Systemic sclerosis [scleroderma] (M34) ICD-10-CM
The M34 code range covers systemic sclerosis [scleroderma] with 10 ICD-10-CM diagnosis codes. 8 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Codes in the M34 Range 10 codes · 8 billable
- M34 Systemic sclerosis [scleroderma]Non-billable
- M34.0 Progressive systemic sclerosis
- M34.1 CR(E)ST syndrome
- M34.2 Systemic sclerosis induced by drug and chemical
- M34.8 Other forms of systemic sclerosisNon-billable
- M34.81 Systemic sclerosis with lung involvement
- M34.82 Systemic sclerosis with myopathy
- M34.83 Systemic sclerosis with polyneuropathy
- M34.89 Other systemic sclerosis
- M34.9 Systemic sclerosis, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the M34 range.
CREST Syndrome
A mild form of LIMITED SCLERODERMA, a multi-system disorder. Its features include symptoms of CALCINOSIS; RAYNAUD DISEASE; ESOPHAGEAL MOTILITY DISORDERS; sclerodactyly, and TELANGIECTASIS. When the defect in esophageal function is not prominent, it is known as CRST syndrome.
About the M34 Code Range
ICD-10 codes M34 and its subcategories specifically classify systemic sclerosis, commonly known as scleroderma, a complex autoimmune condition that causes skin thickening and organ fibrosis. These codes are essential for identifying the various forms and complications of systemic sclerosis in medical records and billing.
The section includes the base code M34 for systemic sclerosis and detailed codes such as M34.0 for progressive systemic sclerosis, and M34.1 for CREST syndrome—also referred to as Raynaud's phenomenon, limited systemic sclerosis, or CREST syndrome—highlighting its limited skin involvement. Other codes cover systemic sclerosis caused by drugs or chemicals (M34.2) and subtypes with specific organ involvement like lung disease (M34.81), myopathy (M34.82), or polyneuropathy (M34.83). The codes M34.8 and M34.89 address other systemic sclerosis variants, including pediatric or diffuse forms, while M34.9 is used for unspecified systemic sclerosis with a broad range of related complications. Using the ICD-10 code for systemic sclerosis accurately helps clinicians and coders capture the precise type and associated conditions, improving diagnosis and treatment documentation.
Questions About This Page
How many billable codes are in the M34 range?
Of the 10 codes in this range, 8 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the M34 range classify?
The range classifies systemic sclerosis [scleroderma]. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
