Hereditary nephropathy, not elsewhere classified (N07)
The ICD-10 code N07 represents hereditary nephropathy not classified elsewhere, a group of kidney disorders caused by inherited abnormalities affecting the kidney’s filtering units. These codes help specify the exact type of hereditary nephropathy based on distinct microscopic kidney lesion patterns.
This section includes codes such as N07.0 for hereditary minor glomerular abnormality and N07.1 for focal segmental glomerulosclerosis, also known as hereditary focal and segmental glomerular lesions. Other codes like N07.2 and N07.3 cover hereditary diffuse membranous and mesangial proliferative glomerulonephritis, respectively. Additionally, N07.6 identifies hereditary nephropathy with dense deposit disease (fibronectin glomerulopathy). The variety of subclasses captures differences in morphology and genetic backgrounds, assisting coders and clinicians in accurately documenting conditions such as autosomal dominant or recessive focal segmental glomerulosclerosis and hereditary crescentic glomerulonephritis. Using the correct ICD-10 code for hereditary nephropathy ensures precise classification of these rare inherited kidney disorders for better clinical management and health records.
Diseases of the genitourinary system (N00–N99)
Glomerular diseases (N00-N08)
N07 Hereditary nephropathy, not elsewhere classified
- N07.0 Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality
- N07.1 Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions
- N07.2 Hereditary nephropathy, not elsewhere classified with diffuse membranous glomerulonephritis
- N07.3 Hereditary nephropathy, not elsewhere classified with diffuse mesangial proliferative glomerulonephritis
- N07.4 Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis
- N07.5 Hereditary nephropathy, not elsewhere classified with diffuse mesangiocapillary glomerulonephritis
- N07.6 Hereditary nephropathy, not elsewhere classified with dense deposit disease
- N07.7 Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis
- N07.8 Hereditary nephropathy, not elsewhere classified with other morphologic lesions
- N07.9 Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions
- N07.A Hereditary nephropathy, not elsewhere classified with C3 glomerulonephritis
Hereditary nephropathy, not elsewhere classified (N07)
Instructional Notations
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
