2026 ICD-10-CM Diagnosis Code N07.BHereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD]

ICD-10-CM Codes›N00–N99›N00-N08›N07

ICD-10-CM N07.B
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

N07.B is a billable ICD-10-CM diagnosis code for hereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD]. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 698 through 700.

Code Identity

ICD-10-CM Code
N07.B
Billable Status
Yes — Valid for Submission
Code Describes
Hereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD]
Short Description
Hereditary nephrop, NEC with APOL1-mediated kidney disease
Parent Code
N07
Hereditary nephropathy, not elsewhere classified

Code Classification

ChapterN00–N99Diseases of the genitourinary system
SectionN00-N08Glomerular diseases
CategoryN07Hereditary nephropathy, not elsewhere classified
This CodeN07.BHereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD]

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • AMKD (with glomerulonephritis)
  • AMKD (with glomerulosclerosis)

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • AMKD(APOL1-mediated kidney disease) (with glomerulonephritis) (with glomerulosclerosis)
    • Nephropathy
      • hereditary NEC
        • with
          • APOL1-mediated kidney disease (AMKD)

Code History & ChangesHistory

New Code N07.B was added to the ICD-10-CM code set for FY 2026, effective October 1, 2025.

Replacement N07.B replaces the following previously assigned code(s):

  • N07.8 - Hereditary nephropathy, NEC w oth morphologic lesions
FY 2026AddedAdded to the ICD-10-CM code setEffective October 1, 2025.
FY 2026CurrentRevised in the current code setEffective October 1, 2025 through September 30, 2026.

Questions About N07.BOverview

Is N07.B (Hereditary nephropathy, not elsewhere classified) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report hereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD] on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does N07.B group to?

When hereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD] is the principal diagnosis on an inpatient stay, it groups to MS-DRG 698, 699, 700, with relative weights from 0.6899 to 1.6544 depending on complications. Higher weights mean higher Medicare reimbursement.