Other interstitial pulmonary diseases (J84) ICD-10-CM
The J84 code range covers other interstitial pulmonary diseases with 31 ICD-10-CM diagnosis codes. 24 of them are billable and valid for claim submission in fiscal year 2027, and the category headers group them but cannot themselves be billed.
Code Also
A "code also" note instructs that two codes may be required to fully describe a condition, but this note does not provide sequencing direction.
- , if applicable, associated condition
Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.
Type 2 Excludes
A type 2 excludes note represents "Not included here". An excludes2 note indicates that the condition excluded is not part of the condition represented by the code, but a patient may have both conditions at the same time. When an Excludes2 note appears under a code, it is acceptable to use both the code and the excluded code together, when appropriate.
Codes in the J84 Range 31 codes · 24 billable
- J84 Other interstitial pulmonary diseasesNon-billable
- J84.0 Alveolar and parieto-alveolar conditionsNon-billable
- J84.01 Alveolar proteinosis
- J84.02 Pulmonary alveolar microlithiasis
- J84.03 Idiopathic pulmonary hemosiderosis
- J84.09 Other alveolar and parieto-alveolar conditions
- J84.1 Other interstitial pulmonary diseases with fibrosisNon-billable
- J84.10 Pulmonary fibrosis, unspecified
- J84.11 Idiopathic interstitial pneumoniaNon-billable
- J84.111 Idiopathic interstitial pneumonia, not otherwise specified
- J84.112 Idiopathic pulmonary fibrosis
- J84.113 Idiopathic non-specific interstitial pneumonitis
- J84.114 Acute interstitial pneumonitis
- J84.115 Respiratory bronchiolitis interstitial lung disease
- J84.116 Cryptogenic organizing pneumonia
- J84.117 Desquamative interstitial pneumonia
- J84.17 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhereNon-billable
- J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
- J84.178 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
- J84.2 Lymphoid interstitial pneumonia
- J84.8 Other specified interstitial pulmonary diseasesNon-billable
- J84.81 Lymphangioleiomyomatosis
- J84.82 Adult pulmonary Langerhans cell histiocytosis
- J84.83 Surfactant mutations of the lung
- J84.84 Other interstitial lung diseases of childhoodNon-billable
- J84.841 Neuroendocrine cell hyperplasia of infancy
- J84.842 Pulmonary interstitial glycogenosis
- J84.843 Alveolar capillary dysplasia with vein misalignment
- J84.848 Other interstitial lung diseases of childhood
- J84.89 Other specified interstitial pulmonary diseases
- J84.9 Interstitial pulmonary disease, unspecified
Clinical Terms in This Code Range
Definitions from the National Library of Medicine for conditions coded in the J84 range.
Cryptogenic Organizing Pneumonia
An interstitial lung disease of unknown etiology, occurring between 21-80 years of age. It is characterized by a dramatic onset of a pneumonia-like illness with cough, fever, malaise, fatigue, and weight loss. Pathological features include prominent interstitial inflammation without collagen fibrosis, diffuse fibroblastic foci, and no microscopic honeycomb change. There is excessive proliferation of granulation tissue within small airways and alveolar ducts.
Desquamative Interstitial Pneumonia
A rare idiopathic interstitial pneumonia characterized by accumulation of macrophages in alveolar spaces and interstitial inflammation. It usually occurs in smokers. Some patients develop progressive interstitial lung fibrosis.
Hamman-Rich Syndrome
Acute idiopathic interstitial pneumonitis characterized by diffuse PULMONARY ALVEOLI damage with uniform edematous connective tissue proliferation. It is often associated with extensive fibroblastic distortion of the lung parenchyma and leads to ADULT RESPIRATORY DISTRESS SYNDROME in later stages.
Idiopathic Interstitial Pneumonias
A group of interstitial lung diseases with no known etiology. There are several entities with varying patterns of inflammation and fibrosis. They are classified by their distinct clinical-radiological-pathological features and prognosis. They include IDIOPATHIC PULMONARY FIBROSIS; CRYPTOGENIC ORGANIZING PNEUMONIA; and others.
Idiopathic Pulmonary Fibrosis
A common interstitial lung disease of unknown etiology, usually occurring between 50-70 years of age. Clinically, it is characterized by an insidious onset of breathlessness with exertion and a nonproductive cough, leading to progressive DYSPNEA. Pathological features show scant interstitial inflammation, patchy collagen fibrosis, prominent fibroblast proliferation foci, and microscopic honeycomb change.
Lymphangioleiomyomatosis
A disease characterized by the progressive invasion of SMOOTH MUSCLE CELLS into the LYMPHATIC VESSELS, and the BLOOD VESSELS. The majority of the cases occur in the LUNGS of women of child-bearing age, eventually blocking the flow of air, blood, and lymph. The common symptom is shortness of breath (DYSPNEA).
Neuroendocrine Cell Hyperplasia of Infancy
A form of interstitial lung disease characterized by increased numbers of pulmonary neuroendocrine cells, typically presenting in the first year of life with persistent tachypnea, retractions, crackles and hypoxemia that has a highly specific chest CT pattern that includes ground-glass opacities and air-trapping.
Pulmonary Fibrosis
A process in which normal lung tissues are progressively replaced by FIBROBLASTS and COLLAGEN causing an irreversible loss of the ability to transfer oxygen into the bloodstream via PULMONARY ALVEOLI. Patients show progressive DYSPNEA finally resulting in death.
About the J84 Code Range
These lung diseases include conditions involving the alveoli, or air sacs, and interstitial diseases with fibrosis, or scarring.
J84.0 groups alveolar and parieto-alveolar conditions by named type. J84.1 groups diseases with fibrosis. Its subdivisions distinguish named forms of idiopathic interstitial pneumonia, which has no known cause, and fibrosis in diseases classified elsewhere.
J84.2 identifies lymphoid interstitial pneumonia. J84.8 groups other specified diseases, including childhood interstitial lung diseases. J84.9 identifies interstitial pulmonary disease when the type is unspecified.
Questions About This Page
How many billable codes are in the J84 range?
Of the 31 codes in this range, 24 are billable and valid for claim submission from October 1, 2026 through September 30, 2027. Category header codes group them but cannot be reported on claims.
What does the J84 range classify?
The range classifies other interstitial pulmonary diseases. Each code links to its own reference page with billing status, MS-DRG grouping, coding notes, and clinical information.
Related References
Source: CMS FY 2027 ICD-10-CM Tabular List and order file, effective October 1, 2026 through September 30, 2027.
