Polyarteritis nodosa and related conditions (M30)

The ICD-10 code M30 covers polyarteritis nodosa and related conditions, a group of disorders involving inflammation of medium-sized arteries throughout the body. These codes are used to classify different forms and manifestations of this systemic vasculitis, including variants affecting lungs, children, and mucocutaneous tissues.

The main code, M30.0, represents polyarteritis nodosa itself, which is sometimes also called primary systemic arteritis or vasculitis of medium sized vessels. This code helps identify cases where arteries become inflamed causing diverse symptoms like neuropathy, myopathy, or nephrotic syndrome. When lung involvement occurs, M30.1 is applied; this includes conditions such as Churg-Strauss syndrome or eosinophilic granulomatosis with polyangiitis. The pediatric form, known as juvenile polyarteritis, is captured by M30.2. M30.3 covers Kawasaki disease, a mucocutaneous lymph node syndrome linked to inflammation of coronary arteries and aneurysm risk. Other related necrotizing vasculitis types fall under M30.8. These precise ICD-10 codes provide essential tools for medical coders to document specific types of polyarteritis nodosa and its variants for accurate diagnosis, treatment, and statistical tracking.