2026 ICD-10-CM Diagnosis Code G71.228Other centronuclear myopathy

ICD-10-CM Codes›G00–G99›G70-G73›G71

ICD-10-CM G71.228
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G71.228 is a billable ICD-10-CM diagnosis code for other centronuclear myopathy. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as autosomal dominant centronuclear myopathy. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.

Code Identity

ICD-10-CM Code
G71.228
Billable Status
Yes — Valid for Submission
Code Describes
Other centronuclear myopathy
Short Description
Other centronuclear myopathy
Same as the full description in the CMS dataset.
Parent Code
G71.22
Centronuclear myopathy

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG70-G73Diseases of myoneural junction and muscle
CategoryG71Primary disorders of muscles
This CodeG71.228Other centronuclear myopathy

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal dominant centronuclear myopathy
  • Autosomal recessive centronuclear myopathy
  • Myotubular myopathy

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Autosomal centronuclear myopathy
  • Autosomal dominant centronuclear myopathy
  • Autosomal recessive centronuclear myopathy
  • Centronuclear myopathy, NOS

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Myopathy
      • centronuclear
    • Myopathy
      • centronuclear
        • autosomal (dominant) (recessive)
    • Myopathy
      • centronuclear
        • other specified NEC

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS018
Myopathies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Centronuclear myopathy

Centronuclear myopathy is a condition characterized by muscle weakness (myopathy) and wasting (atrophy) in the skeletal muscles, which are the muscles used for movement. The severity of centronuclear myopathy varies among affected individuals, even among members of the same family.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement G71.228 replaces the following previously assigned code(s):

  • G71.2 - Congenital myopathies
FY 2021AddedAdded to the ICD-10-CM code setEffective October 1, 2020.
FY 2022–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G71.228Overview

Is G71.228 (Centronuclear myopathy) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other centronuclear myopathy on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.