Glomerular diseases (N00-N08)

ICD-10 codes N00 through N08 cover a group of kidney disorders affecting the glomeruli, the filtering units of the kidneys. These codes are specifically used to classify various glomerular diseases, including acute, chronic, hereditary, and nephrotic syndromes with detailed descriptions of the morphological changes involved.

This range includes codes for acute nephritic syndrome (N00) with subtypes defined by different glomerular abnormalities such as minor abnormalities, focal and segmental lesions, membranous glomerulonephritis, and crescentic glomerulonephritis. Codes like N01 describe rapidly progressive nephritic syndrome, which is a quickly worsening kidney inflammation with similar detailed morphologies. Recurrent and persistent hematuria (N02) codes address ongoing or repeated blood in urine linked to specific glomerular lesions. Chronic forms (N03) and nephrotic syndrome (N04) are also covered with distinctions based on types of glomerular damage, from minor abnormalities to dense deposit disease or membranoproliferative lesions. The codes include hereditary nephropathies (N07) with various glomerular patterns and glomerular disorders secondary to other diseases (N08). Importantly, many synonyms such as "minimal change disease," "focal segmental glomerulosclerosis," and "IgA nephropathy" are tied to specific codes to guide accurate classification of these complex kidney conditions.

  • Diseases of the genitourinary system (N00–N99)

    • Glomerular diseases (N00-N08)

        • Acute nephritic syndrome (N00)

        • N00 Acute nephritic syndrome
        • N00.0 Acute nephritic syndrome with minor glomerular abnormality
        • N00.1 Acute nephritic syndrome with focal and segmental glomerular lesions
        • N00.2 Acute nephritic syndrome with diffuse membranous glomerulonephritis
        • N00.3 Acute nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
        • N00.4 Acute nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
        • N00.5 Acute nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
        • N00.6 Acute nephritic syndrome with dense deposit disease
        • N00.7 Acute nephritic syndrome with diffuse crescentic glomerulonephritis
        • N00.8 Acute nephritic syndrome with other morphologic changes
        • N00.9 Acute nephritic syndrome with unspecified morphologic changes
        • N00.A Acute nephritic syndrome with C3 glomerulonephritis
        • Rapidly progressive nephritic syndrome (N01)

        • N01 Rapidly progressive nephritic syndrome
        • N01.0 Rapidly progressive nephritic syndrome with minor glomerular abnormality
        • N01.1 Rapidly progressive nephritic syndrome with focal and segmental glomerular lesions
        • N01.2 Rapidly progressive nephritic syndrome with diffuse membranous glomerulonephritis
        • N01.3 Rapidly progressive nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
        • N01.4 Rapidly progressive nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
        • N01.5 Rapidly progressive nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
        • N01.6 Rapidly progressive nephritic syndrome with dense deposit disease
        • N01.7 Rapidly progressive nephritic syndrome with diffuse crescentic glomerulonephritis
        • N01.8 Rapidly progressive nephritic syndrome with other morphologic changes
        • N01.9 Rapidly progressive nephritic syndrome with unspecified morphologic changes
        • N01.A Rapidly progressive nephritic syndrome with C3 glomerulonephritis
        • Recurrent and persistent hematuria (N02)

        • N02 Recurrent and persistent hematuria
        • N02.0 Recurrent and persistent hematuria with minor glomerular abnormality
        • N02.1 Recurrent and persistent hematuria with focal and segmental glomerular lesions
        • N02.2 Recurrent and persistent hematuria with diffuse membranous glomerulonephritis
        • N02.3 Recurrent and persistent hematuria with diffuse mesangial proliferative glomerulonephritis
        • N02.4 Recurrent and persistent hematuria with diffuse endocapillary proliferative glomerulonephritis
        • N02.5 Recurrent and persistent hematuria with diffuse mesangiocapillary glomerulonephritis
        • N02.6 Recurrent and persistent hematuria with dense deposit disease
        • N02.7 Recurrent and persistent hematuria with diffuse crescentic glomerulonephritis
        • N02.8 Recurrent and persistent hematuria with other morphologic changes
        • N02.9 Recurrent and persistent hematuria with unspecified morphologic changes
        • N02.A Recurrent and persistent hematuria with C3 glomerulonephritis
        • N02.B Recurrent and persistent immunoglobulin A nephropathy
        • N02.B1 Recurrent and persistent immunoglobulin A nephropathy with glomerular lesion
        • N02.B2 Recurrent and persistent immunoglobulin A nephropathy with focal and segmental glomerular lesion
        • N02.B3 Recurrent and persistent immunoglobulin A nephropathy with diffuse membranoproliferative glomerulonephritis
        • N02.B4 Recurrent and persistent immunoglobulin A nephropathy with diffuse membranous glomerulonephritis
        • N02.B5 Recurrent and persistent immunoglobulin A nephropathy with diffuse mesangial proliferative glomerulonephritis
        • N02.B6 Recurrent and persistent immunoglobulin A nephropathy with diffuse mesangiocapillary glomerulonephritis
        • N02.B9 Other recurrent and persistent immunoglobulin A nephropathy
        • Chronic nephritic syndrome (N03)

        • N03 Chronic nephritic syndrome
        • N03.0 Chronic nephritic syndrome with minor glomerular abnormality
        • N03.1 Chronic nephritic syndrome with focal and segmental glomerular lesions
        • N03.2 Chronic nephritic syndrome with diffuse membranous glomerulonephritis
        • N03.3 Chronic nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
        • N03.4 Chronic nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
        • N03.5 Chronic nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
        • N03.6 Chronic nephritic syndrome with dense deposit disease
        • N03.7 Chronic nephritic syndrome with diffuse crescentic glomerulonephritis
        • N03.8 Chronic nephritic syndrome with other morphologic changes
        • N03.9 Chronic nephritic syndrome with unspecified morphologic changes
        • N03.A Chronic nephritic syndrome with C3 glomerulonephritis
        • Nephrotic syndrome (N04)

        • N04 Nephrotic syndrome
        • N04.0 Nephrotic syndrome with minor glomerular abnormality
        • N04.1 Nephrotic syndrome with focal and segmental glomerular lesions
        • N04.2 Nephrotic syndrome with diffuse membranous glomerulonephritis
        • N04.20 Nephrotic syndrome with diffuse membranous glomerulonephritis, unspecified
        • N04.21 Primary membranous nephropathy with nephrotic syndrome
        • N04.22 Secondary membranous nephropathy with nephrotic syndrome
        • N04.29 Other nephrotic syndrome with diffuse membranous glomerulonephritis
        • N04.3 Nephrotic syndrome with diffuse mesangial proliferative glomerulonephritis
        • N04.4 Nephrotic syndrome with diffuse endocapillary proliferative glomerulonephritis
        • N04.5 Nephrotic syndrome with diffuse mesangiocapillary glomerulonephritis
        • N04.6 Nephrotic syndrome with dense deposit disease
        • N04.7 Nephrotic syndrome with diffuse crescentic glomerulonephritis
        • N04.8 Nephrotic syndrome with other morphologic changes
        • N04.9 Nephrotic syndrome with unspecified morphologic changes
        • N04.A Nephrotic syndrome with C3 glomerulonephritis
        • Unspecified nephritic syndrome (N05)

        • N05 Unspecified nephritic syndrome
        • N05.0 Unspecified nephritic syndrome with minor glomerular abnormality
        • N05.1 Unspecified nephritic syndrome with focal and segmental glomerular lesions
        • N05.2 Unspecified nephritic syndrome with diffuse membranous glomerulonephritis
        • N05.3 Unspecified nephritic syndrome with diffuse mesangial proliferative glomerulonephritis
        • N05.4 Unspecified nephritic syndrome with diffuse endocapillary proliferative glomerulonephritis
        • N05.5 Unspecified nephritic syndrome with diffuse mesangiocapillary glomerulonephritis
        • N05.6 Unspecified nephritic syndrome with dense deposit disease
        • N05.7 Unspecified nephritic syndrome with diffuse crescentic glomerulonephritis
        • N05.8 Unspecified nephritic syndrome with other morphologic changes
        • N05.9 Unspecified nephritic syndrome with unspecified morphologic changes
        • N05.A Unspecified nephritic syndrome with C3 glomerulonephritis
        • Isolated proteinuria with specified morphological lesion (N06)

        • N06 Isolated proteinuria with specified morphological lesion
        • N06.0 Isolated proteinuria with minor glomerular abnormality
        • N06.1 Isolated proteinuria with focal and segmental glomerular lesions
        • N06.2 Isolated proteinuria with diffuse membranous glomerulonephritis
        • N06.20 Isolated proteinuria with diffuse membranous glomerulonephritis, unspecified
        • N06.21 Primary membranous nephropathy with isolated proteinuria
        • N06.22 Secondary membranous nephropathy with isolated proteinuria
        • N06.29 Other isolated proteinuria with diffuse membranous glomerulonephritis
        • N06.3 Isolated proteinuria with diffuse mesangial proliferative glomerulonephritis
        • N06.4 Isolated proteinuria with diffuse endocapillary proliferative glomerulonephritis
        • N06.5 Isolated proteinuria with diffuse mesangiocapillary glomerulonephritis
        • N06.6 Isolated proteinuria with dense deposit disease
        • N06.7 Isolated proteinuria with diffuse crescentic glomerulonephritis
        • N06.8 Isolated proteinuria with other morphologic lesion
        • N06.9 Isolated proteinuria with unspecified morphologic lesion
        • N06.A Isolated proteinuria with C3 glomerulonephritis
        • Hereditary nephropathy, not elsewhere classified (N07)

        • N07 Hereditary nephropathy, not elsewhere classified
        • N07.0 Hereditary nephropathy, not elsewhere classified with minor glomerular abnormality
        • N07.1 Hereditary nephropathy, not elsewhere classified with focal and segmental glomerular lesions
        • N07.2 Hereditary nephropathy, not elsewhere classified with diffuse membranous glomerulonephritis
        • N07.3 Hereditary nephropathy, not elsewhere classified with diffuse mesangial proliferative glomerulonephritis
        • N07.4 Hereditary nephropathy, not elsewhere classified with diffuse endocapillary proliferative glomerulonephritis
        • N07.5 Hereditary nephropathy, not elsewhere classified with diffuse mesangiocapillary glomerulonephritis
        • N07.6 Hereditary nephropathy, not elsewhere classified with dense deposit disease
        • N07.7 Hereditary nephropathy, not elsewhere classified with diffuse crescentic glomerulonephritis
        • N07.8 Hereditary nephropathy, not elsewhere classified with other morphologic lesions
        • N07.9 Hereditary nephropathy, not elsewhere classified with unspecified morphologic lesions
        • N07.A Hereditary nephropathy, not elsewhere classified with C3 glomerulonephritis

Instructional Notations

Code Also

A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.

  • any associated kidney failure N17

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • hypertensive chronic kidney disease I12