2027 ICD-10-CM Diagnosis Code Q80.9Congenital ichthyosis, unspecified
ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q80
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q80.9 is a billable ICD-10-CM diagnosis code for congenital ichthyosis, unspecified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 606 through 607. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q80.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations (Q80-Q89).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Alacrima
- Autosomal dominant ichthyosis
- Bathing suit ichthyosis
- CEDNIK syndrome
- Congenital anomaly of lacrimal gland
- Congenital biliary atresia
- Congenital cataract ichthyosis syndrome
- Congenital hypotrichia
- Congenital ichthyosis of skin
- Congenital ichthyosis with hypotrichosis syndrome
- Congenital ichthyosis, intellectual disability, spastic quadriplegia syndrome
- Congenital ichthyosis, microcephalus, tetraplegia syndrome
- Congenital keratoderma
- Cutaneous syndrome with ichthyosis
- HELIX syndrome
- Hypohidrosis
- Ichthyosis
- Ichthyosis congenita with biliary atresia
- Ichthyosis, alopecia, eclabion, ectropion, intellectual disability syndrome
- Ichthyosis, cerebellar degeneration and hepatosplenomegaly
- Ichthyosis, intellectual disability, dwarfism, renal impairment syndrome
- Ichthyosis, oral and digital anomalies syndrome
- Ichthyosis, short stature, brachydactyly, microspherophakia syndrome
- Keratoderma hereditarium mutilans with ichthyosis syndrome
- Lamellar ichthyosis
- Lentiglobus
- Limb reduction-ichthyosis syndrome
- MEDNIK syndrome
- Microphakia
- Microspherophakia
- Multiple sclerosis, ichthyosis, factor VIII deficiency syndrome
- Mutilating keratoderma
- Neonatal sclerosing cholangitis, ichthyosis, hypotrichosis syndrome
- Photosensitivity with ichthyosis, brittle hair, impaired intelligence, decreased fertility and short stature syndrome
- Premature ovarian insufficiency
- Salt-losing nephropathy
- Sclerosing cholangitis
- Sclerosing dysplasia of bone, ichthyosis, premature ovarian failure syndrome
- Severe ichthyoses
- Spastic tetraplegia
- Spherophakia
- Trichothiodystrophy
- Xerostomia
- X-linked intellectual disability, hypogonadism, ichthyosis, obesity, short stature syndrome
- XTE syndrome
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q80.9: its own notes plus those printed at Q80 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q80.9, its category, or a range that includes it.
Excludes1 2
These codes carry an Excludes1 note naming Q80.9: they are not reported together with it, unless the two conditions are unrelated.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Alligator skin disease Q80.9
Disease, diseased See Also: Syndrome;
alligator-skin Q80.9
fish-skin Q80.9
Ichthyosis (congenital) Q80.9
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Ichthyosis
any of several generalized skin disorders characterized by dryness, roughness, and scaliness, due to hypertrophy of the stratum corneum epidermis. most are genetic, but some are acquired, developing in association with other systemic disease or genetic syndrome.
Patient EducationClinical
Skin Conditions
Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:
The full article covers:
- What does your skin do?
- What problems and conditions can affect your skin?
- How can I keep my skin healthy?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q80.9 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q80.9Overview
What is the ICD-10 code for congenital ichthyosis, unspecified?
The ICD-10-CM code for congenital ichthyosis, unspecified is Q80.9 (sometimes written as Q809). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q80.9 (Congenital ichthyosis) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report congenital ichthyosis, unspecified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q80.9 group to?
When congenital ichthyosis, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 607, 606, with relative weights from 0.8772 to 1.5721 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q80.9 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital ichthyosis, unspecified on inpatient claims. The code appears in the Other congenital malformations (Q80-Q89) range of the CMS exempt list.
Can Q80.9 be reported with G60.1?
Not as a rule. The Excludes1 note at Q80, which applies to Q80.9, lists "Refsum's disease (G60.1)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
