2027 ICD-10-CM Diagnosis Code M30.1Polyarteritis with lung involvement [Churg-Strauss]
ICD-10-CM Codes›M00–M99›M30-M36›M30
- Billable — Valid for Submission
- CC — Complication or Comorbidity
- Risk Adjusts — HCC 278
- Chronic Condition
M30.1 is a billable ICD-10-CM diagnosis code for polyarteritis with lung involvement [Churg-Strauss]. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 542 through 544. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 74 closely related codes. Coders also document this condition as antineutrophil cytoplasmic antibody positive vasculitis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Systemic lupus erythematosus and connective tissue disorders and Vasculitis.
For Medicare Advantage risk adjustment, M30.1 maps to CMS-HCC Category 278 (Idiopathic Pulmonary Fibrosis and Lung Involvement in Systemic Sclerosis) under the V28 model, adding a risk factor of about 0.818 for a community, non-dual, aged beneficiary in payment year 2027.
Code Identity
Code Classification
Medicare Risk Adjustment (HCC)Billing
M30.1 maps to a payment category in the CMS-HCC model used to risk-adjust Medicare Advantage payments. Weights are the published community factors for payment year 2027.
Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Antineutrophil cytoplasmic antibody positive vasculitis
- Eosinophilic granulomatosis with polyangiitis
- Granulomatosis with polyangiitis
- Hypersensitivity angiitis
- Lung disorder due to autoimmune disorder
- Necrosis of artery
- Pulmonary disease due to allergic granulomatosis angiitis
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to M30.1: its own notes plus those printed at M30, block M30-M36, and Chapter 13. A note printed at a category, block or chapter applies to every code under it.
Includes
Further defines, or gives examples of, the content of the category.
- autoimmune disease NOS
- collagen (vascular) disease NOS
- systemic autoimmune disease
- systemic collagen (vascular) disease
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Allergic granulomatous angiitis
- Eosinophilic granulomatosis with polyangiitis [EGPA]
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
- microscopic polyarteritis (M31.7)
- autoimmune disease, single organ or single cell-type -code to relevant condition category
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
- arthropathic psoriasis (L40.5-)
- certain conditions originating in the perinatal period (P04-P96)
- certain infectious and parasitic diseases (A00-B99)
- compartment syndrome (traumatic) (T79.A-)
- complications of pregnancy, childbirth and the puerperium (O00-O9A)
- congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
- endocrine, nutritional and metabolic diseases (E00-E88)
- injury, poisoning and certain other consequences of external causes (S00-T88)
- neoplasms (C00-D49)
- symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)
Notes
General instructions on how these codes are used.
- Use an external cause code following the code for the musculoskeletal condition, if applicable, to identify the cause of the musculoskeletal condition
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name M30.1, its category, or a range that includes it.
Excludes1 2
These codes carry an Excludes1 note naming M30.1: they are not reported together with it, unless the two conditions are unrelated.
Excludes2 5
These codes carry an Excludes2 note naming M30.1: its condition is not part of those codes, and both may be reported when the patient has both.
- I77.82 Antineutrophilic cytoplasmic antibody [ANCA] vasculitiseosinophilic granulomatosis with polyangiitis (M30.1)
- Chapter 9 (I00-I99) Diseases of the circulatory system
- I77 Other disorders of arteries and arterioles
- J82 Pulmonary eosinophilia, not elsewhere classified
- Chapter 12 (L00-L99) Diseases of the skin and subcutaneous tissue
Code First 1
These codes say to code first a condition named in the note, and M30.1 is one of the conditions named.
- J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Churg-Strauss syndrome M30.1
Syndrome See Also: Disease;
Churg-Strauss M30.1
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Churg-Strauss Syndrome
widespread necrotizing angiitis with granulomas. pulmonary involvement is frequent. asthma or other respiratory infection may precede evidence of vasculitis. eosinophilia and lung involvement differentiate this disease from polyarteritis nodosa.
Patient EducationClinical
Eosinophilic Disorders
Eosinophils are a type of white blood cell. They help fight off infections and play a role in your body's immune response. They can also build up and cause inflammation.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert M30.1 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About M30.1Overview
What is the ICD-10 code for polyarteritis with lung involvement [Churg-Strauss]?
The ICD-10-CM code for polyarteritis with lung involvement [Churg-Strauss] is M30.1 (sometimes written as M301). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is M30.1 (Polyarteritis nodosa and related conditions) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report polyarteritis with lung involvement [Churg-Strauss] on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does M30.1 group to?
When polyarteritis with lung involvement [Churg-Strauss] is the principal diagnosis on an inpatient stay, it groups to MS-DRG 543, 544, 542, with relative weights from 0.7404 to 1.7208 depending on complications. Higher weights mean higher Medicare reimbursement.
Is M30.1 a CC or MCC?
CMS lists M30.1 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 74 closely related codes in its exclusion list.
Can M30.1 be reported with M31.7?
Not as a rule. The Excludes1 note at M30, which applies to M30.1, lists "microscopic polyarteritis (M31.7)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
What HCC is M30.1?
M30.1 (polyarteritis with lung involvement [Churg-Strauss]) maps to CMS-HCC Category 278 (Idiopathic Pulmonary Fibrosis and Lung Involvement in Systemic Sclerosis), commonly written as HCC 278, in the CMS-HCC V28 model used for Medicare Advantage risk adjustment in payment year 2027. It mapped to HCC 40 under the retired V24 model. It also maps in the PACE (CMS-HCC V22), ESRD (V21), and ESRD (V24) models. In the Part D prescription drug model it maps to RxHCC 84.
Does M30.1 risk-adjust for Medicare Advantage payment?
Yes. When documented and reported on a Medicare Advantage encounter, M30.1 adds a risk adjustment factor of about 0.818 to the beneficiary's RAF score for a community, non-dual, aged enrollee (published V28 weights range from 0.650 to 1.640 depending on the payment segment). A more severe related category (HCC 276 and HCC 277) supersedes it when both are reported. See the full factor table on the HCC 278 category page.
