Rapidly progressive nephritic syndrome (N01) ICD-10-CM
The N01 code range covers rapidly progressive nephritic syndrome with 12 ICD-10-CM diagnosis codes. 11 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Includes
This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
- rapidly progressive glomerular disease
- rapidly progressive glomerulonephritis
- rapidly progressive nephritis
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- nephritic syndrome NOS N05
Codes in the N01 Range 12 codes · 11 billable
- N01 Rapidly progressive nephritic syndromeNon-billable
- N01.0 Rapidly progressive nephritic syndrome with minor glomerular abnormality
- N01.1 Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
- N01.2 Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
- N01.3 Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
- N01.4 Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
- N01.5 Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
- N01.6 Rapidly progressive nephritic syndrome with dense deposit disease
- N01.7 Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
- N01.8 Rapidly progressive nephritic syndrome with other morphologic changes
- N01.9 Rapidly progressive nephritic syndrome with unspecified morphologic changes
- N01.A Rapidly progressive nephritic syndrome with C3 glomerulonephritis
About the N01 Code Range
Rapidly progressive nephritic syndrome sits within glomerular diseases. Glomeruli are the kidney’s filtering structures.
The subdivisions distinguish the changes named in the glomeruli. N01.0 identifies a minor abnormality, while N01.1 identifies focal and segmental lesions. Other subdivisions name diffuse patterns, including membranous, mesangial proliferative, endocapillary proliferative, mesangiocapillary, and crescentic glomerulonephritis.
N01.6 names dense deposit disease, and N01.A names C3 glomerulonephritis. Separate subdivisions identify other or unspecified morphologic changes.
Questions About This Page
How many billable codes are in the N01 range?
Of the 12 codes in this range, 11 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the N01 range classify?
The range classifies rapidly progressive nephritic syndrome. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
