2026 ICD-10-CM Diagnosis Code G71.02Facioscapulohumeral muscular dystrophy

ICD-10-CM Codes›G00–G99›G70-G73›G71

ICD-10-CM G71.02
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

G71.02 is a billable ICD-10-CM diagnosis code for facioscapulohumeral muscular dystrophy. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). Coders also document this condition as autosomal dominant muscular dystrophy not predominantly limb girdle. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Myopathies.

Code Identity

ICD-10-CM Code
G71.02
Billable Status
Yes — Valid for Submission
Code Describes
Facioscapulohumeral muscular dystrophy
Short Description
Facioscapulohumeral muscular dystrophy
Same as the full description in the CMS dataset.
Parent Code
G71.0
Muscular dystrophy

Code Classification

ChapterG00–G99Diseases of the nervous system
SectionG70-G73Diseases of myoneural junction and muscle
CategoryG71Primary disorders of muscles
This CodeG71.02Facioscapulohumeral muscular dystrophy

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal dominant muscular dystrophy not predominantly limb girdle
  • Autosomal recessive muscular dystrophy not predominantly limb girdle
  • Facioscapulohumeral muscular dystrophy
  • Scapulohumeral muscular dystrophy

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Scapulohumeral muscular dystrophy

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Atrophy, atrophic(of)
      • fascioscapulohumeral (Landouzy- Déjérine)
    • Atrophy, atrophic(of)
      • Landouzy-Déjérine
    • Atrophy, atrophic(of)
      • muscle, muscular (diffuse) (general) (idiopathic) (primary)
        • pseudohypertrophic
    • Atrophy, atrophic(of)
      • pseudohypertrophic (muscle)
    • Disease, diseased
      • Erb (-Landouzy)
    • Dystrophy, dystrophia
      • Erb's
    • Dystrophy, dystrophia
      • Landouzy-Déjérine
    • Dystrophy, dystrophia
      • muscular
        • Erb type
    • Dystrophy, dystrophia
      • muscular
        • facioscapulohumeral
    • Dystrophy, dystrophia
      • muscular
        • Landouzy-Déjérine type
    • Dystrophy, dystrophia
      • muscular
        • scapulohumeral
    • Erb's
      • disease
    • Erb's
      • pseudohypertrophic muscular dystrophy
    • Fascioscapulohumeral myopathy
    • Landouzy-Déjérine dystrophy or facioscapulohumeral atrophy
    • Myopathy
      • facioscapulohumeral
    • Myopathy
      • scapulohumeral
    • Paralysis, paralytic(complete) (incomplete)
      • muscle, muscular NEC
        • pseudohypertrophic
    • Pseudohypertrophic muscular dystrophy(Erb's)
    • Scapulohumeral myopathy

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NVS018
Myopathies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Facioscapulohumeral Muscular Dystrophy

    an autosomal dominant disorder affecting the skeletal muscles of the face, scapula, and upper arm. patients present with muscle weakness in these anatomic areas. the muscle weakness eventually spreads to other skeletal muscles as well.

  • Facioscapulohumeral Muscular Dystrophy 1|FSHD1

    an autosomal dominant form of facioscapulohumeral muscular dystrophy associated with contraction of the d4z4 macrosatellite repeat.

  • Facioscapulohumeral Muscular Dystrophy 2|FSHD2

    a form of facioscapulohumeral muscular dystrophy with digenic inheritance, caused by a combination of heterozygous mutation in the smchd1 gene and the presence of a haplotype that is permissive for dux4.

Patient EducationClinical

Muscular Dystrophy

Muscular dystrophy (MD) is a group of more than 30 genetic diseases. They cause weakness of the muscles. Over time, the weakness gets worse and can cause trouble walking and doing daily activities. Some types of MD can also affect other organs.

The full article covers:

  • What is muscular dystrophy (MD)?
  • What are the types of muscular dystrophy (MD)?
  • What causes muscular dystrophy (MD)?
  • How is muscular dystrophy (MD) diagnosed?
  • What are the treatments for muscular dystrophy (MD)?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Code History & ChangesHistory

Replacement G71.02 replaces the following previously assigned code(s):

  • G71.0 - Muscular dystrophy
FY 2019AddedAdded to the ICD-10-CM code setEffective October 1, 2018.
FY 2020–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About G71.02Overview

Is G71.02 (Muscular dystrophy) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report facioscapulohumeral muscular dystrophy on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.