2026 ICD-10-CM Diagnosis Code E83.110Hereditary hemochromatosis

ICD-10-CM Codes›E00–E89›E70-E88›E83

ICD-10-CM E83.110
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

E83.110 is a billable ICD-10-CM diagnosis code for hereditary hemochromatosis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified nutritional and metabolic disorders.

Code Identity

ICD-10-CM Code
E83.110
Billable Status
Yes — Valid for Submission
Code Describes
Hereditary hemochromatosis
Short Description
Hereditary hemochromatosis
Same as the full description in the CMS dataset.
Parent Code
E83.11
Hemochromatosis

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE70-E88Metabolic disorders
CategoryE83Disorders of mineral metabolism
This CodeE83.110Hereditary hemochromatosis

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Bronze diabetes
  • Digenic hemochromatosis
  • Ferroportin disease
  • FTH1-related iron overload
  • Hemochromatosis type 1
  • Hemochromatosis type 3
  • Hemochromatosis type 4
  • Hereditary hemochromatosis
  • Hypochromic microcytic anemia with iron overload
  • Juvenile hemochromatosis
  • Microcytic hypochromic anemia
  • Pigment cirrhosis
  • Primary hemochromatosis
  • SLC40A1-related hemochromatosis
  • Symptomatic form of hemochromatosis type 1
  • Type 2A juvenile hereditary hemochromatosis
  • Type 2B juvenile hereditary hemochromatosis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Bronzed diabetes
  • Pigmentary cirrhosis (of liver)
  • Primary (hereditary) hemochromatosis

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Cirrhosis, cirrhotic(hepatic) (liver)
      • pigmentary
    • Diabetes, diabetic(mellitus) (sugar)
      • bronzed
    • Hemochromatosis
      • hereditary (primary)
    • Hemochromatosis
      • primary

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR END016
Other specified and unspecified nutritional and metabolic disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Hemochromatosis

    a disorder of iron metabolism characterized by a triad of hemosiderosis; liver cirrhosis; and diabetes mellitus. it is caused by massive iron deposits in parenchymal cells that may develop after a prolonged increase of iron absorption. (jablonski's dictionary of syndromes & eponymic diseases, 2d ed)

  • Hemochromatosis Protein

    a membrane protein and mhc class i antigen. it contains an immunoglobulin c1-set domain and interacts with beta 2-microglobulin. it may also regulate the interaction of transferrin with the transferrin receptor. mutations in the hfe gene are associated with cases of familial hemochromatosis.

Patient EducationClinical

Hemochromatosis

Hemochromatosis is a disease in which too much iron builds up in your body. Your body needs iron but too much of it is toxic. If you have hemochromatosis, you absorb more iron than you need. Your body has no natural way to get rid of the extra iron. It stores it in body tissues, especially the liver, heart, and pancreas.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert E83.110 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
275.01 Heredit hemochromatosis
Exact Match The mapping is direct, with no qualifiers.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About E83.110Overview

Is E83.110 (Hemochromatosis) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report hereditary hemochromatosis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of E83.110?

Under the General Equivalence Mappings, hereditary hemochromatosis converts to ICD-9-CM 275.01 (heredit hemochromatosis). The mapping is a direct match.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.