1. Home
  2. ICD-10-CM Codes
  3. N00–N99
  4. N00-N08
  5. N07
  6. 2026 ICD-10-CM Code N07

2026 ICD-10-CM Diagnosis Code N07

Hereditary nephropathy, not elsewhere classified

ICD-10-CM Code:
N07
ICD-10 Code for:
Hereditary nephropathy, not elsewhere classified
Is Billable?
Not Valid for Submission
Code Navigator:

N07 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of hereditary nephropathy, not elsewhere classified. The code is not specific and is NOT valid for the year 2026 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

Specific Coding Applicable to Hereditary nephropathy, not elsewhere classified

Non-specific codes like N07 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10-CM codes with a higher level of specificity when coding for hereditary nephropathy, not elsewhere classified:

  • Use N07.0 for Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality - BILLABLE CODE

  • Use N07.1 for Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions - BILLABLE CODE

  • Use N07.2 for Hereditary nephropathy, not elsewhere classified with diffuse membranous glomerulonephritis - BILLABLE CODE

  • Use N07.3 for Hereditary nephropathy, not elsewhere classified with diffuse mesangial proliferative glomerulonephritis - BILLABLE CODE

  • Use N07.4 for Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis - BILLABLE CODE

  • Use N07.5 for Hereditary nephropathy, not elsewhere classified with diffuse mesangiocapillary glomerulonephritis - BILLABLE CODE

  • Use N07.6 for Hereditary nephropathy, not elsewhere classified with dense deposit disease - BILLABLE CODE

  • Use N07.7 for Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis - BILLABLE CODE

  • Use N07.8 for Hereditary nephropathy, not elsewhere classified with other morphologic lesions - BILLABLE CODE

  • Use N07.9 for Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions - BILLABLE CODE

  • Use N07.A for Hereditary nephropathy, not elsewhere classified with C3 glomerulonephritis - BILLABLE CODE

  • Use N07.B for Hereditary nephropathy, not elsewhere classified with APOL1-mediated kidney disease [AMKD] - BILLABLE CODE

Code Classification

  • Diseases of the genitourinary system
    N00–N99
    • Glomerular diseases
      N00-N08
      • Hereditary nephropathy, not elsewhere classified
        N07

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.


Type 2 Excludes

Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
  • Alport's syndrome Q87.81
  • hereditary amyloid nephropathy E85
  • nail patella syndrome Q87.2
  • non-neuropathic heredofamilial amyloidosis E85

Patient Education


Genetic Disorders

What are genetic disorders?

Genetic disorders are health conditions caused by changes (also called mutations or variants) in your genes. Genes are parts of DNA found in your cells that carry instructions for how your body grows, develops, and functions. Many genes tell your body how to make proteins, which are needed for your body to work properly.

What causes genetic disorders?

A genetic disorder happens when a gene variant changes how a protein is made. The variant may cause the protein to work poorly or not be made at all. If genes don't make the right proteins, or don't make them correctly, it can lead to a genetic disorder.

Not all gene changes cause disease. Often, these changes have no effect. But sometimes, even a small change in DNA can affect how proteins are made.

Gene variants can be grouped into two main types:

  • Inherited variants (also called germline variants) are passed down from your parents. They come from egg or sperm cells.
  • Non-inherited (also called somatic variants) are not passed down from your parents. They happen during your lifetime. They may be caused by things like harmful chemicals or ultraviolet (UV) rays from the sun.

What are the types of genetic disorders?

Genetic disorders may be caused by:

  • Single gene disorders are caused by changes in one gene. Examples can include sickle cell anemia, where a change in a single gene can cause the condition, and Charcot-Marie-Tooth disease, where a variant in one of many different genes can cause the condition.
  • Chromosomal disorders are caused by missing, extra, or altered chromosomes. Chromosomes are structures that carry genes. These disorders involve changes in the number of chromosomes people have or changes in the structure of one or more chromosomes. An example is Down syndrome, which is caused by an extra copy of chromosome 21.
  • Complex (multifactorial) disorders are caused by changes in many genes. Each change alone may not cause the disease, but together they increase the risk. Lifestyle and environmental factors, such as exercise, diet, or exposure to pollutants, also play a role. Colon cancer is an example.

What are the different ways a genetic disorder can be inherited?

Some genetic conditions are passed down through families (inherited) in one of several patterns, depending on the specific gene involved.

Patterns of inheritance can include:

  • Dominant means you only need one changed gene to cause the condition.
  • Recessive means you need two changed copies of the gene (one from each parent) for the condition to occur.
  • X-linked conditions involve genes located on the X chromosome. These conditions often affect males more frequently.
  • Mitochondrial conditions are passed down by the mother.

How are genetic disorders diagnosed?

Your health care provider may check for a genetic condition based on:

  • A physical examination.
  • Your personal medical history.
  • Your family health history.
  • Laboratory tests, including genetic testing.

NIH: National Library of Medicine


[Learn More in MedlinePlus]

Kidney Diseases

You have two kidneys, each about the size of your fist. They are near the middle of your back, just below the rib cage. Inside each kidney there are about a million tiny structures called nephrons. They filter your blood. They remove wastes and extra water, which become urine. The urine flows through tubes called ureters. It goes to your bladder, which stores the urine until you go to the bathroom.

Most kidney diseases attack the nephrons. This damage may leave kidneys unable to remove wastes. Causes can include genetic problems, injuries, or medicines. You have a higher risk of kidney disease if you have diabetes, high blood pressure, or a close family member with kidney disease. Chronic kidney disease damages the nephrons slowly over several years. Other kidney problems include:

  • Cancer
  • Cysts
  • Stones
  • Infections

Your doctor can do blood and urine tests to check if you have kidney disease. If your kidneys fail, you will need dialysis or a kidney transplant.

NIH: National Institute of Diabetes and Digestive and Kidney Diseases


[Learn More in MedlinePlus]

Code History

  • FY 2026 - No Change, effective from 10/1/2025 through 9/30/2026
  • FY 2025 - No Change, effective from 10/1/2024 through 9/30/2025
  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.