ICD-10-CM Code Q61.4

Renal dysplasia

Version 2020 Billable Code POA Exempt

Valid for Submission

Q61.4 is a billable code used to specify a medical diagnosis of renal dysplasia. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code Q61.4 might also be used to specify conditions or terms like bilateral multicystic renal dysplasia, bilateral renal dysplasia, bilateral secondary renal dysplasia, bresek syndrome, disorder of fetal abdominal region, dysplasia of left kidney, etc The code is exempt from present on admission (POA) reporting for inpatient admissions to general acute care hospitals.

Short Description:Renal dysplasia
Long Description:Renal dysplasia

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code Q61.4:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Multicystic dysplastic kidney
  • Multicystic kidney (development)
  • Multicystic kidney disease
  • Multicystic renal dysplasia

Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code Q61.4 are found in the index:


The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Bilateral multicystic renal dysplasia
  • Bilateral renal dysplasia
  • Bilateral secondary renal dysplasia
  • BRESEK syndrome
  • Disorder of fetal abdominal region
  • Dysplasia of left kidney
  • Dysplasia of left kidney
  • Dysplasia of right kidney
  • Dysplasia of right kidney
  • Fibrosis of pancreas
  • Left renal agenesis
  • Left renal agenesis co-occurrent with right renal dysplasia
  • Multicystic renal dysplasia
  • Multiple renal cysts
  • Primary renal dysplasia
  • Renal agenesis
  • Renal agenesis
  • Renal dysplasia
  • Renal dysplasia and retinal aplasia
  • Renal dysplasia due to fetal exposure to angiotensin converting enzyme inhibitor
  • Renal hepatic pancreatic dysplasia
  • Right renal agenesis
  • Right renal agenesis co-occurrent with left renal dysplasia
  • Saldino-Mainzer dysplasia
  • Secondary renal dysplasia
  • Thymic, renal, anal, lung dysplasia syndrome
  • Torticollis, keloids, cryptorchidism, renal dysplasia syndrome
  • Ulbright Hodes syndrome

Clinical Information

  • MULTICYSTIC DYSPLASTIC KIDNEY-. a nongenetic defect due to malformation of the kidney which appears as a bunch of grapes with multiple renal cysts but lacking the normal renal bean shape and the collection drainage system. this condition can be detected in utero with ultrasonography.

Diagnostic Related Groups

The ICD-10 code Q61.4 is grouped in the following groups for version MS-DRG V37.0 What are Diagnostic Related Groups?
The Diagnostic Related Groups (DRGs) are a patient classification scheme which provides a means of relating the type of patients a hospital treats. The DRGs divides all possible principal diagnoses into mutually exclusive principal diagnosis areas referred to as Major Diagnostic Categories (MDC).
applicable from 10/01/2019 through 09/30/2020.


Present on Admission (POA)

Q61.4 is exempt from POA reporting - The Present on Admission (POA) indicator is used for diagnosis codes included in claims involving inpatient admissions to general acute care hospitals. POA indicators must be reported to CMS on each claim to facilitate the grouping of diagnoses codes into the proper Diagnostic Related Groups (DRG). CMS publishes a listing of specific diagnosis codes that are exempt from the POA reporting requirement. Review other POA exempt codes here .

CMS POA Indicator Options and Definitions
POA Indicator CodePOA Reason for CodeCMS will pay the CC/MCC DRG?
YDiagnosis was present at time of inpatient admission.YES
NDiagnosis was not present at time of inpatient admission.NO
UDocumentation insufficient to determine if the condition was present at the time of inpatient admission.NO
WClinically undetermined - unable to clinically determine whether the condition was present at the time of inpatient admission.YES
1Unreported/Not used - Exempt from POA reporting. NO

Convert Q61.4 to ICD-9

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Congenital malformations of the urinary system (Q60-Q64)
      • Cystic kidney disease (Q61)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients

Kidney Cysts

A cyst is a fluid-filled sac. You may get simple kidney cysts as you age; they are usually harmless. There are also some diseases which cause kidney cysts. One type is polycystic kidney disease (PKD). It runs in families. In PKD, many cysts grow in the kidneys. This can enlarge the kidneys and make them work poorly. About half of people with the most common type of PKD end up with kidney failure. PKD also causes cysts in other parts of the body, such as the liver.

Often, there are no symptoms at first. Later, symptoms include

  • Pain in the back and lower sides
  • Headaches
  • Blood in the urine

Doctors diagnose PKD with imaging tests and family history. There is no cure. Treatments can help with symptoms and complications. They include medicines and lifestyle changes, and if there is kidney failure, dialysis or kidney transplants.

Acquired cystic kidney disease (ACKD) happens in people who have chronic kidney disease, especially if they are on dialysis. Unlike PKD, the kidneys are normal sized, and cysts do not form in other parts of the body. ACKD often has no symptoms. Usually, the cysts are harmless and do not need treatment. If they do cause complications, treatments include medicines, draining the cysts, or surgery.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases

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