Nephrotic syndrome (N04)

The ICD-10 code section N04 covers nephrotic syndrome, a kidney disorder causing excess protein loss in urine. These codes specify different types and underlying causes of nephrotic syndrome to help accurately capture patient diagnoses.

This code range includes various specific forms such as N04.0 for nephrotic syndrome with minor glomerular abnormalities, also known as minimal change glomerulonephritis, and N04.1 for cases involving focal and segmental glomerulosclerosis (FSGS). The codes N04.2 through N04.29 refer to nephrotic syndrome with membranous glomerulonephritis, with subcategories for primary and secondary membranous nephropathy. Other notable codes include N04.3 for diffuse mesangial proliferative glomerulonephritis and N04.5 for diffuse mesangiocapillary (membranoproliferative) glomerulonephritis. The N04.9 code covers nephrotic syndrome cases with unspecified or varied morphologic changes, including steroid-sensitive and steroid-resistant forms, as well as syndromes associated with congenital or systemic diseases. Knowing the ICD-10 code for nephrotic syndrome is essential for coding accurate clinical details for diagnosis and treatment planning.

N04 - Nephrotic syndrome
N04.2 - Nephrotic syndrome with diffuse membranous glomerulo

Filter diagnosis codes list:

Diseases of the genitourinary system (N00–N99)
- Glomerular diseases (N00-N08)
  - - N04 Nephrotic syndrome
    - N04.0 Nephrotic syndrome with minor glomerular abnormality
    - N04.1 Nephrotic syndrome with focal and segmental glomerular lesions
    - N04.2 Nephrotic syndrome with diffuse membranous glomerulonephritis
    - N04.20 Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified
    - N04.21 Primary membranous nephropathy with nephrotic syndrome
    - N04.22 Secondary membranous nephropathy with nephrotic syndrome
    - N04.29 Other nephrotic syndrome with diffuse membranous glomerulonephritis
    - N04.3 Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
    - N04.4 Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
    - N04.5 Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
    - N04.6 Nephrotic syndrome with dense deposit disease
    - N04.7 Nephrotic syndrome with diffuse crescentic glomerulonephritis
    - N04.8 Nephrotic syndrome with other morphologic changes
    - N04.9 Nephrotic syndrome with unspecified morphologic changes
    - N04.A Nephrotic syndrome with C3 glomerulonephritis

Instructional Notations

Includes

This note appears immediately under a three character code title to further define, or give examples of, the content of the category.

congenital nephrotic syndrome
lipoid nephrosis

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Nephrosis, Lipoid

A kidney disease with no or minimal histological glomerular changes on light microscopy and with no immune deposits. It is characterized by lipid accumulation in the epithelial cells of KIDNEY TUBULES and in the URINE. Patients usually show NEPHROTIC SYNDROME indicating the presence of PROTEINURIA with accompanying EDEMA.