ICD-10-CM Code G71.11

Myotonic muscular dystrophy

Version 2020 Billable Code

Valid for Submission

G71.11 is a billable code used to specify a medical diagnosis of myotonic muscular dystrophy. The code is valid for the year 2020 for the submission of HIPAA-covered transactions. The ICD-10-CM code G71.11 might also be used to specify conditions or terms like cardiomyopathy in myotonic dystrophy, congenital myotonic dystrophy, dilated cardiomyopathy secondary to muscular dystrophy, dilated cardiomyopathy secondary to myotonic dystrophy, dilated cardiomyopathy secondary to neuromuscular disorder, dystrophia myotonica facies, etc

ICD-10:G71.11
Short Description:Myotonic muscular dystrophy
Long Description:Myotonic muscular dystrophy

Tabular List of Diseases and Injuries

The Tabular List of Diseases and Injuries is a list of ICD-10 codes, organized "head to toe" into chapters and sections with guidance for inclusions, exclusions, descriptions and more. The following references are applicable to the code G71.11:

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Dystrophia myotonica Steinert
  • Myotonia atrophica
  • Myotonic dystrophy
  • Proximal myotonic myopathy (PROMM)
  • Steinert disease

Index to Diseases and Injuries

The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10 code(s). The following references for the code G71.11 are found in the index:


Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Cardiomyopathy in myotonic dystrophy
  • Congenital myotonic dystrophy
  • Dilated cardiomyopathy secondary to muscular dystrophy
  • Dilated cardiomyopathy secondary to myotonic dystrophy
  • Dilated cardiomyopathy secondary to neuromuscular disorder
  • Dystrophia myotonica facies
  • Proximal myotonic myopathy
  • Steinert myotonic dystrophy syndrome

Convert G71.11 to ICD-9

  • 359.21 - Myotonic musclr dystrphy

Code Classification

  • Diseases of the nervous system (G00–G99)
    • Diseases of myoneural junction and muscle (G70-G73)
      • Primary disorders of muscles (G71)

Code History

  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016
    (First year ICD-10-CM implemented into the HIPAA code set)
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020

Information for Patients


Muscular Dystrophy

Muscular dystrophy (MD) is a group of more than 30 inherited diseases. They all cause muscle weakness and muscle loss. Some forms of MD appear in infancy or childhood. Others may not appear until middle age or later. The different types can vary in whom they affect, which muscles they affect, and what the symptoms are. All forms of MD grow worse as the person's muscles get weaker. Most people with MD eventually lose the ability to walk.

There is no cure for muscular dystrophy. Treatments can help with the symptoms and prevent complications. They include physical and speech therapy, orthopedic devices, surgery, and medications. Some people with MD have mild cases that worsen slowly. Others cases are disabling and severe.

NIH: National Institute of Neurological Disorders and Stroke


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Myotonic dystrophy Myotonic dystrophy is part of a group of inherited disorders called muscular dystrophies. It is the most common form of muscular dystrophy that begins in adulthood.Myotonic dystrophy is characterized by progressive muscle wasting and weakness. People with this disorder often have prolonged muscle contractions (myotonia) and are not able to relax certain muscles after use. For example, a person may have difficulty releasing their grip on a doorknob or handle. Also, affected people may have slurred speech or temporary locking of their jaw.Other signs and symptoms of myotonic dystrophy include clouding of the lens of the eye (cataracts) and abnormalities of the electrical signals that control the heartbeat (cardiac conduction defects). In affected men, hormonal changes may lead to early balding and an inability to father a child (infertility). The features of this disorder often develop during a person's twenties or thirties, although they can occur at any age. The severity of the condition varies widely among affected people, even among members of the same family.There are two major types of myotonic dystrophy: type 1 and type 2. Their signs and symptoms overlap, although type 2 tends to be milder than type 1. The muscle weakness associated with type 1 particularly affects the lower legs, hands, neck, and face. Muscle weakness in type 2 primarily involves the muscles of the neck, shoulders, elbows, and hips. The two types of myotonic dystrophy are caused by mutations in different genes.A variation of type 1 myotonic dystrophy, called congenital myotonic dystrophy, is apparent at birth. Characteristic features include weak muscle tone (hypotonia), an inward- and upward-turning foot (clubfoot), breathing problems, delayed development, and intellectual disability. Some of these health problems can be life-threatening.
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