Polyarteritis nodosa and related conditions (M30) ICD-10-CM
The M30 code range covers polyarteritis nodosa and related conditions with 6 ICD-10-CM diagnosis codes. 5 of them are billable and valid for claim submission in fiscal year 2026, and the category headers group them but cannot themselves be billed.
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
- microscopic polyarteritis M31.7
Codes in the M30 Range 6 codes · 5 billable
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the M30 range.
Granulomatosis with Polyangiitis
A multisystemic disease of a complex genetic background. It is characterized by inflammation of the blood vessels (VASCULITIS) leading to damage in any number of organs. The common features include granulomatous inflammation of the RESPIRATORY TRACT and KIDNEYS. Most patients have measurable autoantibodies (ANTINEUTROPHIL CYTOPLASMIC ANTIBODIES) against MYELOBLASTIN.
Mucocutaneous Lymph Node Syndrome
An acute, febrile, mucocutaneous condition accompanied by swelling of cervical lymph nodes in infants and young children. The principal symptoms are fever, congestion of the ocular conjunctivae, reddening of the lips and oral cavity, protuberance of tongue papillae, and edema or erythema of the extremities.
Polyarteritis Nodosa
A form of necrotizing non-granulomatous inflammation occurring primarily in medium-sized ARTERIES, often with microaneurysms. It is characterized by muscle, joint, and abdominal pain resulting from arterial infarction and scarring in affected organs. Polyarteritis nodosa with lung involvement is called CHURG-STRAUSS SYNDROME.
About the M30 Code Range
The ICD-10 code M30 covers polyarteritis nodosa and related conditions, a group of disorders involving inflammation of medium-sized arteries throughout the body. These codes are used to classify different forms and manifestations of this systemic vasculitis, including variants affecting lungs, children, and mucocutaneous tissues.
The main code, M30.0, represents polyarteritis nodosa itself, which is sometimes also called primary systemic arteritis or vasculitis of medium sized vessels. This code helps identify cases where arteries become inflamed causing diverse symptoms like neuropathy, myopathy, or nephrotic syndrome. When lung involvement occurs, M30.1 is applied; this includes conditions such as Churg-Strauss syndrome or eosinophilic granulomatosis with polyangiitis. The pediatric form, known as juvenile polyarteritis, is captured by M30.2. M30.3 covers Kawasaki disease, a mucocutaneous lymph node syndrome linked to inflammation of coronary arteries and aneurysm risk. Other related necrotizing vasculitis types fall under M30.8. These precise ICD-10 codes provide essential tools for medical coders to document specific types of polyarteritis nodosa and its variants for accurate diagnosis, treatment, and statistical tracking.
Questions About This Page
How many billable codes are in the M30 range?
Of the 6 codes in this range, 5 are billable and valid for claim submission from October 1, 2025 through September 30, 2026. Category header codes group them but cannot be reported on claims.
What does the M30 range classify?
The range classifies polyarteritis nodosa and related conditions. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2026 ICD-10-CM Tabular List and order file, effective October 1, 2025 through September 30, 2026.
