2027 ICD-10-CM Diagnosis Code Q13.81Rieger anomaly

ICD-10-CM Codes›Q00-Q99›Q10-Q18›Q13

ICD-10-CM Q13.81
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q13.81 is a billable ICD-10-CM diagnosis code for rieger anomaly. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 124 through 125. The code is exempt from POA reporting. Coders also document this condition as acquired partial lipodystrophy. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Congenital malformations of eye, ear, face, neck.

Code Identity

ICD-10-CM Code
Q13.81
Billable Status
Yes — Valid for Submission
Code Describes
Rieger anomaly
Short Description
Rieger anomaly
Same as the full description in the CMS dataset.
Parent Code
Q13.8
Other congenital malformations of anterior segment of eye

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ10-Q18Congenital malformations of eye, ear, face and neck
CategoryQ13Congenital malformations of anterior segment of eye
This CodeQ13.81Rieger anomaly

Present on Admission (POA)Billing

Q13.81 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of eye, ear, face and neck (Q10-Q18).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acquired partial lipodystrophy
  • Axenfeld-Rieger syndrome
  • Irido-trabecular dysgenesis
  • Lipodystrophy, partial, with Rieger anomaly, short stature, and insulinopenic diabetes mellitus
  • Rieger syndrome

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q13.81: its own notes plus those printed at block Q10-Q18 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Axenfeld-Rieger syndrome

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Block Q10-Q18 Congenital malformations of eye, ear, face and neck applies to 62 codes
  • cleft lip and cleft palate (Q35-Q37)
  • congenital malformation of cervical spine (Q05.0, Q05.5, Q67.5, Q76.0-Q76.4)
  • congenital malformation of larynx (Q31.-)
  • congenital malformation of lip NEC (Q38.0)
  • congenital malformation of nose (Q30.-)
  • congenital malformation of parathyroid gland (Q89.2)
  • congenital malformation of thyroid gland (Q89.2)
From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Use Additional Code

Add a second code, after this one, to fully describe the condition.

  • code for associated glaucoma (H42)

Code Also

A second code may be needed to fully describe the condition; the note gives no sequencing direction.

  • any other associated congenital malformations such as cardiac defects

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q13.81, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q13.81: they are not reported together with it, unless the two conditions are unrelated.

  • H21.4 Pupillary membranes
    congenital pupillary membranes (Q13.8) names Q13.8, which includes this code

Code First 1

These codes say to code first a condition named in the note, and Q13.81 is one of the conditions named.

  • H42 Glaucoma in diseases classified elsewhere
    Rieger anomaly (Q13.81)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL005
Congenital malformations of eye, ear, face, neck
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q13.81 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
743.44 Anom anter chamber-eye
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2024No changes
FY 2025RevisedCode revised
FY 2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q13.81Overview

What is the ICD-10 code for rieger anomaly?

The ICD-10-CM code for rieger anomaly is Q13.81 (sometimes written as Q1381). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q13.81 (Other congenital malformations of anterior segment of eye) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report rieger anomaly on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q13.81 group to?

When rieger anomaly is the principal diagnosis on an inpatient stay, it groups to MS-DRG 125, 124, with relative weights from 0.7699 to 1.2470 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q13.81 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for rieger anomaly on inpatient claims. The code appears in the Congenital malformations of eye, ear, face and neck (Q10-Q18) range of the CMS exempt list.

Does Q13.81 need an additional code?

When the condition applies, yes. The Use Additional Code note reads: code for associated glaucoma (H42). The additional code is reported after Q13.81.