ICD-10-CM Code Q81.9

Epidermolysis bullosa, unspecified

Version 2020 Billable Code POA Exempt

Valid for Submission

Q81.9 is a billable code used to specify a medical diagnosis of epidermolysis bullosa, unspecified. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code Q81.9 might also be used to specify conditions or terms like congenital nephrotic syndrome, interstitial lung disease, epidermolysis bullosa syndrome or epidermolysis bullosa or localized dystrophic epidermolysis bullosa or nephrotic syndrome, deafness, pretibial epidermolysis bullosa syndrome or pretibial epidermolysis bullosa. The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Short Description:Epidermolysis bullosa, unspecified
Long Description:Epidermolysis bullosa, unspecified

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code Q81.9 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Congenital nephrotic syndrome, interstitial lung disease, epidermolysis bullosa syndrome
  • Epidermolysis bullosa
  • Localized dystrophic epidermolysis bullosa
  • Nephrotic syndrome, deafness, pretibial epidermolysis bullosa syndrome
  • Pretibial epidermolysis bullosa

Clinical Information

  • EPIDERMOLYSIS BULLOSA-. group of genetically determined disorders characterized by the blistering of skin and mucosae. there are four major forms: acquired simple junctional and dystrophic. each of the latter three has several varieties.
  • EPIDERMOLYSIS BULLOSA ACQUISITA-. form of epidermolysis bullosa characterized by trauma induced subepidermal blistering with no family history of the disease. direct immunofluorescence shows immunoglobulin g deposited at the dermo epidermal junction.
  • EPIDERMOLYSIS BULLOSA DYSTROPHICA-. form of epidermolysis bullosa characterized by atrophy of blistered areas severe scarring and nail changes. it is most often present at birth or in early infancy and occurs in both autosomal dominant and recessive forms. all forms of dystrophic epidermolysis bullosa result from mutations in collagen type vii a major component fibrils of basement membrane and epidermis.
  • EPIDERMOLYSIS BULLOSA JUNCTIONAL-. form of epidermolysis bullosa having onset at birth or during the neonatal period and transmitted through autosomal recessive inheritance. it is characterized by generalized blister formation extensive denudation and separation and cleavage of the basal cell plasma membranes from the basement membrane.
  • EPIDERMOLYSIS BULLOSA SIMPLEX-. a form of epidermolysis bullosa characterized by serous bullae that heal without scarring. mutations in the genes that encode keratin 5 and keratin 14 have been associated with several subtypes of epidermolysis bullosa simplex.

Diagnostic Related Groups

The ICD-10 code Q81.9 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.


Present on Admission (POA)

Q81.9 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here .

CMS POA Indicator Options and Definitions
POA Indicator CodePOA Reason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q81.9 to ICD-9

  • 757.39 - Skin anomaly NEC (Approximate Flag)

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Epidermolysis bullosa (Q81)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Skin Conditions

Your skin is your body's largest organ. It covers and protects your body. Your skin

  • Holds body fluids in, preventing dehydration
  • Keeps harmful microbes out, preventing infections
  • Helps you feel things like heat, cold, and pain
  • Keeps your body temperature even
  • Makes vitamin D when the sun shines on it

Anything that irritates, clogs, or inflames your skin can cause symptoms such as redness, swelling, burning, and itching. Allergies, irritants, your genetic makeup, and certain diseases and immune system problems can cause rashes, hives, and other skin conditions. Many skin problems, such as acne, also affect your appearance.

NIH: National Institute of Arthritis and Musculoskeletal and Skin Diseases

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