2026 ICD-10-CM Diagnosis Code Q61.9Cystic kidney disease, unspecified

ICD-10-CM Codes›Q00-Q99›Q60-Q64›Q61

ICD-10-CM Q61.9
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q61.9 is a billable ICD-10-CM diagnosis code for cystic kidney disease, unspecified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 698 through 700. The code is exempt from POA reporting. Coders also document this condition as autosomal dominant polycystic kidney disease. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q61.9
Billable Status
Yes — Valid for Submission
Code Describes
Cystic kidney disease, unspecified
Short Description
Cystic kidney disease, unspecified
Same as the full description in the CMS dataset.
Parent Code
Q61
Cystic kidney disease

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ60-Q64Congenital malformations of the urinary system
CategoryQ61Cystic kidney disease
This CodeQ61.9Cystic kidney disease, unspecified

Present on Admission (POA)Billing

Q61.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal dominant polycystic kidney disease
  • Cerebral ventriculomegaly, cystic kidney disease
  • Congenital enlargement of ventricle of brain
  • Meckel-Gruber syndrome
  • Multinodular goiter
  • Multinodular goiter, cystic kidney, polydactyly syndrome
  • Multiple congenital cysts of kidney
  • Ventriculomegaly

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Meckel-Gruber syndrome

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Cystic
      • kidney (congenital)
    • Degeneration, degenerative
      • kidney
        • cystic, congenital
    • Disease, diseased
      • cystic
        • kidney, congenital
    • Disease, diseased
      • kidney (functional) (pelvis)
        • cystic (congenital)
    • Disease, diseased
      • renal (functional) (pelvis)
        • cystic, congenital
    • Meckel-Gruber syndrome

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Autosomal Dominant Polycystic Kidney Disease

    polycystic kidney disease inherited in an autosomal dominant pattern. symptoms usually appear at middle age and include abdominal pain, hematuria and high blood pressure. patients may develop brain aneurysms and liver cysts.

  • Autosomal Dominant Polycystic Kidney Disease Type 2

    autosomal dominant polycystic kidney disease caused by a mutation in pkd2.

  • Autosomal Dominant Polycystic Kidney Disease Type I

    autosomal dominant polycystic kidney disease caused by a mutation in pkd1.

  • Autosomal Recessive Polycystic Kidney Disease|Autosomal Recessive Polycystic Kidney|Polycystic Kidney Disease, Infantile Type

    polycystic kidney disease inherited in an autosomal recessive pattern. patients present with progressive renal failure early in life. the autosomal recessive trait is associated with abnormalities of chromosome 6.

  • CDISC Polycystic Kidney Disease (PKD) Therapeutic Area User Guide Version 1.0|Polycystic Kidney Disease (PKD) Therapeutic Area User Guide v1.0

    the 1.0 version of the polycystic kidney disease cdisc therapeutic area user guide.

  • Cystic Kidney Disease

    a congenital or acquired kidney disorder characterized by the presence of renal cysts.

  • Glomerulocystic Disease|Glomerulocystic Kidney Disease

    a condition characterized by dilatation of the bowman space and affecting more than 5% of the glomeruli.

  • IFT88 wt Allele|D13S1056E|DAF19|DAF19, C. elegans, Homolog of Gene|Intraflagellar Transport 88 Homolog (Chlamydomonas) Gene|Intraflagellar Transport 88 Homolog Gene|Intraflagellar Transport 88 wt Allele|MGC26259|Polaris Homolog Gene|Polaris, Mouse, Homolog of Gene|Probe HTg737 (Polycystic Kidney Disease, Autosomal Recessive) Gene|TG737|TG737, Mouse, Homolog of Gene|TTC10|hTg737

    human ift88 wild-type allele is located in the vicinity of 13q12.1 and is approximately 125 kb in length. this allele, which encodes intraflagellar transport protein 88 homolog, plays a role in the assembly of both cilia and autophagosomes.

  • Intraflagellar Transport Protein 88 Homolog|IFT88|Recessive Polycystic Kidney Disease Protein Tg737 Homolog|TPR Repeat Protein 10|Testicular Tissue Protein Li 93|Tetratricopeptide Repeat Domain 10|Tetratricopeptide Repeat Protein 10

    intraflagellar transport protein 88 homolog (833 aa, ~94 kda) is encoded by the human ift88 gene. this protein is involved in cilium and autophagosome assembly.

  • Medullary Cystic Kidney Disease Type I|Autosomal Dominant Interstitial Kidney Disease

    an inherited form of cystic kidney disease that leads to fibrosis and impaired renal function as a result of defects in the muc1 gene, which encodes mucin 1.

  • Medullary Cystic Kidney Disease Type II

    an inherited form of cystic kidney disease leading to fibrosis and impaired renal function that is caused by mutations in the umod gene, which encodes uromodulin/tamm-horsfall mucoprotein.

  • MUC1 wt Allele|ADMCKD|ADMCKD1|CA 15-3|CD227|EMA|H23AG|KL-6|MAM6|MCD|MCKD|MCKD1|MUC-1|MUC-1/SEC|MUC-1/X|MUC1|MUC1/ZD|Medullary Cystic Kidney Disease 1 (Autosomal Dominant) Gene|Mucin 1, Cell Surface Associated wt Allele|Mucin 1, Transmembrane Gene|Mucin 1, Tumor-Associated Epithelial Gene|Mucin 1, Urinary Gene|Mucin Like 1 Gene|Mucin-Like 1 Gene|PEM|PUM

    human muc1 wild-type allele is located within 1q21 and is approximately 121 kb in length. this allele, which encodes mucin-like protein 1, plays a role in both cellular defense by binding pathogens and in cell signaling.

  • PKD1 Gene|PKD1|PKD1|Polycystic Kidney Disease 1 (Autosomal Dominant) Gene

    this gene plays a role in kidney development.

  • PKD1 wt Allele|PBP|Polycystic Kidney Disease 1 (Autosomal Dominant) wt Allele|Polycystin 1 Gene

    human pkd1 wild-type allele is located in the vicinity of 16p13.3 and is approximately 47 kb in length. this allele, which encodes polycystin-1 protein, is involved in the development of the kidney. mutations in the gene are associated with polycystic kidney disease autosomal dominant type 1.

  • PKD1L1 Gene|PKD1L1|PKD1L1|Polycystic Kidney Disease 1 Like 1 Gene

    this gene is involved in the modulation of calcium transport.

  • PKD1L1 wt Allele|PRO19563|Polycystic Kidney Disease 1 Like 1 wt Allele|Polycystin 1-Like 1 Gene|UNQ5785/PRO19563

    human pkd1l1 wild-type allele is located in the vicinity of 7p12.3 and is approximately 174 kb in length. this allele, which encodes polycystic kidney disease protein 1-like 1 protein, plays a role in the modulation of ciliary calcium concentration.

  • Polycystic Kidney Disease Protein 1-Like 1|PC1-Like 1 Protein|PKD1L1|Polycystin-1L1

    polycystic kidney disease protein 1-like 1 (2849 aa, ~315 kda) is encoded by the human pkd1l1 gene. this protein is involved in ciliary calcium concentration modulation.

  • Polycystic Kidney Disease Protein 1-Like 2|PC1-Like 2 Protein|PKD1L2|Polycystic Kidney Disease 1-Like 2|Polycystin-1L2

    polycystic kidney disease protein 1-like 2 (2459 aa, ~273 kda) is encoded by the human pkd1l2 gene. this protein may play a role in calcium transport and receptor signaling.

  • Polycystic Kidney Disease, Infantile Severe, with Tuberous Sclerosis|Autosomal Dominant Polycystic Kidney Disease Type 1 with Tuberous Sclerosis|PKDTS|TSC2-PKD1 Contiguous Gene Deletion Syndrome

    an autosomal dominant condition caused by a contiguous gene deletion involving the pkd1 and tsc2 genes, encoding polycystin-1 and tuberin respectively. it is characterized by polycystic kidneys and tuberous sclerosis.

  • Polycystic Kidney Disease|Fibrocystic Renal Disease|PKD - Polycystic Kidney Disease

    a usually autosomal dominant and less frequently autosomal recessive genetic disorder characterized by the presence of numerous cysts in the kidneys leading to end-stage renal failure. the autosomal dominant trait is associated with abnormalities on the short arm of chromosome 16. symptoms in patients with the autosomal dominant trait usually appear at middle age and include abdominal pain, hematuria, and high blood pressure. patients may develop brain aneurysms and liver cysts. patients with the autosomal recessive trait present with progressive renal failure early in life and symptoms resulting from hepatic fibrosis. the autosomal recessive trait is associated with abnormalities of chromosome 6. polycystic kidney disease may also result as a side effect in patients on renal dialysis.

  • Polycystin-1|Autosomal Dominant Polycystic Kidney Disease Protein 1

    polycystin-1 (4303 aa, ~463 kda) is encoded by the human pkd1 gene. this protein may play a role in protein-protein and protein-carbohydrate interactions during kidney development.

  • Polycystin-1 Measurement|Autosomal Dominant Polycystic Kidney Disease 1 Protein|PC1|PKD1 Measurement|Polycystin 1, Transient Receptor Potential Channel Interacting|Polycystin-1|Polycystin-1|TRPP1

    the determination of the polycystin-1 present in a sample.

  • PKD1 wt Allele|Eliosin Gene|PBP|PC1|Pc-1|Polycystic Kidney Disease 1 (Autosomal Dominant) Gene|Polycystic Kidney Disease-Associated Protein Gene|Polycystin 1 Gene|Polycystin 1, Transient Receptor Potential Channel Interacting wt Allele|Transient Receptor Potential Cation Channel, Subfamily P, Member 1 Gene

    human pkd1 wild-type allele is located in the vicinity of 16p13.3 and is approximately 47 kb in length. this allele, which encodes polycystin-1 protein, is involved in the development of the kidney. mutations in the gene are associated with polycystic kidney disease autosomal dominant type 1.

  • PKD1L2 wt Allele|KIAA1879|PC1L2|Polycystic Kidney Disease 1-Like 2 Gene|Polycystin 1 Like 2 (Gene/Pseudogene) wt Allele|Polycystin 1-Like 2 Gene

    human pkd1l2 wild-type allele is located in the vicinity of 16q23.2 and is approximately 119 kb in length. this allele, which encodes polycystin-1-like protein 2, may be involved in g protein-coupled receptor signaling and the regulation of calcium transport.

  • Polycystic Kidney Disease 1-Like 2|PC1-Like 2 Protein|PKD1L2|Polycystic Kidney Disease Protein 1-Like 2|Polycystin-1L2

    polycystin-1-like protein 2 (2459 aa, ~273 kda) is encoded by the human pkd1l2 gene. this protein may play a role in calcium transport and receptor signaling.

  • Polycystin-1|Autosomal Dominant Polycystic Kidney Disease Protein 1|PC1|Polycystic Kidney Disease-Associated Protein|Polycystin 1

    polycystin-1 (4303 aa, ~463 kda) is encoded by the human pkd1 gene. this protein may play a role in protein-protein and protein-carbohydrate interactions during kidney development.

  • Multinodular Goiter

    nodular goiter characterized by more than one discrete tissue mass.

  • Non-Toxic Multinodular Goiter|Nontoxic multinodular goiter

    a multinodular goiter that is not associated with changes in thyroid function or malignancy.

  • Thyrotoxicosis with Toxic Multinodular Goiter with Thyrotoxic Crisis|Thyrotoxicosis with toxic multinodular goiter with thyrotoxic crisis

    evidence of thyrotoxicosis with toxic multinodular goiter with thyrotoxic crisis.

  • Thyrotoxicosis with Toxic Multinodular Goiter without Thyrotoxic Crisis|Thyrotoxicosis with toxic multinodular goiter without thyrotoxic crisis

    evidence of thyrotoxicosis with toxic multinodular goiter without thyrotoxic crisis.

Patient EducationClinical

Kidney Cysts

A cyst is a fluid-filled sac. You may get simple kidney cysts as you age; they are usually harmless. There are also some diseases which cause kidney cysts. One type is polycystic kidney disease (PKD). It runs in families. In PKD, many cysts grow in the kidneys. This can enlarge the kidneys and make them work poorly.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q61.9 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
753.10 Cystic kidney diseas NOS
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q61.9Overview

Is Q61.9 (Cystic kidney disease) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report cystic kidney disease, unspecified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q61.9 group to?

When cystic kidney disease, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 698, 699, 700, with relative weights from 0.6899 to 1.6544 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q61.9 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for cystic kidney disease, unspecified on inpatient claims.

What is the ICD-9 equivalent of Q61.9?

Under the General Equivalence Mappings, cystic kidney disease, unspecified converts to ICD-9-CM 753.10 (cystic kidney diseas NOS). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.