Nephrotic syndrome (N04)

Browse all the diagnosis codes used for nephrotic syndrome (n04). For easy navigation, the diagnosis codes are sorted in alphabetical order and grouped by sections. Each section is clearly marked with its description, and the corresponding three-digit code range. This format makes it simple to browse diagnosis codes in this chapter or section and find what you're looking for. We've also added green checkmark icons to label billable codes, and red warning icons for non-billable ones. This makes it easy to identify which codes can be billed.

Clinical Information

Nephrosis, Lipoid - A kidney disease with no or minimal histological glomerular changes on light microscopy and with no immune deposits. It is characterized by lipid accumulation in the epithelial cells of KIDNEY TUBULES and in the URINE. Patients usually show NEPHROTIC SYNDROME indicating the presence of PROTEINURIA with accompanying EDEMA.

Nephrotic Syndrome - A condition characterized by severe PROTEINURIA, greater than 3.5 g/day in an average adult. The substantial loss of protein in the urine results in complications such as HYPOPROTEINEMIA; generalized EDEMA; HYPERTENSION; and HYPERLIPIDEMIAS. Diseases associated with nephrotic syndrome generally cause chronic kidney dysfunction.

Instructional Notations


This note appears immediately under a three character code title to further define, or give examples of, the content of the category.

  • congenital nephrotic syndrome
  • lipoid nephrosis
  • Diseases of the genitourinary system (N00–N99)

    • Glomerular diseases (N00-N08)

        • Nephrotic syndrome (N04)

        • N04 Nephrotic syndrome
        • N04.0 Nephrotic syndrome with minor glomerular abnormality
        • N04.1 Nephrotic syndrome with focal and segmental glomerular lesions
        • N04.2 Nephrotic syndrome with diffuse membranous glomerulonephritis NEW CODE
        • N04.20 Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified NEW CODE
        • N04.21 Primary membranous nephropathy with nephrotic syndrome NEW CODE
        • N04.22 Secondary membranous nephropathy with nephrotic syndrome NEW CODE
        • N04.29 Other nephrotic syndrome with diffuse membranous glomerulonephritis NEW CODE
        • N04.3 Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
        • N04.4 Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
        • N04.5 Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
        • N04.6 Nephrotic syndrome with dense deposit disease
        • N04.7 Nephrotic syndrome with diffuse crescentic glomerulonephritis
        • N04.8 Nephrotic syndrome with other morphologic changes
        • N04.9 Nephrotic syndrome with unspecified morphologic changes
        • N04.A Nephrotic syndrome with C3 glomerulonephritis