Hereditary nephropathy, not elsewhere classified (N07) ICD-10-CM
The N07 code range covers hereditary nephropathy, not elsewhere classified with 13 ICD-10-CM diagnosis codes. 12 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Codes in the N07 Range 13 codes · 12 billable
- N07 Hereditary nephropathy, not elsewhere classifiedNon-billable
- N07.0 Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality
- N07.1 Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions
- N07.2 Hereditary nephropathy, not elsewhere classified with diffuse membranous glomerulonephritis
- N07.3 Hereditary nephropathy, not elsewhere classified with diffuse mesangial proliferative glomerulonephritis
- N07.4 Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis
- N07.5 Hereditary nephropathy, not elsewhere classified with diffuse mesangiocapillary glomerulonephritis
- N07.6 Hereditary nephropathy, not elsewhere classified with dense deposit disease
- N07.7 Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis
- N07.8 Hereditary nephropathy, not elsewhere classified with other morphologic lesions
- N07.9 Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions
- N07.A Hereditary nephropathy, not elsewhere classified with C3 glomerulonephritis
- N07.B Hereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD] New
About the N07 Code Range
The ICD-10 code N07 represents hereditary nephropathy not classified elsewhere, a group of kidney disorders caused by inherited abnormalities affecting the kidney’s filtering units. These codes help specify the exact type of hereditary nephropathy based on distinct microscopic kidney lesion patterns.
This section includes codes such as N07.0 for hereditary minor glomerular abnormality and N07.1 for focal segmental glomerulosclerosis, also known as hereditary focal and segmental glomerular lesions. Other codes like N07.2 and N07.3 cover hereditary diffuse membranous and mesangial proliferative glomerulonephritis, respectively. Additionally, N07.6 identifies hereditary nephropathy with dense deposit disease (fibronectin glomerulopathy). The variety of subclasses captures differences in morphology and genetic backgrounds, assisting coders and clinicians in accurately documenting conditions such as autosomal dominant or recessive focal segmental glomerulosclerosis and hereditary crescentic glomerulonephritis. Using the correct ICD-10 code for hereditary nephropathy ensures precise classification of these rare inherited kidney disorders for better clinical management and health records.
Questions About This Page
How many billable codes are in the N07 range?
Of the 13 codes in this range, 12 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the N07 range classify?
The range classifies hereditary nephropathy, not elsewhere classified. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
