Other necrotizing vasculopathies (M31) ICD-10-CM
The M31 code range covers other necrotizing vasculopathies with 16 ICD-10-CM diagnosis codes. 13 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Codes in the M31 Range 16 codes · 13 billable
- M31 Other necrotizing vasculopathiesNon-billable
- M31.0 Hypersensitivity angiitis
- M31.1 Thrombotic microangiopathyNon-billable
- M31.10 Thrombotic microangiopathy, unspecified
- M31.11 Hematopoietic stem cell transplantation-associated thrombotic microangiopathy [HSCT-TMA]
- M31.19 Other thrombotic microangiopathy
- M31.2 Lethal midline granuloma
- M31.3 Wegener's granulomatosisNon-billable
- M31.30 Wegener's granulomatosis without renal involvement
- M31.31 Wegener's granulomatosis with renal involvement
- M31.4 Aortic arch syndrome [Takayasu]
- M31.5 Giant cell arteritis with polymyalgia rheumatica
- M31.6 Other giant cell arteritis
- M31.7 Microscopic polyangiitis
- M31.8 Other specified necrotizing vasculopathies
- M31.9 Necrotizing vasculopathy, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the M31 range.
Aortic Arch Syndrome due to Takayasu Arteritis
Aortic arch syndrome caused by Takayasu arteritis.
Granuloma, Lethal Midline
A condition that is characterized by inflammation, ulceration, and perforation of the nose and the PALATE with progressive destruction of midline facial structures. This syndrome can be manifested in several diseases including the nasal type of EXTRANODAL NK-T-CELL LYMPHOMA and GRANULOMATOSIS WITH POLYANGIITIS.
Granulomatosis with Polyangiitis
A multisystemic disease of a complex genetic background. It is characterized by inflammation of the blood vessels (VASCULITIS) leading to damage in any number of organs. The common features include granulomatous inflammation of the RESPIRATORY TRACT and KIDNEYS. Most patients have measurable autoantibodies (ANTINEUTROPHIL CYTOPLASMIC ANTIBODIES) against MYELOBLASTIN.
Microscopic Polyangiitis
A primary systemic vasculitis of small- and some medium-sized vessels. It is characterized by a tropism for kidneys and lungs, positive association with anti-neutrophil cytoplasmic antibodies (ANCA), and a paucity of immunoglobulin deposits in vessel walls.
Necrotizing Vasculopathy
Disorders of blood vessels characterized by luminal narrowing due to intramural immune deposits.
Thrombotic Microangiopathies
Diseases that result in THROMBOSIS in MICROVASCULATURE. The two most prominent diseases are PURPURA, THROMBOTIC THROMBOCYTOPENIC; and HEMOLYTIC-UREMIC SYNDROME. Multiple etiological factors include VASCULAR ENDOTHELIAL CELL damage due to SHIGA TOXIN; FACTOR H deficiency; and aberrant VON WILLEBRAND FACTOR formation.
Vasculitis, Leukocytoclastic, Cutaneous
Disorder characterized by a vasculitic syndrome associated with exposure to an antigen such as a drug, infectious agent, or other foreign or endogenous substance. Its pathophysiology includes immune complex deposition and a wide range of skin lesions. Hypersensitivity or allergy is present in some but not all cases.
About the M31 Code Range
These blood vessel disorders appear within systemic connective tissue disorders. The category separates named conditions from other specified and unspecified forms.
M31.1 divides thrombotic microangiopathy into unspecified, stem cell transplantation-associated, and other forms. M31.3 separates Wegener's granulomatosis by whether the kidneys are involved. Giant cell arteritis has separate codes for cases with polymyalgia rheumatica, M31.5, and other cases, M31.6. Other subdivisions name conditions such as aortic arch syndrome and microscopic polyangiitis.
Questions About This Page
How many billable codes are in the M31 range?
Of the 16 codes in this range, 13 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the M31 range classify?
The range classifies other necrotizing vasculopathies. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
