2026 ICD-10-CM Diagnosis Code G71.038Other limb girdle muscular dystrophy

ICD-10-CM Codes›G00–G99›G70-G73›G71

ICD-10-CM G71.038
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G71.038 is a billable ICD-10-CM diagnosis code for other limb girdle muscular dystrophy. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.

Code Identity

ICD-10-CM Code
G71.038
Billable Status
Yes — Valid for Submission
Code Describes
Other limb girdle muscular dystrophy
Short Description
Other limb girdle muscular dystrophy
Same as the full description in the CMS dataset.
Parent Code
G71.034
Limb girdle muscular dystrophy due to sarcoglycan dysfunction

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG70-G73Diseases of myoneural junction and muscle
CategoryG71Primary disorders of muscles
This CodeG71.038Other limb girdle muscular dystrophy

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal recessive limb girdle muscular dystrophy type 2A
  • Autosomal recessive limb girdle muscular dystrophy type 2B
  • Autosomal recessive limb girdle muscular dystrophy type 2C
  • Autosomal recessive limb girdle muscular dystrophy type 2D
  • Autosomal recessive limb girdle muscular dystrophy type 2E
  • Autosomal recessive limb girdle muscular dystrophy type 2F
  • Autosomal recessive limb girdle muscular dystrophy type 2G
  • Autosomal recessive limb girdle muscular dystrophy type 2I
  • Autosomal recessive limb girdle muscular dystrophy type 2J
  • Autosomal recessive limb girdle muscular dystrophy type 2K
  • Autosomal recessive limb girdle muscular dystrophy type 2L
  • Autosomal recessive limb girdle muscular dystrophy type 2M
  • Autosomal recessive limb girdle muscular dystrophy type 2N
  • Autosomal recessive limb girdle muscular dystrophy type 2O
  • Autosomal recessive limb girdle muscular dystrophy type 2P
  • Autosomal recessive limb girdle muscular dystrophy type 2Q
  • Autosomal recessive limb girdle muscular dystrophy type 2S
  • Autosomal recessive limb girdle muscular dystrophy type 2T
  • Autosomal recessive limb girdle muscular dystrophy type 2U
  • Autosomal recessive limb girdle muscular dystrophy type 2Y
  • Autosomal recessive muscular dystrophy with limb girdle distribution
  • BVES-related limb girdle muscular dystrophy
  • Childhood-onset progressive contractures, limb girdle weakness, muscle dystrophy syndrome
  • Laminin alpha-2 related limb girdle muscular dystrophy R23
  • Limb girdle muscular dystrophy due to POMK deficiency
  • LIMS2-related limb girdle muscular dystrophy
  • Muscular dystrophy with predominantly proximal limb girdle distribution
  • POMGNT2-related limb girdle muscular dystrophy R24
  • X-linked limb girdle muscular dystrophy with normal dystrophin
  • X-linked muscular dystrophy not predominantly limb girdle
  • X-linked muscular dystrophy with limb girdle distribution

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • LGMD R22
  • Other autosomal recessive limb girdle muscular dystrophy

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Dystrophy, dystrophia
      • Leyden-Möbius
        • meaning Limb girdle muscular dystrophy, specified type NEC
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • autosomal recessive NEC
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • collagen VI related
            • autosomal recessive
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • FKRP-related autosomal recessive
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R7 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R8 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R10 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R11 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R13 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R14 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R15 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R16 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R17 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R18 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R19 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R20 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R21 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R22 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R23 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R24 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2 (autosomal recessive)
            • specified NEC
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2G (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2H (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2J (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2K (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2M (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2N (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2O (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2P (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2Q (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2S (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2T (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2U (autosomal recessive)

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS018
Myopathies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Limb-girdle muscular dystrophy

Limb-girdle muscular dystrophy is a term for a group of diseases that cause weakness and wasting of the muscles in the arms and legs. The muscles most affected are those closest to the body (proximal muscles), specifically the muscles of the shoulders, upper arms, pelvic area, and thighs.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replaced This code was replaced in the FY 2026 code set by:

  • G71.036 - Limb girdle musc dyst due to fukutin related protein dysfnct
  • G71.036 - Limb girdle musc dyst due to fukutin related protein dysfnct
  • G71.036 - Limb girdle musc dyst due to fukutin related protein dysfnct
  • G71.036 - Limb girdle musc dyst due to fukutin related protein dysfnct
  • G71.036 - Limb girdle musc dyst due to fukutin related protein dysfnct
  • G71.036 - Limb girdle musc dyst due to fukutin related protein dysfnct

Replacement G71.038 replaces the following previously assigned code(s):

  • G71.09 - Other specified muscular dystrophies
FY 2023AddedAdded to the ICD-10-CM code setEffective October 1, 2022.
FY 2024–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G71.038Overview

Is G71.038 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report other limb girdle muscular dystrophy on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.