2026 ICD-10-CM Diagnosis Code Q61.3Polycystic kidney, unspecified

ICD-10-CM Codes›Q00-Q99›Q60-Q64›Q61

ICD-10-CM Q61.3
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q61.3 is a billable ICD-10-CM diagnosis code for polycystic kidney, unspecified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 698 through 700. The code is exempt from POA reporting. Coders also document this condition as autosomal dominant polycystic kidney disease. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q61.3
Billable Status
Yes — Valid for Submission
Code Describes
Polycystic kidney, unspecified
Short Description
Polycystic kidney, unspecified
Same as the full description in the CMS dataset.
Parent Code
Q61
Cystic kidney disease

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ60-Q64Congenital malformations of the urinary system
CategoryQ61Cystic kidney disease
This CodeQ61.3Polycystic kidney, unspecified

Present on Admission (POA)Billing

Q61.3 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal dominant polycystic kidney disease
  • Congenital hepatic fibrosis
  • Neonatal diabetes, congenital hypothyroidism, congenital glaucoma, hepatic fibrosis, polycystic kidney syndrome
  • NPHP3-related Meckel-like syndrome

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Cyst(colloid) (mucous) (simple) (retention)
      • congenital NEC
        • kidney
          • more than one (multiple)
            • specified as polycystic
    • Cyst(colloid) (mucous) (simple) (retention)
      • kidney
        • more than one (multiple)
          • specified as polycystic
    • Degeneration, degenerative
      • kidney
        • polycystic
    • Disease, diseased
      • kidney (functional) (pelvis)
        • polycystic
    • Disease, diseased
      • polycystic
        • kidney or renal
    • Disease, diseased
      • renal (functional) (pelvis)
        • polycystic (congenital)
    • Nephritis, nephritic(albuminuric) (azotemic) (congenital) (disseminated) (epithelial) (familial) (focal) (granulomatous) (hemorrhagic) (infantile) (nonsuppurative, excretory) (uremic)
      • polycystic
    • Polycystic(disease)
      • degeneration, kidney
    • Polycystic(disease)
      • kidney

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Autosomal Dominant Polycystic Kidney Disease

    polycystic kidney disease inherited in an autosomal dominant pattern. symptoms usually appear at middle age and include abdominal pain, hematuria and high blood pressure. patients may develop brain aneurysms and liver cysts.

  • Autosomal Dominant Polycystic Kidney Disease Type 2

    autosomal dominant polycystic kidney disease caused by a mutation in pkd2.

  • Autosomal Dominant Polycystic Kidney Disease Type I

    autosomal dominant polycystic kidney disease caused by a mutation in pkd1.

  • Polycystic Kidney Disease, Infantile Severe, with Tuberous Sclerosis|Autosomal Dominant Polycystic Kidney Disease Type 1 with Tuberous Sclerosis|PKDTS|TSC2-PKD1 Contiguous Gene Deletion Syndrome

    an autosomal dominant condition caused by a contiguous gene deletion involving the pkd1 and tsc2 genes, encoding polycystin-1 and tuberin respectively. it is characterized by polycystic kidneys and tuberous sclerosis.

  • Polycystin-1|Autosomal Dominant Polycystic Kidney Disease Protein 1

    polycystin-1 (4303 aa, ~463 kda) is encoded by the human pkd1 gene. this protein may play a role in protein-protein and protein-carbohydrate interactions during kidney development.

  • Congenital Hepatic Fibrosis

    a congenital disorder usually inherited in an autosomal recessive pattern. it affects the hepatobiliary system and the kidneys. it is characterized by liver fibrosis, portal hypertension, and renal cysts.

  • Polycystin-1 Measurement|Autosomal Dominant Polycystic Kidney Disease 1 Protein|PC1|PKD1 Measurement|Polycystin 1, Transient Receptor Potential Channel Interacting|Polycystin-1|Polycystin-1|TRPP1

    the determination of the polycystin-1 present in a sample.

  • Polycystin-1|Autosomal Dominant Polycystic Kidney Disease Protein 1|PC1|Polycystic Kidney Disease-Associated Protein|Polycystin 1

    polycystin-1 (4303 aa, ~463 kda) is encoded by the human pkd1 gene. this protein may play a role in protein-protein and protein-carbohydrate interactions during kidney development.

Patient EducationClinical

Kidney Cysts

A cyst is a fluid-filled sac. You may get simple kidney cysts as you age; they are usually harmless. There are also some diseases which cause kidney cysts. One type is polycystic kidney disease (PKD). It runs in families. In PKD, many cysts grow in the kidneys. This can enlarge the kidneys and make them work poorly.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q61.3 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
753.12 Polycystic kidney NOS
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q61.3Overview

Is Q61.3 (Cystic kidney disease) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report polycystic kidney, unspecified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q61.3 group to?

When polycystic kidney, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 698, 699, 700, with relative weights from 0.6899 to 1.6544 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q61.3 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for polycystic kidney, unspecified on inpatient claims.

What is the ICD-9 equivalent of Q61.3?

Under the General Equivalence Mappings, polycystic kidney, unspecified converts to ICD-9-CM 753.12 (polycystic kidney NOS). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.