Version 2024

2024 ICD-10-CM Diagnosis Code Q61

Cystic kidney disease

ICD-10-CM Code:
Q61
ICD-10 Code for:
Cystic kidney disease
Is Billable?
Not Valid for Submission
Code Navigator:

Code Classification

  • Congenital malformations, deformations and chromosomal abnormalities
    (Q00-Q99)
    • Congenital malformations of the urinary system
      (Q60-Q64)
      • Cystic kidney disease
        (Q61)

Q61 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of cystic kidney disease. The code is not specific and is NOT valid for the year 2024 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Specific Coding Applicable to Cystic kidney disease

Non-specific codes like Q61 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10-CM codes with a higher level of specificity when coding for cystic kidney disease:

  • Q61.0 for Congenital renal cyst - NON-BILLABLE CODE

  • Use Q61.00 for Congenital renal cyst, unspecified - BILLABLE CODE

  • Use Q61.01 for Congenital single renal cyst - BILLABLE CODE

  • Use Q61.02 for Congenital multiple renal cysts - BILLABLE CODE

  • Q61.1 for Polycystic kidney, infantile type - NON-BILLABLE CODE

  • Use Q61.11 for Cystic dilatation of collecting ducts - BILLABLE CODE

  • Use Q61.19 for Other polycystic kidney, infantile type - BILLABLE CODE

  • Use Q61.2 for Polycystic kidney, adult type - BILLABLE CODE

  • Use Q61.3 for Polycystic kidney, unspecified - BILLABLE CODE

  • Use Q61.4 for Renal dysplasia - BILLABLE CODE

  • Use Q61.5 for Medullary cystic kidney - BILLABLE CODE

  • Use Q61.8 for Other cystic kidney diseases - BILLABLE CODE

  • Use Q61.9 for Cystic kidney disease, unspecified - BILLABLE CODE

Clinical Information

  • Autosomal Dominant Polycystic Kidney Disease

    polycystic kidney disease inherited in an autosomal dominant pattern. symptoms usually appear at middle age and include abdominal pain, hematuria and high blood pressure. patients may develop brain aneurysms and liver cysts.
  • Autosomal Dominant Polycystic Kidney Disease Type 2

    autosomal dominant polycystic kidney disease caused by a mutation in pkd2.
  • Autosomal Dominant Polycystic Kidney Disease Type I

    autosomal dominant polycystic kidney disease caused by a mutation in pkd1.
  • Autosomal Recessive Polycystic Kidney Disease|Autosomal Recessive Polycystic Kidney|Polycystic Kidney Disease, Infantile Type

    polycystic kidney disease inherited in an autosomal recessive pattern. patients present with progressive renal failure early in life. the autosomal recessive trait is associated with abnormalities of chromosome 6.
  • CDISC Polycystic Kidney Disease (PKD) Therapeutic Area User Guide Version 1.0|Polycystic Kidney Disease (PKD) Therapeutic Area User Guide v1.0

    the 1.0 version of the polycystic kidney disease cdisc therapeutic area user guide.
  • Cystic Kidney Disease

    a congenital or acquired kidney disorder characterized by the presence of renal cysts.
  • Glomerulocystic Disease|Glomerulocystic Kidney Disease

    a condition characterized by dilatation of the bowman space and affecting more than 5% of the glomeruli.
  • IFT88 wt Allele|D13S1056E|DAF19|DAF19, C. elegans, Homolog of Gene|Intraflagellar Transport 88 Homolog (Chlamydomonas) Gene|Intraflagellar Transport 88 Homolog Gene|Intraflagellar Transport 88 wt Allele|MGC26259|Polaris Homolog Gene|Polaris, Mouse, Homolog of Gene|Probe HTg737 (Polycystic Kidney Disease, Autosomal Recessive) Gene|TG737|TG737, Mouse, Homolog of Gene|TTC10|hTg737

    human ift88 wild-type allele is located in the vicinity of 13q12.1 and is approximately 125 kb in length. this allele, which encodes intraflagellar transport protein 88 homolog, plays a role in the assembly of both cilia and autophagosomes.
  • Intraflagellar Transport Protein 88 Homolog|IFT88|Recessive Polycystic Kidney Disease Protein Tg737 Homolog|TPR Repeat Protein 10|Testicular Tissue Protein Li 93|Tetratricopeptide Repeat Domain 10|Tetratricopeptide Repeat Protein 10

    intraflagellar transport protein 88 homolog (833 aa, ~94 kda) is encoded by the human ift88 gene. this protein is involved in cilium and autophagosome assembly.
  • Medullary Cystic Kidney Disease Type I|Autosomal Dominant Interstitial Kidney Disease

    an inherited form of cystic kidney disease that leads to fibrosis and impaired renal function as a result of defects in the muc1 gene, which encodes mucin 1.
  • Medullary Cystic Kidney Disease Type II

    an inherited form of cystic kidney disease leading to fibrosis and impaired renal function that is caused by mutations in the umod gene, which encodes uromodulin/tamm-horsfall mucoprotein.
  • MUC1 wt Allele|ADMCKD|ADMCKD1|CA 15-3|CD227|EMA|H23AG|KL-6|MAM6|MCD|MCKD|MCKD1|MUC-1|MUC-1/SEC|MUC-1/X|MUC1|MUC1/ZD|Medullary Cystic Kidney Disease 1 (Autosomal Dominant) Gene|Mucin 1, Cell Surface Associated wt Allele|Mucin 1, Transmembrane Gene|Mucin 1, Tumor-Associated Epithelial Gene|Mucin 1, Urinary Gene|Mucin Like 1 Gene|Mucin-Like 1 Gene|PEM|PUM

    human muc1 wild-type allele is located within 1q21 and is approximately 121 kb in length. this allele, which encodes mucin-like protein 1, plays a role in both cellular defense by binding pathogens and in cell signaling.
  • PKD1 Gene|PKD1|PKD1|Polycystic Kidney Disease 1 (Autosomal Dominant) Gene

    this gene plays a role in kidney development.
  • PKD1 wt Allele|PBP|Polycystic Kidney Disease 1 (Autosomal Dominant) wt Allele|Polycystin 1 Gene

    human pkd1 wild-type allele is located in the vicinity of 16p13.3 and is approximately 47 kb in length. this allele, which encodes polycystin-1 protein, is involved in the development of the kidney. mutations in the gene are associated with polycystic kidney disease autosomal dominant type 1.
  • PKD1L1 Gene|PKD1L1|PKD1L1|Polycystic Kidney Disease 1 Like 1 Gene

    this gene is involved in the modulation of calcium transport.
  • PKD1L1 wt Allele|PRO19563|Polycystic Kidney Disease 1 Like 1 wt Allele|Polycystin 1-Like 1 Gene|UNQ5785/PRO19563

    human pkd1l1 wild-type allele is located in the vicinity of 7p12.3 and is approximately 174 kb in length. this allele, which encodes polycystic kidney disease protein 1-like 1 protein, plays a role in the modulation of ciliary calcium concentration.
  • Polycystic Kidney Disease Protein 1-Like 1|PC1-Like 1 Protein|PKD1L1|Polycystin-1L1

    polycystic kidney disease protein 1-like 1 (2849 aa, ~315 kda) is encoded by the human pkd1l1 gene. this protein is involved in ciliary calcium concentration modulation.
  • Polycystic Kidney Disease Protein 1-Like 2|PC1-Like 2 Protein|PKD1L2|Polycystic Kidney Disease 1-Like 2|Polycystin-1L2

    polycystic kidney disease protein 1-like 2 (2459 aa, ~273 kda) is encoded by the human pkd1l2 gene. this protein may play a role in calcium transport and receptor signaling.
  • Polycystic Kidney Disease, Infantile Severe, with Tuberous Sclerosis|Autosomal Dominant Polycystic Kidney Disease Type 1 with Tuberous Sclerosis|PKDTS|TSC2-PKD1 Contiguous Gene Deletion Syndrome

    an autosomal dominant condition caused by a contiguous gene deletion involving the pkd1 and tsc2 genes, encoding polycystin-1 and tuberin respectively. it is characterized by polycystic kidneys and tuberous sclerosis.
  • Polycystic Kidney Disease|Fibrocystic Renal Disease|PKD - Polycystic Kidney Disease

    a usually autosomal dominant and less frequently autosomal recessive genetic disorder characterized by the presence of numerous cysts in the kidneys leading to end-stage renal failure. the autosomal dominant trait is associated with abnormalities on the short arm of chromosome 16. symptoms in patients with the autosomal dominant trait usually appear at middle age and include abdominal pain, hematuria, and high blood pressure. patients may develop brain aneurysms and liver cysts. patients with the autosomal recessive trait present with progressive renal failure early in life and symptoms resulting from hepatic fibrosis. the autosomal recessive trait is associated with abnormalities of chromosome 6. polycystic kidney disease may also result as a side effect in patients on renal dialysis.
  • Polycystin-1|Autosomal Dominant Polycystic Kidney Disease Protein 1

    polycystin-1 (4303 aa, ~463 kda) is encoded by the human pkd1 gene. this protein may play a role in protein-protein and protein-carbohydrate interactions during kidney development.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
  • acquired cyst of kidney N28.1
  • Potter's syndrome Q60.6

Patient Education


Kidney Cysts

A cyst is a fluid-filled sac. You may get simple kidney cysts as you age; they are usually harmless. There are also some diseases which cause kidney cysts. One type is polycystic kidney disease (PKD). It runs in families. In PKD, many cysts grow in the kidneys. This can enlarge the kidneys and make them work poorly. About half of people with the most common type of PKD end up with kidney failure. PKD also causes cysts in other parts of the body, such as the liver.

Often, there are no symptoms at first. Later, symptoms include:

  • Pain in the back and lower sides
  • Headaches
  • Blood in the urine

Doctors diagnose PKD with imaging tests and family history. There is no cure. Treatments can help with symptoms and complications. They include medicines and lifestyle changes, and if there is kidney failure, dialysis or kidney transplants.

Acquired cystic kidney disease (ACKD) happens in people who have chronic kidney disease, especially if they are on dialysis. Unlike PKD, the kidneys are normal sized, and cysts do not form in other parts of the body. ACKD often has no symptoms. Usually, the cysts are harmless and do not need treatment. If they do cause complications, treatments include medicines, draining the cysts, or surgery.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases


[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.