2026 ICD-10-CM Diagnosis Code G31.09Other frontotemporal neurocognitive disorder
ICD-10-CM Codes›G00–G99›G30-G32›G31
- Billable — Valid for Submission
- Chronic Condition
G31.09 is a billable ICD-10-CM diagnosis code for other frontotemporal neurocognitive disorder. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Neurocognitive disorders.
Code Identity
Code Classification
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Amyotrophic lateral sclerosis plus syndrome
- Amyotrophic lateral sclerosis with frontotemporal dementia
- Behavioral variant of frontotemporal dementia
- CHMP2B-related frontotemporal dementia
- Dementia due to chromosomal anomaly
- Dementia of frontal lobe type
- Familial multiple system tauopathy
- Frontal lobe degeneration
- Frontotemporal dementia
- Frontotemporal dementia due to C9orf72 mutation
- Frontotemporal dementia due to FUS mutation
- Frontotemporal dementia due to TARDBP mutation
- Frontotemporal dementia due to VCP mutation
- Frontotemporal dementia with parkinsonism-17
- GRN-related frontotemporal dementia
- Inclusion body myopathy with early-onset Paget disease and frontotemporal dementia
- Myopathy with cytoplasmic inclusions
- Right temporal lobar atrophy
- Semantic dementia
Tabular List NotesGuidance
Coding notes and annotation back-references applicable to this code.
Inclusion Terms
- Frontal dementia
Use Additional Code
- code, if applicable, to identify mild neurocognitive disorders due to known physiological condition F06.7
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
The “use additional code” indicates that a secondary code could be used to further specify the patient’s condition. This note is not mandatory and is only used if enough information is available to assign an additional code.
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- sclerosis, lobar (of brain) - See Also: Dementia, in, diseases specified elsewhere; - G31.09
- with behavioral disturbance - See Also: Dementia, in, diseases specified elsewhere; - G31.09
- Dementia (degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety) - F03.90
- frontal (lobe) - See Also: Dementia, in, diseases specified elsewhere; - G31.09
- with behavioral disturbance - See Also: Dementia, in, diseases specified elsewhere; - G31.09
- frontotemporal - G31.09
- with behavioral disturbance - G31.09
- specified NEC - See Also: Dementia, in, diseases specified elsewhere; - G31.09
- with behavioral disturbance - See Also: Dementia, in, diseases specified elsewhere; - G31.09
- Disorder (of) - See Also: Disease;
- neurocognitive - R41.9
- frontotemporal, specified NEC - See Also: Dementia, in, diseases specified elsewhere; - G31.09
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Atrophy, atrophic(of)
- sclerosis, lobar (of brain)
- Atrophy, atrophic(of)
- sclerosis, lobar (of brain)
- with behavioral disturbance
- Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
- frontal (lobe)
- Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
- frontal (lobe)
- with behavioral disturbance
- Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
- frontotemporal
- Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
- frontotemporal
- with behavioral disturbance
- Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
- frontotemporal
- specified NEC
- Dementia(degenerative (primary)) (persisting) (unspecified severity) (without behavioral disturbance, psychotic disturbance, mood disturbance, and anxiety)
- frontotemporal
- specified NEC
- with behavioral disturbance
- Disorder(of)
- neurocognitive
- frontotemporal, specified NEC
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Frontotemporal Dementia
the most common clinical form of frontotemporal lobar degeneration, this dementia presents with personality and behavioral changes often associated with disinhibition, apathy, and lack of insight.Frontotemporal Lobar Degeneration
heterogeneous group of neurodegenerative disorders characterized by frontal and temporal lobe atrophy associated with neuronal loss, gliosis, and dementia. patients exhibit progressive changes in social, behavioral, and/or language function. multiple subtypes or forms are recognized based on presence or absence of tau protein inclusions. ftld includes three clinical syndromes: frontotemporal dementia, semantic dementia, and primary progressive nonfluent aphasia.Amyotrophic Lateral Sclerosis 10, with or without Frontotemporal Dementia|ALS10
an autosomal dominant form of amyotrophic lateral sclerosis caused by mutation(s) in the tardbp gene, encoding tar dna-binding protein 43.Amyotrophic Lateral Sclerosis 14, with or without Frontotemporal Dementia|ALS14
a form of amyotrophic lateral sclerosis caused by heterozygous mutation(s) in the vcp gene, encoding transitional endoplasmic reticulum atpase.Amyotrophic Lateral Sclerosis 15, with or without Frontotemporal Dementia|ALS15
an x-linked dominant form of amyotrophic lateral sclerosis caused by mutation(s) in the ubqln2 gene, encoding ubiquilin-2.Amyotrophic Lateral Sclerosis 26, with or without Frontotemporal Dementia|ALS26
an autosomal dominant form of amyotrophic lateral sclerosis caused by mutation(s) in the tia1 gene, encoding cytotoxic granule associated rna binding protein tia1.Amyotrophic Lateral Sclerosis 6, with or without Frontotemporal Dementia|ALS6
a form of amyotrophic lateral sclerosis caused by heterozygous mutation(s) in the fus gene, encoding rna-binding protein fus.Frontotemporal Dementia and/or Amyotrophic Lateral Sclerosis 2|FTDALS2
an autosomal dominant form of frontotemporal dementia and/or amyotrophic lateral sclerosis caused by mutation(s) in the chchd10 gene, encoding coiled-coil-helix-coiled-coil-helix domain-containing protein 10, mitochondrial.Frontotemporal Dementia and/or Amyotrophic Lateral Sclerosis 4|FTDALS4
an autosomal dominant form of frontotemporal dementia and/or amyotrophic lateral sclerosis caused by mutation(s) in the tbk1 gene, encoding serine/threonine-protein kinase tbk1.Frontotemporal Dementia and/or Amyotrophic Lateral Sclerosis 7|FTDALS7
an autosomal dominant form of frontotemporal dementia and/or amyotrophic lateral sclerosis caused by mutation(s) in the chmp2b gene, encoding charged multivesicular body protein 2b.Frontotemporal Dementia-1|FTD1|FTDP17|Frontotemporal Dementia 1|Frontotemporal Dementia with Parkinsonism-17
an autosomal dominant subtype of frontotemporal dementia caused by mutation(s) in the mapt gene, encoding microtubule-associated protein tau.Amyotrophic Lateral Sclerosis 10, With or Without Frontotemporal Dementia|ALS10
an autosomal dominant form of amyotrophic lateral sclerosis caused by mutation(s) in the tardbp gene, encoding tar dna-binding protein 43.Amyotrophic Lateral Sclerosis 14, With or Without Frontotemporal Dementia|ALS14
a form of amyotrophic lateral sclerosis caused by heterozygous mutation(s) in the vcp gene, encoding transitional endoplasmic reticulum atpase.Amyotrophic Lateral Sclerosis 6, With or Without Frontotemporal Dementia|ALS6
a form of amyotrophic lateral sclerosis caused by heterozygous mutation(s) in the fus gene, encoding rna-binding protein fus.Frontotemporal Dementia
a syndrome caused by progressive degeneration of the frontal or temporal lobes of the brain. it is manifested with personality changes and deterioration of the language skills.Frontotemporal Dementia and/or Amyotrophic Lateral Sclerosis 1|FTDALS1
an autosomal dominant condition caused by heterozygous hexanucleotide repeat expansion in a noncoding region of the c9orf72 gene , encoding guanine nucleotide exchange c9orf72. it is characterized by amyotrophic lateral sclerosis with frontotemporal dementia.Inclusion Body Myopathy with Early-Onset Paget Disease with or without Frontotemporal Dementia 1|IBMPFD1
a rare autosomal dominant inherited disorder caused by mutations in the vcp gene. it can affect the muscles, bones, and brain. patients may develop myopathy that initially involves the muscles of the hips and shoulders and as the disorder progresses it may affect the cardiac and respiratory muscles, leading to life-threatening cardiac and pulmonary failure. approximately half of the adults develop paget disease of bone, and approximately one-third develop frontotemporal dementia.Other Frontotemporal Dementia|Other frontotemporal dementia
evidence of other frontotemporal dementia not specified elsewhere.
Patient EducationClinical
Dementia
Dementia is a loss of mental functions that is severe enough to affect your daily life and activities. These functions include:
The full article covers:
- What is dementia?
- What are the types of dementia?
- Who is at risk for dementia?
- What are the symptoms of dementia?
- How is dementia diagnosed?
- What are the treatments for dementia?
- Can dementia be prevented?
- What Are Frontotemporal Disorders?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert G31.09 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About G31.09Overview
Is G31.09 (Frontotemporal dementia) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report other frontotemporal neurocognitive disorder on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What is the ICD-9 equivalent of G31.09?
Under the General Equivalence Mappings, other frontotemporal neurocognitive disorder converts to ICD-9-CM 331.19 (frontotemp dementia NEC). The mapping is a direct match.
Footnotes
[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.
