2026 ICD-10-CM Diagnosis Code M30.1Polyarteritis with lung involvement [Churg-Strauss]

ICD-10-CM Codes›M00–M99›M30-M36›M30

ICD-10-CM M30.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

M30.1 is a billable ICD-10-CM diagnosis code for polyarteritis with lung involvement [Churg-Strauss]. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 542 through 544. Coders also document this condition as eosinophilic granulomatosis with polyangiitis. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Systemic lupus erythematosus and connective tissue disorders and Vasculitis.

Code Identity

ICD-10-CM Code
M30.1
Billable Status
Yes — Valid for Submission
Code Describes
Polyarteritis with lung involvement [Churg-Strauss]
Short Description
Polyarteritis with lung involvement [Churg-Strauss]
Same as the full description in the CMS dataset.
Parent Code
M30
Polyarteritis nodosa and related conditions

Code Classification

ChapterM00–M99Diseases of the musculoskeletal system and connective tissue
SectionM30-M36Systemic connective tissue disorders
CategoryM30Polyarteritis nodosa and related conditions
This CodeM30.1Polyarteritis with lung involvement [Churg-Strauss]

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Eosinophilic granulomatosis with polyangiitis
  • Granulomatosis with polyangiitis
  • Hypersensitivity angiitis
  • Lung disorder due to autoimmune disorder
  • Necrosis of artery
  • Pulmonary disease due to allergic granulomatosis angiitis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Allergic granulomatous angiitis
  • Eosinophilic granulomatosis with polyangiitis EGPA

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Angiitis
      • allergic granulomatous
    • Churg-Strauss syndrome
    • EGPA(eosinophilic granulomatosis with polyangiitis)
    • Granulomatosis
      • eosinophilic, with polyangiitis [EGPA]
    • Polyarteritis
      • nodosa
        • with lung involvement
    • Syndrome
      • Churg-Strauss

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MUS024
Systemic lupus erythematosus and connective tissue disorders
Default principal diagnosis: inpatient Yes · outpatient Yes
CCSR CIR037
Vasculitis
Default principal diagnosis: inpatient No · outpatient No

Clinical InformationClinical

  • Granulomatosis with Polyangiitis

    a multisystemic disease of a complex genetic background. it is characterized by inflammation of the blood vessels (vasculitis) leading to damage in any number of organs. the common features include granulomatous inflammation of the respiratory tract and kidneys. most patients have measurable autoantibodies (antineutrophil cytoplasmic antibodies) against myeloblastin.

Patient EducationClinical

Eosinophilic Disorders

Eosinophils are a type of white blood cell. They help fight off infections and play a role in your body's immune response. They can also build up and cause inflammation.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert M30.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
446.4 Wegener's granulomatosis
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About M30.1Overview

Is M30.1 (Polyarteritis nodosa and related conditions) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report polyarteritis with lung involvement [Churg-Strauss] on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does M30.1 group to?

When polyarteritis with lung involvement [Churg-Strauss] is the principal diagnosis on an inpatient stay, it groups to MS-DRG 542, 543, 544, with relative weights from 0.7546 to 1.7665 depending on complications. Higher weights mean higher Medicare reimbursement.

What is the ICD-9 equivalent of M30.1?

Under the General Equivalence Mappings, polyarteritis with lung involvement [Churg-Strauss] converts to ICD-9-CM 446.4 (Wegener's granulomatosis). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.