2027 ICD-10-CM Diagnosis Code Q61.9Cystic kidney disease, unspecified

ICD-10-CM Codes›Q00-Q99›Q60-Q64›Q61

ICD-10-CM Q61.9
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q61.9 is a billable ICD-10-CM diagnosis code for cystic kidney disease, unspecified. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 698 through 700. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 3 closely related codes. The code is exempt from POA reporting. Coders also document this condition as autosomal dominant polycystic kidney disease. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q61.9
Billable Status
Yes — Valid for Submission
Code Describes
Cystic kidney disease, unspecified
Short Description
Cystic kidney disease, unspecified
Same as the full description in the CMS dataset.
Parent Code
Cystic kidney disease

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ60-Q64Congenital malformations of the urinary system
CategoryQ61Cystic kidney disease
This CodeQ61.9Cystic kidney disease, unspecified

Present on Admission (POA)Billing

Q61.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the urinary system (Q60-Q64).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal dominant polycystic kidney disease
  • Cerebral ventriculomegaly, cystic kidney disease
  • Congenital enlargement of ventricle of brain
  • Congenital goiter
  • Meckel-Gruber syndrome
  • Multinodular goiter
  • Multinodular goiter, cystic kidney, polydactyly syndrome
  • Multiple congenital cysts of kidney
  • Thyroid follicular nodular disease
  • Ventriculomegaly

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q61.9: its own notes plus those printed at Q61 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Meckel-Gruber syndrome

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Q61 Cystic kidney disease applies to 11 codes
  • acquired cyst of kidney (N28.1)
  • Potter's syndrome (Q60.6)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q61.9, its category, or a range that includes it.

Excludes1 4

These codes carry an Excludes1 note naming Q61.9: they are not reported together with it, unless the two conditions are unrelated.

  • Q01 Encephalocele
    Meckel-Gruber syndrome (Q61.9)
  • Q02 Microcephaly
    Meckel-Gruber syndrome (Q61.9)
  • Q85.8 Other phakomatoses, not elsewhere classified
    Meckel-Gruber syndrome (Q61.9)
  • N28.1 Cyst of kidney, acquired
    cystic kidney disease (congenital) (Q61.-) names Q61.-, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Kidney Diseases, Cystic

    a heterogeneous group of hereditary and acquired disorders in which the kidney contains one or more cysts unilaterally or bilaterally (kidney, cystic).

Patient EducationClinical

Kidney Cysts

A cyst is a fluid-filled sac. You may get simple kidney cysts as you age; they are usually harmless. There are also some diseases which cause kidney cysts. One type is polycystic kidney disease (PKD). It runs in families. In PKD, many cysts grow in the kidneys. This can enlarge the kidneys and make them work poorly.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q61.9 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
753.10 Cystic kidney diseas NOS
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q61.9Overview

What is the ICD-10 code for cystic kidney disease, unspecified?

The ICD-10-CM code for cystic kidney disease, unspecified is Q61.9 (sometimes written as Q619). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q61.9 (Cystic kidney disease) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report cystic kidney disease, unspecified on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q61.9 group to?

When cystic kidney disease, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 699, 698, 700, with relative weights from 0.6740 to 1.6400 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q61.9 a CC or MCC?

CMS lists Q61.9 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 3 closely related codes in its exclusion list.

Is Q61.9 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for cystic kidney disease, unspecified on inpatient claims. The code appears in the Congenital malformations of the urinary system (Q60-Q64) range of the CMS exempt list.