2026 ICD-10-CM Diagnosis Code Q13.81Rieger anomaly

ICD-10-CM Codes›Q00-Q99›Q10-Q18›Q13

ICD-10-CM Q13.81
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q13.81 is a billable ICD-10-CM diagnosis code for rieger anomaly. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 124 through 125. The code is exempt from POA reporting. Coders also document this condition as acquired partial lipodystrophy. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Congenital malformations of eye, ear, face, neck.

Code Identity

ICD-10-CM Code
Q13.81
Billable Status
Yes — Valid for Submission
Code Describes
Rieger anomaly
Short Description
Rieger anomaly
Same as the full description in the CMS dataset.
Parent Code
Q13.8
Other congenital malformations of anterior segment of eye

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ10-Q18Congenital malformations of eye, ear, face and neck
CategoryQ13Congenital malformations of anterior segment of eye
This CodeQ13.81Rieger anomaly

Present on Admission (POA)Billing

Q13.81 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acquired partial lipodystrophy
  • Axenfeld-Rieger syndrome
  • Irido-trabecular dysgenesis
  • Lipodystrophy, partial, with Rieger anomaly, short stature, and insulinopenic diabetes mellitus
  • Rieger syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Axenfeld-Rieger syndrome

Code Also

  • any other associated congenital malformations such as cardiac defects

Use Additional Code

  • code for associated glaucoma H42

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • Rieger
    • Glaucoma
      • in (due to)
        • Rieger anomaly
    • Rieger anomaly or syndrome
    • Syndrome
      • Axenfeld-Rieger

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL005
Congenital malformations of eye, ear, face, neck
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Acquired Partial Lipodystrophy

    partial lipodystrophy, the cause of which is not present at birth. examples include lipodystrophy associated with human immunodeficiency virus (hiv) therapy, and barraquer-simons syndrome, associated with c3 nephritic factor.

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q13.81 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
743.44 Anom anter chamber-eye
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2024No changes
FY 2025RevisedCode revised
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q13.81Overview

Is Q13.81 (Other congenital malformations of anterior segment of eye) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report rieger anomaly on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q13.81 group to?

When rieger anomaly is the principal diagnosis on an inpatient stay, it groups to MS-DRG 124, 125, with relative weights from 0.7678 to 1.3231 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q13.81 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for rieger anomaly on inpatient claims.

What is the ICD-9 equivalent of Q13.81?

Under the General Equivalence Mappings, rieger anomaly converts to ICD-9-CM 743.44 (anom anter chamber-eye). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.