Systemic sclerosis [scleroderma] (M34) ICD-10-CM
The M34 code range covers systemic sclerosis [scleroderma] with 10 ICD-10-CM diagnosis codes. 8 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the M34 Range 10 codes · 8 billable
- M34 Systemic sclerosis [scleroderma]Non-billable
- M34.0 Progressive systemic sclerosis
- M34.1 CR(E)ST syndrome
- M34.2 Systemic sclerosis induced by drug and chemical
- M34.8 Other forms of systemic sclerosisNon-billable
- M34.81 Systemic sclerosis with lung involvement
- M34.82 Systemic sclerosis with myopathy
- M34.83 Systemic sclerosis with polyneuropathy
- M34.89 Other systemic sclerosis
- M34.9 Systemic sclerosis, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the M34 range.
CREST Syndrome
A mild form of LIMITED SCLERODERMA, a multi-system disorder. Its features include symptoms of CALCINOSIS; RAYNAUD DISEASE; ESOPHAGEAL MOTILITY DISORDERS; sclerodactyly, and TELANGIECTASIS. When the defect in esophageal function is not prominent, it is known as CRST syndrome.
Scleroderma, Diffuse
A rapid onset form of SYSTEMIC SCLERODERMA with progressive widespread SKIN thickening over the arms, the legs and the trunk, resulting in stiffness and disability.
Scleroderma, Systemic
A chronic multi-system disorder of CONNECTIVE TISSUE. It is characterized by SCLEROSIS in the SKIN, the LUNGS, the HEART, the GASTROINTESTINAL TRACT, the KIDNEYS, and the MUSCULOSKELETAL SYSTEM. Other important features include diseased small BLOOD VESSELS and AUTOANTIBODIES. The disorder is named for its most prominent feature (hard skin), and classified into subsets by the extent of skin thickening: LIMITED SCLERODERMA and DIFFUSE SCLERODERMA.
About the M34 Code Range
Systemic sclerosis, also called scleroderma, is a systemic connective tissue disorder.
The subdivisions distinguish progressive disease, CR(E)ST syndrome, drug- or chemical-induced disease, other forms, and unspecified disease. M34.8 groups other forms by lung involvement, muscle disease, nerve disease, or another specified form.
Questions About This Page
How many billable codes are in the M34 range?
Of the 10 codes in this range, 8 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the M34 range classify?
The range classifies systemic sclerosis [scleroderma]. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
