2027 ICD-10-CM Diagnosis Code G71.228Other centronuclear myopathy

ICD-10-CM Codes›G00–G99›G70-G73›G71

ICD-10-CM G71.228
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

G71.228 is a billable ICD-10-CM diagnosis code for other centronuclear myopathy. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 91 through 93. As a secondary diagnosis, it counts as a complication or comorbidity (CC) and moves an inpatient stay to a higher severity level within its MS-DRG family. It does not count, however, when the principal diagnosis is one of 22 closely related codes. Coders also document this condition as autosomal dominant centronuclear myopathy. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.

For Medicare Advantage risk adjustment, G71.228 maps to CMS-HCC Category 197 (Muscular Dystrophy) under the V28 model, adding a risk factor of about 0.426 for a community, non-dual, aged beneficiary in payment year 2027.

Code Identity

ICD-10-CM Code
G71.228
Billable Status
Yes — Valid for Submission
Code Describes
Other centronuclear myopathy
Short Description
Other centronuclear myopathy
Same as the full description in the CMS dataset.
Parent Code
Centronuclear myopathy

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG70-G73Diseases of myoneural junction and muscle
CategoryG71Primary disorders of muscles
This CodeG71.228Other centronuclear myopathy

Medicare Risk Adjustment (HCC)Billing

G71.228 maps to a payment category in the CMS-HCC model used to risk-adjust Medicare Advantage payments. Weights are the published community factors for payment year 2027.

CMS-HCC V28 Category (Payment Model)
HCC 197— Muscular Dystrophy
Payment HCC · PY 2027 one of 21 ICD-10-CM codes in this category
Risk Adjustment Factor (RAF) Weight
+0.426
community, non-dual, aged · ranges 0.145–0.681 across segments
Hierarchy
Top of its hierarchy
HCC 197 is not superseded by any other condition category
Prior Model (CMS-HCC V24)
HCC 76
V24 retired V28 pays 100% of MA risk scores since PY 2026
Other CMS Models
PACE (CMS-HCC V22): HCC 76 · ESRD (V21): HCC 76 · ESRD (V24): HCC 76
ESRD V21 weights: 0.062 dialysis, 0.296–0.544 functioning graft · ESRD V24 weights: 0.136 dialysis, 0.322–0.842 functioning graft
Part D (RxHCC)
Not mapped
G71.228 does not risk-adjust in the RxHCC prescription drug model

Source: CMS Payment Year 2027 risk adjustment mappings and model software. Weights are relative factors, not dollar amounts; a beneficiary's total RAF also includes demographics and interactions. Browse all CMS-HCC categories.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal dominant centronuclear myopathy
  • Autosomal recessive centronuclear myopathy
  • Myotubular myopathy

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to G71.228: its own notes plus those printed at G71.2, G71, and Chapter 6. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Autosomal centronuclear myopathy
  • Autosomal dominant centronuclear myopathy
  • Autosomal recessive centronuclear myopathy
  • Centronuclear myopathy, NOS

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From G71.2 Congenital myopathies applies to 5 codes
  • arthrogryposis multiplex congenita (Q74.3)
From G71 Primary disorders of muscles applies to 28 codes
  • arthrogryposis multiplex congenita (Q74.3)
  • metabolic disorders (E70-E88)
  • myositis (M60.-)
From Chapter 6 (G00-G99) Diseases of the nervous system applies to 700 codes
  • certain conditions originating in the perinatal period (P04-P96)
  • certain infectious and parasitic diseases (A00-B99)
  • complications of pregnancy, childbirth and the puerperium (O00-O9A)
  • congenital malformations, deformations, and chromosomal abnormalities (Q00-Q99)
  • endocrine, nutritional and metabolic diseases (E00-E88)
  • injury, poisoning and certain other consequences of external causes (S00-T88)
  • neoplasms (C00-D49)
  • symptoms, signs and abnormal clinical and laboratory findings, not elsewhere classified (R00-R94)

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name G71.228, its category, or a range that includes it.

Excludes2 1

These codes carry an Excludes2 note naming G71.228: its condition is not part of those codes, and both may be reported when the patient has both.

  • Block M60-M63 Disorders of muscles
    muscular dystrophies and myopathies (G71-G72) names G71-G72, which includes this code

Code First 1

These codes say to code first a condition named in the note, and G71.228 is one of the conditions named.

  • M62.84 Sarcopenia
    primary disorders of muscles (G71.-) names G71.-, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS018
Myopathies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Congenital Structural Myopathy

    a group of rare genetic muscle disorders characterized by hypotonia, muscle weakness, and delayed development of motor skills.

Patient EducationClinical

Centronuclear myopathy

Centronuclear myopathy is a condition characterized by muscle weakness (myopathy) and wasting (atrophy) in the skeletal muscles, which are the muscles used for movement. The severity of centronuclear myopathy varies among affected individuals, even among members of the same family.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement G71.228 replaces the following previously assigned code(s):

  • G71.2 - Congenital myopathies
FY 2021AddedAdded to the ICD-10-CM code setEffective October 1, 2020.
FY 2022–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About G71.228Overview

What is the ICD-10 code for other centronuclear myopathy?

The ICD-10-CM code for other centronuclear myopathy is G71.228 (sometimes written as G71228). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is G71.228 (Centronuclear myopathy) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other centronuclear myopathy on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does G71.228 group to?

When other centronuclear myopathy is the principal diagnosis on an inpatient stay, it groups to MS-DRG 91, 92, 93, with relative weights from 0.7783 to 1.7050 depending on complications. Higher weights mean higher Medicare reimbursement.

Is G71.228 a CC or MCC?

CMS lists G71.228 as a CC (complication or comorbidity) for FY 2027. Reported as a secondary diagnosis, it moves the inpatient stay to a higher-weighted DRG within its severity family. It does not count when the principal diagnosis is one of the 22 closely related codes in its exclusion list.

What HCC is G71.228?

G71.228 (other centronuclear myopathy) maps to CMS-HCC Category 197 (Muscular Dystrophy), commonly written as HCC 197, in the CMS-HCC V28 model used for Medicare Advantage risk adjustment in payment year 2027. It mapped to HCC 76 under the retired V24 model. It also maps in the PACE (CMS-HCC V22), ESRD (V21), and ESRD (V24) models. It does not map to any RxHCC in the Part D prescription drug model.

Does G71.228 risk-adjust for Medicare Advantage payment?

Yes. When documented and reported on a Medicare Advantage encounter, G71.228 adds a risk adjustment factor of about 0.426 to the beneficiary's RAF score for a community, non-dual, aged enrollee (published V28 weights range from 0.145 to 0.681 depending on the payment segment). HCC 197 sits at the top of its hierarchy, so no other condition category supersedes it. See the full factor table on the HCC 197 category page.