Other respiratory diseases principally affecting the interstitium (J80-J84)
ICD-10 codes J80-J84 cover respiratory diseases primarily affecting the lung interstitium, a crucial tissue supporting lung function. These codes are used for conditions like acute respiratory distress, pulmonary edema, eosinophilic pneumonia, and various interstitial lung diseases involving fibrosis or inflammation.
This range includes J80 for acute respiratory distress syndrome, often called ARDS or known by synonyms such as postoperative pulmonary edema and acute respiratory distress due to vaping or COVID-19. Codes J81.0 and J81.1 specify acute and chronic pulmonary edema, conditions marked by fluid buildup in the lungs. Pulmonary eosinophilia, inflammation caused by eosinophils, is classified under J82, with subcodes documenting chronic and acute eosinophilic pneumonia and eosinophilic asthma. The J84 category addresses other interstitial lung disorders including idiopathic pulmonary fibrosis (J84.112), lymphoid interstitial pneumonia (J84.2), and rare diseases like lymphangioleiomyomatosis (J84.81). These codes help target complex lung diseases where tissue scarring, inflammation, or genetic defects impair breathing and oxygen exchange.
Diseases of the respiratory system (J00–J99)
Other respiratory diseases principally affecting the interstitium (J80-J84)
- J80 Acute respiratory distress syndrome
Acute respiratory distress syndrome (J80)
J81 Pulmonary edema
- J81.0 Acute pulmonary edema
- J81.1 Chronic pulmonary edema
Pulmonary edema (J81)
J82 Pulmonary eosinophilia, not elsewhere classified
J82.8 Pulmonary eosinophilia, not elsewhere classified
- J82.81 Chronic eosinophilic pneumonia
- J82.82 Acute eosinophilic pneumonia
- J82.83 Eosinophilic asthma
- J82.89 Other pulmonary eosinophilia, not elsewhere classified
Pulmonary eosinophilia, not elsewhere classified (J82)
J84 Other interstitial pulmonary diseases
J84.0 Alveolar and parieto-alveolar conditions
- J84.01 Alveolar proteinosis
- J84.02 Pulmonary alveolar microlithiasis
- J84.03 Idiopathic pulmonary hemosiderosis
- J84.09 Other alveolar and parieto-alveolar conditions
J84.1 Other interstitial pulmonary diseases with fibrosis
- J84.10 Pulmonary fibrosis, unspecified
J84.11 Idiopathic interstitial pneumonia
- J84.111 Idiopathic interstitial pneumonia, not otherwise specified
- J84.112 Idiopathic pulmonary fibrosis
- J84.113 Idiopathic non-specific interstitial pneumonitis
- J84.114 Acute interstitial pneumonitis
- J84.115 Respiratory bronchiolitis interstitial lung disease
- J84.116 Cryptogenic organizing pneumonia
- J84.117 Desquamative interstitial pneumonia
J84.17 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
- J84.170 Interstitial lung disease with progressive fibrotic phenotype in diseases classified elsewhere
- J84.178 Other interstitial pulmonary diseases with fibrosis in diseases classified elsewhere
- J84.2 Lymphoid interstitial pneumonia
J84.8 Other specified interstitial pulmonary diseases
- J84.81 Lymphangioleiomyomatosis
- J84.82 Adult pulmonary Langerhans cell histiocytosis
- J84.83 Surfactant mutations of the lung
J84.84 Other interstitial lung diseases of childhood
- J84.841 Neuroendocrine cell hyperplasia of infancy
- J84.842 Pulmonary interstitial glycogenosis
- J84.843 Alveolar capillary dysplasia with vein misalignment
- J84.848 Other interstitial lung diseases of childhood
- J84.89 Other specified interstitial pulmonary diseases
- J84.9 Interstitial pulmonary disease, unspecified
Other interstitial pulmonary diseases (J84)