Polyarteritis nodosa and related conditions (M30) ICD-10-CM
The M30 code range covers polyarteritis nodosa and related conditions with 6 ICD-10-CM diagnosis codes. 5 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- microscopic polyarteritis M31.7
Codes in the M30 Range 6 codes · 5 billable
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the M30 range.
Churg-Strauss Syndrome
Widespread necrotizing angiitis with granulomas. Pulmonary involvement is frequent. Asthma or other respiratory infection may precede evidence of vasculitis. Eosinophilia and lung involvement differentiate this disease from POLYARTERITIS NODOSA.
Juvenile Polyarteritis
Polyarteritis occurring in children or adolescents.
Mucocutaneous Lymph Node Syndrome
An acute, febrile, mucocutaneous condition accompanied by swelling of cervical lymph nodes in infants and young children. The principal symptoms are fever, congestion of the ocular conjunctivae, reddening of the lips and oral cavity, protuberance of tongue papillae, and edema or erythema of the extremities.
Polyarteritis Nodosa
A form of necrotizing non-granulomatous inflammation occurring primarily in medium-sized ARTERIES, often with microaneurysms. It is characterized by muscle, joint, and abdominal pain resulting from arterial infarction and scarring in affected organs. Polyarteritis nodosa with lung involvement is called CHURG-STRAUSS SYNDROME.
About the M30 Code Range
Within systemic connective tissue disorders, this category groups polyarteritis nodosa with related conditions, including a form involving the lungs and Kawasaki syndrome.
The subdivisions distinguish M30.0 for polyarteritis nodosa, M30.1 for polyarteritis with lung involvement, and M30.2 for juvenile polyarteritis, which affects children. M30.3 identifies Kawasaki syndrome, while M30.8 groups other related conditions.
Questions About This Page
How many billable codes are in the M30 range?
Of the 6 codes in this range, 5 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the M30 range classify?
The range classifies polyarteritis nodosa and related conditions. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
