ICD-10 Code Q82.0

Hereditary lymphedema

Version 2019 Billable Code POA Exempt

Valid for Submission

Q82.0 is a billable code used to specify a medical diagnosis of hereditary lymphedema. The code is valid for the year 2020 for the submission of HIPAA-covered transactions.

ICD-10: Q82.0
Short Description:Hereditary lymphedema
Long Description:Hereditary lymphedema

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Other congenital malformations of skin (Q82)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (first year ICD-10-CM implemented into the HIPAA mandated code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Medical Professionals

Diagnostic Related Groups

The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC). The diagnosis code Q82.0 is grouped in the following groups for version MS-DRG V37.0 applicable from 10/01/2020 through 09/30/2020.

  • 606 - MINOR SKIN DISORDERS WITH MCC
  • 607 - MINOR SKIN DISORDERS WITHOUT MCC

Convert Q82.0 to ICD-9

The following crosswalk between ICD-10 to ICD-9 is based based on the General Equivalence Mappings (GEMS) information:

  • 757.0 - Hereditary edema of legs

Present on Admission (POA)

Q82.0 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement.

CMS POA Indicator Options and Definitions
POA Indicator CodePOA Reason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Anhidrotic ectodermal dysplasia, immunodeficiency, osteopetrosis, lymphedema syndrome
  • Cerebral arteriovenous malformation
  • Congenital elephantiasis
  • Constricting band of extremity
  • Constricting band of extremity
  • Constriction ring of lower limb with lymphedema
  • Constriction ring of upper limb with lymphedema
  • Constriction ring syndrome
  • Constriction ring syndrome
  • Constriction ring syndrome of lower limb
  • Constriction ring syndrome of upper limb
  • Cutaneous lymphangiectasia
  • Distichiasis-lymphedema syndrome
  • Ectodermal dysplasia with sweating defect
  • Edema of foot
  • Hereditary disorder of lymphatic system
  • Hereditary lymphedema
  • Hereditary lymphedema and yellow nails
  • Hereditary lymphedema type I
  • Hereditary lymphedema type II
  • Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome
  • Lymphangiectases
  • Lymphangiectasia with chylous reflux
  • Lymphedema and cerebral arteriovenous anomaly syndrome
  • Lymphedema of lower extremity
  • Lymphedema of lower extremity
  • Lymphedema of upper limb
  • Microcephalus, lymphedema, chorioretinopathy syndrome
  • Primary lymphedema tardum
  • Progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy-like syndrome

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code Q82.0 are found in the index:


Information for Patients


Skin Conditions

Your skin is your body's largest organ. It covers and protects your body. Your skin

  • Holds body fluids in, preventing dehydration
  • Keeps harmful microbes out, preventing infections
  • Helps you feel things like heat, cold, and pain
  • Keeps your body temperature even
  • Makes vitamin D when the sun shines on it

Anything that irritates, clogs, or inflames your skin can cause symptoms such as redness, swelling, burning, and itching. Allergies, irritants, your genetic makeup, and certain diseases and immune system problems can cause rashes, hives, and other skin conditions. Many skin problems, such as acne, also affect your appearance.

NIH: National Institute of Arthritis and Musculoskeletal and Skin Diseases


[Learn More]

Meige disease Meige disease is a condition that affects the normal function of the lymphatic system. The lymphatic system consists of a network of vessels that transport lymphatic fluid and immune cells throughout the body. Meige disease is characterized by the abnormal transport of lymphatic fluid. When this fluid builds up abnormally, it causes swelling (lymphedema) in the lower limbs.Meige disease is classified as a primary lymphedema, which means it is a form of lymphedema that is not caused by other health conditions. In Meige disease, the lymphatic system abnormalities are present from birth (congenital), although the swelling is not usually apparent until puberty. The swelling often begins in the feet and ankles and progresses up the legs to the knees. Some affected individuals develop non-contagious skin infections called cellulitis or erysipelas in the legs, which can further damage the vessels that carry lymphatic fluid.
[Learn More]

Milroy disease Milroy disease is a condition that affects the normal function of the lymphatic system. The lymphatic system produces and transports fluids and immune cells throughout the body. Impaired transport with accumulation of lymph fluid can cause swelling (lymphedema). Individuals with Milroy disease typically have lymphedema in their lower legs and feet at birth or develop it in infancy. The lymphedema typically occurs on both sides of the body and may worsen over time.Milroy disease is associated with other features in addition to lymphedema. Males with Milroy disease are sometimes born with an accumulation of fluid in the scrotum (hydrocele). Males and females may have upslanting toenails, deep creases in the toes, wart-like growths (papillomas), and prominent leg veins. Some individuals develop non-contagious skin infections called cellulitis that can damage the thin tubes that carry lymph fluid (lymphatic vessels). Episodes of cellulitis can cause further swelling in the lower limbs.
[Learn More]

ICD-10 Footnotes

General Equivalence Map Definitions
The ICD-10 and ICD-9 GEMs are used to facilitate linking between the diagnosis codes in ICD-9-CM and the new ICD-10-CM code set. The GEMs are the raw material from which providers, health information vendors and payers can derive specific applied mappings to meet their needs.

  • Approximate Flag - The approximate flag is on, indicating that the relationship between the code in the source system and the code in the target system is an approximate equivalent.
  • No Map Flag - The no map flag indicates that a code in the source system is not linked to any code in the target system.
  • Combination Flag - The combination flag indicates that more than one code in the target system is required to satisfy the full equivalent meaning of a code in the source system.