2026 ICD-10-CM Diagnosis Code J84.89Other specified interstitial pulmonary diseases
ICD-10-CM Codes›J00–J99›J80-J84›J84
- Billable — Valid for Submission
- Chronic Condition
J84.89 is a billable ICD-10-CM diagnosis code for other specified interstitial pulmonary diseases. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 196 through 198. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified lower respiratory disease.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Acute endogenous lipoid pneumonitis
- Cholesterol pneumonitis
- Chronic chemical respiratory disease
- Chronic endogenous lipoid pneumonitis
- Chronic pneumonitis of infancy
- Deficiency of DNA repair
- Diffuse pulmonary meningotheliomatosis
- DNA repair
- Endogenous lipoid pneumonitis
- GIP - Giant cell interstitial pneumonitis
- Interstitial lung disease due to ABCA3 deficiency
- Interstitial pneumonitis
- Lipoid pneumonitis
- Lung disease, immunodeficiency, chromosome breakage syndrome
- Organized pneumonia
- Usual interstitial pneumonitis
- Vinyard sprayers' lung
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Inclusion Terms
- Endogenous lipoid pneumonia
- Interstitial pneumonitis
- Non-specific interstitial pneumonitis NOS
- Organizing pneumonia NOS
Code First
Use Additional Code
Type 1 Excludes
- cryptogenic organizing pneumonia J84.116
- idiopathic non-specific interstitial pneumonitis J84.113
- lipoid pneumonia, exogenous or unspecified J69.1
- lymphoid interstitial pneumonia J84.2
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
Certain conditions have both an underlying etiology and multiple body system manifestations due to the underlying etiology. For such conditions, the ICD-10-CM has a coding convention that requires the underlying condition be sequenced first followed by the manifestation. Wherever such a combination exists, there is a "use additional code" note at the etiology code, and a "code first" note at the manifestation code. These instructional notes indicate the proper sequencing order of the codes, etiology followed by manifestation.
The “use additional code” indicates that a secondary code could be used to further specify the patient’s condition. This note is not mandatory and is only used if enough information is available to assign an additional code.
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- Bronchiolitis (acute) (infective) (subacute) - J21.9
- obliterans - See Also: Bronchiolitis, obliterative; - J44.81
- with organizing pneumonia (BOOP) - J84.89
- Disease, diseased - See Also: Syndrome;
- interstitial - J84.9
- specified NEC - J84.89
- Pneumonia (acute) (double) (migratory) (purulent) (septic) (unresolved) - J18.9
- bronchiolitis obliterans organized (BOOP) - J84.89
- broncho-, bronchial (confluent) (croupous) (diffuse) (disseminated) (hemorrhagic) (involving lobes) (lobar) (terminal) - J18.0
- lipid, lipoid - J69.1
- endogenous - J84.89
- cholesterol - J84.89
- interstitial - J84.9
- non-specific - J84.89
- lipid, lipoid (exogenous) - J69.1
- endogenous - J84.89
- organizing - J84.89
- Pneumonitis (acute) (primary) - See Also: Pneumonia; - J98.4
- cholesterol - J84.89
- interstitial (chronic) - J84.89
- non-specific - J84.89
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- BOOP(bronchiolitis obliterans organized pneumonia)
- Bronchiolitis(acute) (infective) (subacute)
- obliterans
- with organizing pneumonia (BOOP)
- Disease, diseased
- lung
- interstitial
- specified NEC
- Pneumonia(acute) (double) (migratory) (purulent) (septic) (unresolved)
- bronchiolitis obliterans organized (BOOP)
- Pneumonia(acute) (double) (migratory) (purulent) (septic) (unresolved)
- broncho-, bronchial (confluent) (croupous) (diffuse) (disseminated) (hemorrhagic) (involving lobes) (lobar) (terminal)
- lipid, lipoid
- endogenous
- Pneumonia(acute) (double) (migratory) (purulent) (septic) (unresolved)
- cholesterol
- Pneumonia(acute) (double) (migratory) (purulent) (septic) (unresolved)
- interstitial
- non-specific
- Pneumonia(acute) (double) (migratory) (purulent) (septic) (unresolved)
- lipid, lipoid (exogenous)
- endogenous
- Pneumonia(acute) (double) (migratory) (purulent) (septic) (unresolved)
- organizing
- Pneumonitis(acute) (primary)
- cholesterol
- Pneumonitis(acute) (primary)
- interstitial (chronic)
- Pneumonitis(acute) (primary)
- interstitial (chronic)
- non-specific
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
DNA End-Joining Repair
the repair of double-strand dna breaks by rejoining the broken ends of dna to each other directly.DNA Repair
the removal of dna lesions and/or restoration of intact dna strands without base pair mismatches, intrastrand or interstrand crosslinks, or discontinuities in the dna sugar-phosphate backbones.DNA Repair Enzymes
enzymes that are involved in the reconstruction of a continuous two-stranded dna molecule without mismatch from a molecule, which contained damaged regions.DNA Repair-Deficiency Disorders
disorders resulting from defective dna repair processes or the associated cellular responses to dna damage.O(6)-Methylguanine-DNA Methyltransferase
an enzyme that transfers methyl groups from o(6)-methylguanine, and other methylated moieties of dna, to a cysteine residue in itself, thus repairing alkylated dna in a single-step reaction. ec 2.1.1.63.Rad52 DNA Repair and Recombination Protein
a dna-binding protein that mediates dna repair of double strand breaks, and homologous recombination.Recombinational DNA Repair
repair of dna damage by exchange of dna between matching sequences, usually between the allelic dna (alleles) of sister chromatids.DNA
a deoxyribonucleotide polymer that is the primary genetic material of all cells. eukaryotic and prokaryotic organisms normally contain dna in a double-stranded state, yet several important biological processes transiently involve single-stranded regions. dna, which consists of a polysugar-phosphate backbone possessing projections of purines (adenine and guanine) and pyrimidines (thymine and cytosine), forms a double helix that is held together by hydrogen bonds between these purines and pyrimidines (adenine to thymine and guanine to cytosine).
Patient EducationClinical
Interstitial Lung Diseases
Interstitial lung disease is the name for a large group of diseases that inflame or scar the lungs. The inflammation and scarring make it hard to get enough oxygen. The scarring is called pulmonary fibrosis.
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert J84.89 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About J84.89Overview
Is J84.89 (Other specified interstitial pulmonary diseases) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report other specified interstitial pulmonary diseases on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does J84.89 group to?
When other specified interstitial pulmonary diseases is the principal diagnosis on an inpatient stay, it groups to MS-DRG 196, 197, 198, with relative weights from 0.7162 to 1.8872 depending on complications. Higher weights mean higher Medicare reimbursement.
What is the ICD-9 equivalent of J84.89?
Under the General Equivalence Mappings, other specified interstitial pulmonary diseases converts to ICD-9-CM 515 (postinflam pulm fibrosis). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.
