Acute nephritic syndrome (N00) ICD-10-CM
The N00 code range covers acute nephritic syndrome with 15 ICD-10-CM diagnosis codes. 13 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Includes
This note appears immediately under a three character code title to further define, or give examples of, the content of the category.
- acute glomerular disease
- acute glomerulonephritis
- acute nephritis
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the N00 Range 15 codes · 13 billable
- N00 Acute nephritic syndromeNon-billable
- N00.0 Acute nephritic syndrome with minor glomerular abnormality
- N00.1 Acute nephritic syndrome with focal and segmental glomerular lesions
- N00.2 Acute nephritic syndrome with diffuse membranous glomerulonephritis
- N00.3 Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
- N00.4 Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
- N00.5 Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
- N00.6 Acute nephritic syndrome with dense deposit disease
- N00.7 Acute nephritic syndrome with diffuse crescentic glomerulonephritis
- N00.8 Acute nephritic syndrome with other morphologic changes
- N00.9 Acute nephritic syndrome with unspecified morphologic changes
- N00.A Acute nephritic syndrome with C3 glomerulonephritis
- N00.B Acute nephritic syndrome with immune complex membranoproliferative glomerulonephritisNon-billable
- N00.B1 Acute nephritic syndrome with idiopathic immune membranoproliferative glomerulonephritis (IC-MPGN)
- N00.B2 Acute nephritic syndrome with secondary immune complex membranoproliferative glomerulonephritis (IC-MPGN)
About the N00 Code Range
Acute nephritic syndrome appears here with different patterns of glomerular change. The category sits within the glomerular diseases group.
The subdivisions separate minor abnormalities, focal and segmental lesions, diffuse patterns, and dense deposit disease. They also distinguish other morphologic changes from unspecified changes. N00.A names C3 glomerulonephritis. N00.B names immune complex membranoproliferative glomerulonephritis, with further subdivisions for idiopathic and secondary forms.
Questions About This Page
How many billable codes are in the N00 range?
Of the 15 codes in this range, 13 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the N00 range classify?
The range classifies acute nephritic syndrome. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
