2024 ICD-10-CM Diagnosis Code I89.0

Lymphedema, not elsewhere classified

ICD-10-CM Code:
ICD-10 Code for:
Lymphedema, not elsewhere classified
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator: [1]
Code Navigator:

Code Classification

  • Diseases of the circulatory system
    • Diseases of veins, lymphatic vessels and lymph nodes, not elsewhere classified
      • Other noninfective disorders of lymphatic vessels and lymph nodes

I89.0 is a billable diagnosis code used to specify a medical diagnosis of lymphedema, not elsewhere classified. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Acquired cutaneous lymphangiectasia
  • Acquired lymphangiectasia
  • Acquired lymphangiectasia with chylous reflux
  • Acquired lymphedema of lower extremity
  • Bilateral lower limb edema
  • Bilateral upper limb edema
  • Cholestasis in newborn
  • Cholestasis-edema syndrome, Norwegian type
  • Chronic acquired lymphedema
  • Chronic acquired lymphedema
  • Chronic disease of lymphatic vessels
  • Chronic disease of lymphatic vessels
  • Congenital lymphangiectasia
  • Dependent lymphedema
  • Dependent lymphedema
  • Dependent lymphedema due to impaired mobility
  • Edema of left lower limb
  • Edema of left lower limb
  • Edema of left upper limb
  • Edema of left upper limb
  • Edema of male genital organs
  • Edema of male genital organs
  • Edema of oral soft tissues
  • Edema of penis
  • Edema of right lower limb
  • Edema of right lower limb
  • Edema of right upper limb
  • Edema of right upper limb
  • Edema of scrotum
  • Edema of upper arm
  • Elephantiasis neurofibromatosa
  • Facial lymphedema
  • Facial lymphedema
  • Facial lymphedema
  • Facial lymphedema due to acne
  • Facial lymphedema due to rosacea
  • Hereditary disorder of lymphatic system
  • Iatrogenic lymphedema
  • Infectious edema
  • Infectious edema
  • Infectious edema
  • Intestinal lymphangiectasis
  • Jugular lymphatic obstruction sequence
  • Lipedema
  • Lipo-lymphedema
  • Lymphedema
  • Lymphedema associated with obesity
  • Lymphedema due to and following radiotherapy caused by ionizing radiation
  • Lymphedema due to chronic inflammation
  • Lymphedema due to endocrine disease
  • Lymphedema due to infection
  • Lymphedema due to infection
  • Lymphedema due to inflammatory disease
  • Lymphedema due to lymphogranuloma venereum
  • Lymphedema due to malignant infiltration
  • Lymphedema due to podoconiosis
  • Lymphedema due to radiation
  • Lymphedema due to radiation
  • Lymphedema due to recurrent infection
  • Lymphedema due to trauma
  • Lymphedema due to trauma
  • Lymphedema due to trauma
  • Lymphedema due to venous disease
  • Lymphedema due to venous insufficiency
  • Lymphedema hypoparathyroidism syndrome
  • Lymphedema of bilateral lower limbs
  • Lymphedema of bilateral upper limbs
  • Lymphedema of ear
  • Lymphedema of genitalia
  • Lymphedema of genitalia
  • Lymphedema of genitalia
  • Lymphedema of left lower limb
  • Lymphedema of left upper limb
  • Lymphedema of limb
  • Lymphedema of limbs due to immobility, chronic dependency and/or venous insufficiency
  • Lymphedema of lip
  • Lymphedema of lower extremity
  • Lymphedema of lower extremity
  • Lymphedema of penis
  • Lymphedema of right lower limb
  • Lymphedema of right upper limb
  • Lymphedema of scrotum
  • Lymphedema of uncertain etiology
  • Lymphedema of upper arm
  • Lymphedema of upper limb
  • Lymphedema praecox
  • Lymphedema, atrial septal defect, facial changes syndrome
  • Lymphedematous hyperkeratosis
  • Lymphovenous edema
  • Mullerian remnant
  • Neurofibromatosis type 1
  • Obliteration of lymphatic vessel
  • Onchocercal elephantiasis
  • Persistent Mullerian derivative with lymphangiectasia and polydactyly syndrome
  • Podoconiosis
  • Postsurgical lymphedema
  • Primary lymphangiectasis of intestine
  • Primary lymphedema
  • Primary lymphedema with systemic and visceral involvement
  • Primary lymphedema with systemic involvement
  • Primary lymphedema with visceral involvement
  • Secondary intestinal lymphangiectasia
  • Secondary xanthomatous infiltration of the skin
  • Syndromic primary lymphedema
  • Xanthoma secondary to lymphedema

Clinical Classification

Clinical Information

  • Breast Cancer Lymphedema

    abnormal accumulation of lymph in the arm, shoulder and breast area associated with surgical treatment (e.g., mastectomy) or radiation treatment of breast cancer.
  • Lymphedema

    edema due to obstruction of lymph vessels or disorders of the lymph nodes.
  • Non-Filarial Lymphedema

    a form of elephantiasis caused by soil particles which penetrate the skin of the foot. it is limited to tropical regions with soils of high volcanic content.
  • Yellow Nail Syndrome

    a rare condition characterized by the presence of yellow nails, lymphedema, and/or pleural effusion with respiratory tract involvement. abnormal lymphatic network may play a role in its etiology. occasionally inherited, yellow nail syndrome mostly is sporadic without apparent family history.
  • Lipedema

    disorder of adipose tissue characterized by symmetric and bilateral enlargement of the lower extremities due to abnormal deposition of subcutaneous fat often in obese women. it is associated with hematoma, pain and may progress to secondary lymphedema which is known as lipolymphedema.
  • Mastectomy

    surgical procedure to remove one or both breasts.
  • Primary Lymphedema

    a congenital condition that results in swelling in the arms or legs, and can occur during adolescence or adulthood. loss of motion and pain may also accompany the swelling. protein-rich lymphatic fluid accumulates in tissues, engorging and enlarging vessels and often causing visible swelling, tenderness, and pain. left untreated, the affected tissues may continue to swell, and can become hardened or fibrotic and susceptible to infection.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Elephantiasis (nonfilarial) NOS
  • Lymphangiectasis
  • Obliteration, lymphatic vessel
  • Praecox lymphedema
  • Secondary lymphedema

Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • postmastectomy lymphedema I97.2

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert I89.0 to ICD-9-CM

  • ICD-9-CM Code: 457.1 - Other lymphedema

Patient Education


Learn about lymphedema risk factors, symptoms, tests to diagnose, prevention, and treatment.
[Learn More in MedlinePlus]

Lymphedema (PDQ®)

Learn about lymphedema risk factors, symptoms, tests to diagnose, prevention, and treatment.
[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.


[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.