2026 ICD-10-CM Diagnosis Code G71.220X-linked myotubular myopathy

ICD-10-CM Codes›G00–G99›G70-G73›G71

ICD-10-CM G71.220
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G71.220 is a billable ICD-10-CM diagnosis code for x-linked myotubular myopathy. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as myotubular myopathy. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.

Code Identity

ICD-10-CM Code
G71.220
Billable Status
Yes — Valid for Submission
Code Describes
X-linked myotubular myopathy
Short Description
X-linked myotubular myopathy
Same as the full description in the CMS dataset.
Parent Code
G71.22
Centronuclear myopathy

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG70-G73Diseases of myoneural junction and muscle
CategoryG71Primary disorders of muscles
This CodeG71.220X-linked myotubular myopathy

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Myotubular myopathy
  • Myotubular myopathy with type I atrophy
  • Severe X-linked myotubular myopathy
  • Symptomatic form of X-linked centronuclear myopathy in female carrier
  • X-linked myotubular myopathy, abnormal genitalia syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Myotubular (centronuclear) myopathy

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Myopathy
      • myotubular (centronuclear)
    • Myopathy
      • myotubular (centronuclear)
        • X-linked

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS018
Myopathies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

X-linked myotubular myopathy

X-linked myotubular myopathy is a condition that primarily affects muscles used for movement (skeletal muscles) and occurs almost exclusively in males. People with this condition have muscle weakness (myopathy) and decreased muscle tone (hypotonia) that are usually evident at birth.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement G71.220 replaces the following previously assigned code(s):

  • G71.2 - Congenital myopathies
FY 2021AddedAdded to the ICD-10-CM code setEffective October 1, 2020.
FY 2022–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G71.220Overview

Is G71.220 (Centronuclear myopathy) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report x-linked myotubular myopathy on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.