M30.3 - Mucocutaneous lymph node syndrome [Kawasaki]

Version 2023
Short Description:Mucocutaneous lymph node syndrome [Kawasaki]
Long Description:Mucocutaneous lymph node syndrome [Kawasaki]
Status: Valid for Submission
Version:ICD-10-CM 2023
Code Classification:
  • Diseases of the musculoskeletal system and connective tissue (M00–M99)
    • Systemic connective tissue disorders (M30-M36)
      • Polyarteritis nodosa and related conditions (M30)

M30.3 is a billable ICD-10 code used to specify a medical diagnosis of mucocutaneous lymph node syndrome [kawasaki]. The code is valid during the fiscal year 2023 from October 01, 2022 through September 30, 2023 for the submission of HIPAA-covered transactions.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

Clinical Information

Index to Diseases and Injuries References

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for this diagnosis code are found in the injuries and diseases index:

Convert to ICD-9 Code

Source ICD-10 CodeTarget ICD-9 Code
M30.3446.1 - Mucocutan lymph node syn

Patient Education

Kawasaki Disease

What is Kawasaki disease?

Kawasaki disease is a rare illness that usually affects small children. Other names for it are Kawasaki syndrome and mucocutaneous lymph node syndrome. It is a type of vasculitis, which is inflammation of the blood vessels. Kawasaki disease is serious, but most children can fully recover if they are treated right away.

What causes Kawasaki disease?

Kawasaki disease happens when the immune system injures the blood vessels by mistake. Researchers do not fully know why this happens. But when it does, the blood vessels become inflamed and can narrow or close off.

Genetics may play a role in Kawasaki disease. There may also be environmental factors, such as infections. It does not seem to be contagious. This means that it cannot be passed from one child to another.

Who is at risk for Kawasaki disease?

Kawasaki disease usually affects children under the age of 5. But older children and adults can sometimes get it. It is more common in boys than girls. It can affect children of any race, but those with Asian or Pacific Islander descent are more likely to get it.

What are the symptoms of Kawasaki disease?

The symptoms of Kawasaki disease may include:

What other problems can Kawasaki disease cause?

Sometimes Kawasaki disease can affect the walls of the coronary arteries. These arteries bring supply blood and oxygen to your heart. This can lead to:

Kawasaki disease can also affect other parts of the body, including the brain and nervous system, the immune system, and the digestive system.

How is Kawasaki disease diagnosed?

There is no specific test for Kawasaki disease. To make a diagnosis, your child's health care provider may use many tools:

What are the treatments for Kawasaki disease?

Kawasaki disease is usually treated in the hospital with an intravenous (IV) dose of immunoglobulin (IVIG). Aspirin may also be part of the treatment. But do not give your child aspirin unless the health care provider tells you to. Aspirin can cause Reye syndrome in children. This is a rare, serious illness that can affect the brain and liver.

Usually treatment works. But if it is not working well enough, the provider may also give your child other medicines to fight the inflammation. If the disease affects your child's heart, he or she might need additional medicines, surgery, or other medical procedures.

[Learn More in MedlinePlus]

Kawasaki disease

Kawasaki disease is a sudden and time-limited (acute) illness that affects infants and young children. Affected children develop a prolonged fever lasting several days, a skin rash, and swollen lymph nodes in the neck (cervical lymphadenopathy). They also develop redness in the whites of the eyes (conjunctivitis) and redness (erythema) of the lips, lining of the mouth (oral mucosa), tongue, palms of the hands, and soles of the feet.

Without treatment, 15 to 25 percent of individuals with Kawasaki disease develop bulging and thinning of the walls of the arteries that supply blood to the heart muscle (coronary artery aneurysms) or other damage to the coronary arteries, which can be life-threatening.

[Learn More in MedlinePlus]

Code History