2026 ICD-10-CM Diagnosis Code G71.29Other congenital myopathy

ICD-10-CM Codes›G00–G99›G70-G73›G71

ICD-10-CM G71.29
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G71.29 is a billable ICD-10-CM diagnosis code for other congenital myopathy. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.

Code Identity

ICD-10-CM Code
G71.29
Billable Status
Yes — Valid for Submission
Code Describes
Other congenital myopathy
Short Description
Other congenital myopathy
Same as the full description in the CMS dataset.
Parent Code
G71.2
Congenital myopathies

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG70-G73Diseases of myoneural junction and muscle
CategoryG71Primary disorders of muscles
This CodeG71.29Other congenital myopathy

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Actin accumulation myopathy
  • Akinesia
  • Antenatal multi-minicore disease with arthrogryposis multiplex congenita
  • Autosomal dominant central core disease
  • Autosomal dominant congenital fiber-type disproportion myopathy due to ACTA1 mutation
  • Autosomal dominant congenital fiber-type disproportion myopathy due to SELENON mutation
  • Autosomal dominant congenital fiber-type disproportion myopathy due to TPM3 mutation
  • Autosomal recessive central core disease
  • Autosomal recessive congenital fiber-type disproportion myopathy due to ACTA1 mutation
  • Autosomal recessive congenital fiber-type disproportion myopathy due to SELENON mutation
  • Autosomal recessive congenital fiber-type disproportion myopathy due to TPM3 mutation
  • Benign congenital myopathy
  • Benign Samaritan congenital myopathy
  • Bethlem myopathy
  • Cap myopathy
  • Central core disease
  • Congenital fiber-type disproportion myopathy due to ACTA1 mutation
  • Congenital fiber-type disproportion myopathy due to MYH7 mutation
  • Congenital fiber-type disproportion myopathy due to SELENON mutation
  • Congenital fiber-type disproportion myopathy due to TPM3 mutation
  • Congenital fiber-type disproportion myopathy due to ZAK mutation
  • Congenital generalized hypercontractile muscle stiffness syndrome
  • Congenital lethal myopathy Compton North type
  • Congenital multi-minicore disease with external ophthalmoplegia
  • Congenital myopathy with abnormal subcellular organelles
  • Congenital myopathy with fiber type disproportion
  • Congenital myopathy with internal nuclei and atypical cores
  • Congenital myopathy with myasthenic-like onset
  • Congenital myopathy with reduced type 2 muscle fibers
  • Congenital myopathy with uniform fiber type
  • Congenital nonprogressive myopathy with Moebius and Robin sequences
  • Cylindrical spirals myopathy
  • Desmin related myopathy with Mallory body-like inclusions
  • Desmin-related myofibrillar myopathy
  • Early-onset myopathy, areflexia, respiratory distress, dysphagia syndrome
  • Inclusion body myopathy with early-onset Paget disease and frontotemporal dementia
  • Intellectual disability, cataract, calcified pinna, myopathy syndrome
  • Intellectual disability, myopathy, short stature, endocrine defect syndrome
  • Multi-core congenital myopathy
  • Muscle filaminopathy
  • Myopathy with abnormality of histochemical fiber type
  • Myopathy with cytoplasmic inclusions
  • Myopathy with hexagonally cross-linked tubular arrays
  • Myopathy with tubular aggregates
  • Myopathy with type I hypotrophy
  • Myosclerosis
  • Myosin storage myopathy
  • Nemaline myopathy
  • Nemaline myopathy, early onset type
  • Pinnal calcification
  • Proximal myopathy
  • Reducing-body myopathy
  • Sarcotubular myopathy
  • Zebra body myopathy

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Central core disease
  • Minicore disease
  • Multicore disease
  • Multiminicore disease

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Disease, diseased
      • central core
    • Disease, diseased
      • minicore
    • Disease, diseased
      • multicore
    • Disease, diseased
      • multiminicore
    • Disproportion
      • fiber-type
        • congenital
    • Myopathy
      • central core
    • Myopathy
      • hyaline body
    • Myopathy
      • myosin storage

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS018
Myopathies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Akinesia

    lack of movement.

  • Fetal Akinesia Deformation Sequence|FADS|Pena-Shokeir syndrome, Type 1

    a condition characterized by fetal akinesia and intrauterine growth restriction, that may be associated with mutation(s) in the rapsn or dok7 genes, encoding 43 kda receptor-associated protein of the synapse and protein dok-7, respectively.

Patient EducationClinical

Genetic Disorders

Genetic disorders are health conditions caused by changes (also called mutations or variants) in your genes. Genes are parts of DNA found in your cells that carry instructions for how your body grows, develops, and functions. Many genes tell your body how to make proteins, which are needed for your body to work properly.

The full article covers:

  • What are genetic disorders?
  • What causes genetic disorders?
  • What are the types of genetic disorders?
  • What are the different ways a genetic disorder can be inherited?
  • How are genetic disorders diagnosed?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement G71.29 replaces the following previously assigned code(s):

  • G71.2 - Congenital myopathies
FY 2021AddedAdded to the ICD-10-CM code setEffective October 1, 2020.
FY 2022–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G71.29Overview

Is G71.29 (Congenital myopathies) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other congenital myopathy on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.