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  3. N00–N99
  4. N00-N08
  5. Rapidly progressive nephritic syndrome (N01)

Rapidly progressive nephritic syndrome (N01)

The ICD-10 code N01 and its subcategories define various forms of rapidly progressive nephritic syndrome, a serious kidney condition characterized by a swift decline in kidney function. These codes are used to specify distinct pathological types of this syndrome based on the microscopic features of kidney inflammation and damage.

This ICD-10 code section covers multiple subtypes, including N01.0 for cases with minor glomerular abnormalities, N01.1 for focal and segmental glomerular lesions, and types associated with specific histological findings such as diffuse membranous glomerulonephritis (N01.2), crescentic glomerulonephritis (N01.7), and dense deposit disease (N01.6). Synonyms like "subacute glomerulonephritis" or "idiopathic rapidly progressive glomerulonephritis" help clarify code N01.9 for unspecified morphologic changes. Recognizing these synonyms and morphologic distinctions is essential for medical coders and healthcare providers to select the accurate ICD-10 code for documentation, billing, and patient management related to this aggressive kidney disorder.

  • Diseases of the genitourinary system (N00–N99)

    • Glomerular diseases (N00-N08)

        • Rapidly progressive nephritic syndrome (N01)

        • N01 Rapidly progressive nephritic syndrome
        • N01.0 Rapidly progressive nephritic syndrome with minor glomerular abnormality
        • N01.1 Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
        • N01.2 Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
        • N01.3 Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
        • N01.4 Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
        • N01.5 Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
        • N01.6 Rapidly progressive nephritic syndrome with dense deposit disease
        • N01.7 Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
        • N01.8 Rapidly progressive nephritic syndrome with other morphologic changes
        • N01.9 Rapidly progressive nephritic syndrome with unspecified morphologic changes
        • N01.A Rapidly progressive nephritic syndrome with C3 glomerulonephritis

Instructional Notations

Includes

This note appears immediately under a three character code title to further define, or give examples of, the content of the category.

  • rapidly progressive glomerular disease
  • rapidly progressive glomerulonephritis
  • rapidly progressive nephritis

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • nephritic syndrome NOS N05