2021 ICD-10-CM Code J84.1

Other interstitial pulmonary diseases with fibrosis

Version 2021

Not Valid for Submission

J84.1 is a non-specific and non-billable diagnosis code code, consider using a code with a higher level of specificity for a diagnosis of other interstitial pulmonary diseases with fibrosis. The code is not specific and is NOT valid for the year 2021 for the submission of HIPAA-covered transactions. Category or Header define the heading of a category of codes that may be further subdivided by the use of 4th, 5th, 6th or 7th characters.

ICD-10:J84.1
Short Description:Other interstitial pulmonary diseases with fibrosis
Long Description:Other interstitial pulmonary diseases with fibrosis

Code Classification

Specific Coding for Other interstitial pulmonary diseases with fibrosis

Non-specific codes like J84.1 require more digits to indicate the appropriate level of specificity. Consider using any of the following ICD-10 codes with a higher level of specificity when coding for other interstitial pulmonary diseases with fibrosis:

  • BILLABLE CODE - Use J84.10 for Pulmonary fibrosis, unspecified
  • NON-BILLABLE CODE - J84.11 for Idiopathic interstitial pneumonia
  • BILLABLE CODE - Use J84.111 for Idiopathic interstitial pneumonia, not otherwise specified
  • BILLABLE CODE - Use J84.112 for Idiopathic pulmonary fibrosis
  • BILLABLE CODE - Use J84.113 for Idiopathic non-specific interstitial pneumonitis
  • BILLABLE CODE - Use J84.114 for Acute interstitial pneumonitis
  • BILLABLE CODE - Use J84.115 for Respiratory bronchiolitis interstitial lung disease
  • BILLABLE CODE - Use J84.116 for Cryptogenic organizing pneumonia
  • BILLABLE CODE - Use J84.117 for Desquamative interstitial pneumonia
  • NON-BILLABLE CODE - J84.17 for Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
  • BILLABLE CODE - Use J84.170 for Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
  • BILLABLE CODE - Use J84.178 for Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code J84.1:


Type 1 Excludes

Type 1 Excludes
A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

Information for Patients


Interstitial Lung Diseases

Interstitial lung disease is the name for a large group of diseases that inflame or scar the lungs. The inflammation and scarring make it hard to get enough oxygen. The scarring is called pulmonary fibrosis.

Breathing in dust or other particles in the air is responsible for some types of interstitial lung diseases. Specific types include

Other causes include autoimmune diseases or occupational exposures to molds, gases, or fumes. Some types of interstitial lung disease have no known cause.

Treatment depends on the type of exposure and the stage of the disease. It may involve medicines, oxygen therapy, or a lung transplant in severe cases.


[Learn More in MedlinePlus]

Pulmonary Fibrosis

Also called: IPF, Idiopathic pulmonary fibrosis

Pulmonary fibrosis is a condition in which the tissue deep in your lungs becomes scarred over time. This tissue gets thick and stiff. That makes it hard for you to catch your breath, and your blood may not get enough oxygen.

Causes of pulmonary fibrosis include environmental pollutants, some medicines, some connective tissue diseases, and interstitial lung disease. Interstitial lung disease is the name for a large group of diseases that inflame or scar the lungs. In most cases, the cause cannot be found. This is called idiopathic pulmonary fibrosis.

Symptoms include

Your doctor may use your medical history, imaging tests, a biopsy, and lung function tests to diagnose pulmonary fibrosis. There is no cure. Treatments can help with symptoms and improve your quality of life. They include medicines, oxygen therapy, pulmonary rehabilitation, or a lung transplant.

NIH: National Heart, Lung, and Blood Institute


[Learn More in MedlinePlus]

Code History

  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016 (First year ICD-10-CM implemented into the HIPAA code set)