2026 ICD-10-CM Diagnosis Code G91.2(Idiopathic) normal pressure hydrocephalus
ICD-10-CM Codes›G00–G99›G89-G99›G91
- Billable — Valid for Submission
- Chronic Condition
G91.2 is a billable ICD-10-CM diagnosis code for (idiopathic) normal pressure hydrocephalus. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as dementia associated with normal pressure hydrocephalus. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other nervous system disorders (neither hereditary nor degenerative).
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Dementia associated with normal pressure hydrocephalus
- Normal pressure hydrocephalus
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Inclusion Terms
- Normal pressure hydrocephalus NOS
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Hydrocephalus(acquired) (external) (internal) (malignant) (recurrent)
- normal pressure
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Dandy-Walker Syndrome
a congenital abnormality of the central nervous system marked by failure of the midline structures of the cerebellum to develop, dilation of the fourth ventricle, and upward displacement of the transverse sinuses, tentorium, and torcula. clinical features include occipital bossing, progressive head enlargement, bulging of anterior fontanelle, papilledema, ataxia, gait disturbances, nystagmus, and intellectual compromise. (from menkes, textbook of child neurology, 5th ed, pp294-5)Hydrocephalus
excessive accumulation of cerebrospinal fluid within the cranium which may be associated with dilation of cerebral ventricles, intracranial hypertension; headache; lethargy; urinary incontinence; and ataxia.Hydrocephalus, Normal Pressure
a form of compensated hydrocephalus characterized clinically by a slowly progressive gait disorder (see gait disorders, neurologic), progressive intellectual decline, and urinary incontinence. spinal fluid pressure tends to be in the high normal range. this condition may result from processes which interfere with the absorption of csf including subarachnoid hemorrhage, chronic meningitis, and other conditions. (from adams et al., principles of neurology, 6th ed, pp631-3)Walker-Warburg Syndrome
rare autosomal recessive lissencephaly type 2 associated with congenital muscular dystrophy and eye anomalies (e.g., retinal detachment; cataract; microphthalmos). it is often associated with additional brain malformations such as hydrocephaly and cerebellar hypoplasia and is the most severe form of the group of related syndromes (alpha-dystroglycanopathies) with common congenital abnormalities in the brain, eye and muscle development.
Patient EducationClinical
Hydrocephalus
Hydrocephalus is the buildup of too much cerebrospinal fluid in the brain. Normally, this fluid cushions your brain. When you have too much, though, it puts harmful pressure on your brain.
Read the full article at MedlinePlus
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Convert G91.2 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About G91.2Overview
Is G91.2 (Hydrocephalus) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report (idiopathic) normal pressure hydrocephalus on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What is the ICD-9 equivalent of G91.2?
Under the General Equivalence Mappings, (idiopathic) normal pressure hydrocephalus converts to ICD-9-CM 331.5 (norml pressure hydroceph). The mapping is a direct match.
Footnotes
[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.
