2026 ICD-10-CM Diagnosis Code G71.035Limb girdle muscular dystrophy due to anoctamin-5 dysfunction

ICD-10-CM Codes›G00–G99›G70-G73›G71

ICD-10-CM G71.035
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G71.035 is a billable ICD-10-CM diagnosis code for limb girdle muscular dystrophy due to anoctamin-5 dysfunction. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.

Code Identity

ICD-10-CM Code
G71.035
Billable Status
Yes — Valid for Submission
Code Describes
Limb girdle muscular dystrophy due to anoctamin-5 dysfunction
Short Description
Limb girdle musc dyst due to anoctamin-5 dysfunction
Parent Code
G71.034
Limb girdle muscular dystrophy due to sarcoglycan dysfunction

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG70-G73Diseases of myoneural junction and muscle
CategoryG71Primary disorders of muscles
This CodeG71.035Limb girdle muscular dystrophy due to anoctamin-5 dysfunction

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Anoctamin-5-related LGMD R12
  • Anoctaminopathy
  • Autosomal recessive limb girdle muscular dystrophy type 2L
  • Miyoshi myopathy type 3

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anoctaminopathy
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • anoctamin-5-related autosomal recessive (R12)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • due to
            • anoctamin-5 dysfunction
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • R12 (autosomal recessive)
    • Dystrophy, dystrophia
      • muscular
        • limb-girdle
          • type 2L (autosomal recessive)
    • Myopathy
      • Miyoshi, type 3

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS018
Myopathies
Default principal diagnosis: inpatient Yes · outpatient Yes

Code History & ChangesHistory

Replacement G71.035 replaces the following previously assigned code(s):

  • G71.09 - Other specified muscular dystrophies
FY 2023AddedAdded to the ICD-10-CM code setEffective October 1, 2022.
FY 2024–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G71.035Overview

Is G71.035 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report limb girdle muscular dystrophy due to anoctamin-5 dysfunction on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.