected infants susceptible to serious infections and loss of necessary proteins, minerals, and fluids. Additionally, a buildup of granulation tissue in the airway can lead to a weak, hoarse cry and difficulty breathing.Other complications of JEB generalized severe can include fusion of the fingers and toes, abnormalities of the fingernails and toenails, joint deformities (contractures) that limit movement, hair loss (alopecia), and thinning of the protective outer layer (enamel) of the teeth. Because the signs and symptoms of JEB generalized severe are so serious, infants with this condition usually do not survive beyond the first year of life.The milder form of junctional epidermolysis bullosa is called JEB generalized intermediate. The blistering associated with JEB generalized intermediate may be limited to the hands, feet, knees, and elbows, and it often improves after the newborn period. Other characteristic features of this form of the condition include hair loss, abnormal fingernails and toenails, and irregular tooth enamel. Most affected individuals do not have extensive scarring or granulation tissue formation, so breathing difficulties and other severe complications are rare. JEB generalized intermediate is typically associated with a normal lifespan.
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