2027 ICD-10-CM Diagnosis Code N07Hereditary nephropathy, not elsewhere classified

ICD-10-CM Codes›N00–N99›N00-N08›N07

ICD-10-CM N07
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

N07 is a non-billable ICD-10-CM category code for hereditary nephropathy, not elsewhere classified, so it cannot be submitted on claims. Use a more specific code from this category instead, such as N07.0, N07.1, N07.2, and N07.3.

Code Identity

ICD-10-CM Code
N07
Billable Status
No — Non-Billable Category
Code Describes
Hereditary nephropathy, not elsewhere classified
Short Description
Hereditary nephropathy, not elsewhere classified
Same as the full description in the CMS dataset.
Chapter
N00-N08
Glomerular diseases

Code Classification

ChapterN00–N99Diseases of the genitourinary system
SectionN00-N08Glomerular diseases
CategoryN07Hereditary nephropathy, not elsewhere classified
This CodeN07Hereditary nephropathy, not elsewhere classified

Specific Coding for Hereditary nephropathy, not elsewhere classifiedOverview

Non-specific codes like N07 require more characters. Use one of these billable codes instead:

  • Use N07.0 for Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality

  • Use N07.1 for Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions

  • Use N07.2 for Hereditary nephropathy, not elsewhere classified with diffuse membranous glomerulonephritis

  • Use N07.3 for Hereditary nephropathy, not elsewhere classified with diffuse mesangial proliferative glomerulonephritis

  • Use N07.4 for Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis

  • Use N07.5 for Hereditary nephropathy, not elsewhere classified with diffuse mesangiocapillary glomerulonephritis

  • Use N07.6 for Hereditary nephropathy, not elsewhere classified with dense deposit disease

  • Use N07.7 for Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis

  • Use N07.8 for Hereditary nephropathy, not elsewhere classified with other morphologic lesions

  • Use N07.9 for Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions

  • Use N07.A for Hereditary nephropathy, not elsewhere classified with C3 glomerulonephritis

  • Use N07.B for Hereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD]

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to N07: its own notes plus those printed at block N00-N08 and Chapter 14. A note printed at a category, block or chapter applies to every code under it.

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Block N00-N08 Glomerular diseases applies to 107 codes
  • hypertensive chronic kidney disease (I12.-)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

On N07 itself
  • Alport's syndrome (Q87.81-)
  • hereditary amyloid nephropathy (E85.-)
  • nail patella syndrome (Q87.2)
  • non-neuropathic heredofamilial amyloidosis (E85.-)
From Chapter 14 (N00-N99) Diseases of the genitourinary system applies to 838 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Code Also

A second code may be needed to fully describe the condition; the note gives no sequencing direction.

From Block N00-N08 Glomerular diseases applies to 107 codes
  • any associated kidney failure (N17-N19).

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Patient EducationClinical

Genetic Disorders

Genetic disorders are health conditions caused by changes (also called mutations or variants) in your genes. Genes are parts of DNA found in your cells that carry instructions for how your body grows, develops, and functions. Many genes tell your body how to make proteins, which are needed for your body to work properly.

The full article covers:

  • What are genetic disorders?
  • What causes genetic disorders?
  • What are the types of genetic disorders?
  • What are the different ways a genetic disorder can be inherited?
  • How are genetic disorders diagnosed?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About N07Overview

What is the ICD-10 code for hereditary nephropathy, not elsewhere classified?

N07 is the ICD-10-CM category for hereditary nephropathy, not elsewhere classified, but it is a non-billable header: claims need a more specific code from this category, listed on this page.

Is N07 (Hereditary nephropathy, not elsewhere classified) a billable code?

No. This is a category header that groups the codes for hereditary nephropathy, not elsewhere classified, and headers cannot be submitted on claims. Claims for hereditary nephropathy, not elsewhere classified need a more specific code from this category, such as N07.0, N07.1, and N07.2.

Can N07 be reported with a code from I12?

Not as a rule. The Excludes1 note at block N00-N08, which applies to N07, lists "hypertensive chronic kidney disease (I12.-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).