2026 ICD-10-CM Diagnosis Code Q75.041Lambdoid craniosynostosis, unilateral

ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q75

ICD-10-CM Q75.041
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q75.041 is a billable ICD-10-CM diagnosis code for lambdoid craniosynostosis, unilateral. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. Coders also document this condition as congenital left unilambdoid craniosynostosis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q75.041
Billable Status
Yes — Valid for Submission
Code Describes
Lambdoid craniosynostosis, unilateral
Short Description
Lambdoid craniosynostosis, unilateral
Same as the full description in the CMS dataset.
Parent Code
Q75.04
Lambdoid craniosynostosis

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategoryQ75Other congenital malformations of skull and face bones
This CodeQ75.041Lambdoid craniosynostosis, unilateral

Present on Admission (POA)Billing

Q75.041 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Congenital left unilambdoid craniosynostosis
  • Congenital right unilambdoid craniosynostosis
  • Non-syndromic unilambdoid craniosynostosis
  • Parieto-occipital craniosynostosis
  • Plagiocephaly
  • Simple craniosynostosis

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Craniosynostosis
      • lambdoid
        • unilateral

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Craniosynostoses

    premature closure of one or more cranial sutures. it often results in plagiocephaly. craniosynostoses that involve multiple sutures are sometimes associated with congenital syndromes such as acrocephalosyndactylia; and craniofacial dysostosis.

  • Plagiocephaly

    the condition characterized by uneven or irregular shape of the head often in parallelogram shape with a flat spot on the back or one side of the head. it can either result from the premature cranial suture closure (craniosynostosis) or from external forces (nonsynostotic plagiocephaly).

  • Plagiocephaly, Nonsynostotic

    a deformity of the skull that is not due to bone fusion (synostosis), such as craniosynostoses, and is characterized by an asymmetric skull and face. it is observed with an increased frequency in infants after the adoption of supine sleeping recommendations to prevent sudden infant death syndrome.

Code History & ChangesHistory

Replacement Q75.041 replaces the following previously assigned code(s):

  • Q75.0 - Craniosynostosis
FY 2024AddedAdded to the ICD-10-CM code setEffective October 1, 2023.
FY 2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q75.041Overview

Is Q75.041 (Lambdoid craniosynostosis) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report lambdoid craniosynostosis, unilateral on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q75.041 group to?

When lambdoid craniosynostosis, unilateral is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q75.041 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for lambdoid craniosynostosis, unilateral on inpatient claims.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.