1. Home
  2. ICD-10-CM Codes
  3. J00–J99
  4. J80-J84
  5. Other interstitial pulmonary diseases (J84)

Other interstitial pulmonary diseases (J84)

    • ICD-10 Index

      • Diseases of the respiratory system (J00–J99)

        • Other respiratory diseases principally affecting the interstitium (J80-J84)

            • Other interstitial pulmonary diseases (J84)
            • J84 - Other interstitial pulmonary diseases NON-BILLABLE CODE
            • J84.0 - Alveolar and parieto-alveolar conditions NON-BILLABLE CODE
            • J84.01 - Alveolar proteinosis BILLABLE CODE
            • J84.02 - Pulmonary alveolar microlithiasis BILLABLE CODE
            • J84.03 - Idiopathic pulmonary hemosiderosis BILLABLE CODE
            • J84.09 - Other alveolar and parieto-alveolar conditions BILLABLE CODE
            • J84.1 - Other interstitial pulmonary diseases with fibrosis NON-BILLABLE CODE
            • J84.10 - Pulmonary fibrosis, unspecified BILLABLE CODE
            • J84.11 - Idiopathic interstitial pneumonia NON-BILLABLE CODE
            • J84.111 - Idiopathic interstitial pneumonia, not otherwise specified BILLABLE CODE
            • J84.112 - Idiopathic pulmonary fibrosis BILLABLE CODE
            • J84.113 - Idiopathic non-specific interstitial pneumonitis BILLABLE CODE
            • J84.114 - Acute interstitial pneumonitis BILLABLE CODE
            • J84.115 - Respiratory bronchiolitis interstitial lung disease BILLABLE CODE
            • J84.116 - Cryptogenic organizing pneumonia BILLABLE CODE
            • J84.117 - Desquamative interstitial pneumonia BILLABLE CODE
            • J84.17 - Oth interstit pulmon dis w fibrosis in dis classd elswhr NON-BILLABLE CODE
            • J84.170 - Interstit lung dis w progr fibrotic phenotype dis classd e BILLABLE CODE
            • J84.178 - Oth interstit pulmon dis with fibrosis in dis classd elswhr BILLABLE CODE
            • J84.2 - Lymphoid interstitial pneumonia BILLABLE CODE
            • J84.8 - Other specified interstitial pulmonary diseases NON-BILLABLE CODE
            • J84.81 - Lymphangioleiomyomatosis BILLABLE CODE
            • J84.82 - Adult pulmonary Langerhans cell histiocytosis BILLABLE CODE
            • J84.83 - Surfactant mutations of the lung BILLABLE CODE
            • J84.84 - Other interstitial lung diseases of childhood NON-BILLABLE CODE
            • J84.841 - Neuroendocrine cell hyperplasia of infancy BILLABLE CODE
            • J84.842 - Pulmonary interstitial glycogenosis BILLABLE CODE
            • J84.843 - Alveolar capillary dysplasia with vein misalignment BILLABLE CODE
            • J84.848 - Other interstitial lung diseases of childhood BILLABLE CODE
            • J84.89 - Other specified interstitial pulmonary diseases BILLABLE CODE
            • J84.9 - Interstitial pulmonary disease, unspecified BILLABLE CODE

Clinical Information for Other interstitial pulmonary diseases (J84)

Idiopathic Pulmonary Fibrosis - A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

Lymphangioleiomyomatosis - A disease characterized by the progressive invasion of SMOOTH MUSCLE CELLS into the LYMPHATIC VESSELS, and the BLOOD VESSELS. The majority of the cases occur in the LUNGS of women of child-bearing age, eventually blocking the flow of air, blood, and lymph. The common symptom is shortness of breath (DYSPNEA).

Cryptogenic Organizing Pneumonia - An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a "pneumonia-like" illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts.

Asbestosis - A form of pneumoconiosis caused by inhalation of asbestos fibers which elicit potent inflammatory responses in the parenchyma of the lung. The disease is characterized by interstitial fibrosis of the lung, varying from scattered sites to extensive scarring of the alveolar interstitium.

Idiopathic Pulmonary Fibrosis - A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.

Pulmonary Fibrosis - A process in which normal lung tissues are progressively replaced by FIBROBLASTS and COLLAGEN causing an irreversible loss of the ability to transfer oxygen into the bloodstream via PULMONARY ALVEOLI. Patients show progressive DYSPNEA finally resulting in death.

Invasive Pulmonary Aspergillosis - Lung infections with the invasive forms of ASPERGILLUS, usually after surgery, transplantation, prolonged NEUTROPENIA or treatment with high-doses of CORTICOSTEROIDS. Invasive pulmonary aspergillosis can progress to CHRONIC NECROTIZING PULMONARY ASPERGILLOSIS or hematogenous spread to other organs.

Pulmonary Aspergillosis - Infections of the respiratory tract with fungi of the genus ASPERGILLUS.

Dyspnea - Difficult or labored breathing.

Aspergillus - A genus of mitosporic fungi containing about 100 species and eleven different teleomorphs in the family Trichocomaceae.

Dyspnea - Difficult or labored breathing.

Instructional Notations

Type 1 Excludes Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • drug-induced interstitial lung disorders J70.2 J70.4
  • interstitial emphysema J98.2

Type 2 Excludes Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.

  • lung diseases due to external agents J60 J70