2024 ICD-10-CM Diagnosis Code D64.3

Other sideroblastic anemias

Short Description:
Other sideroblastic anemias
Is Billable?
Yes - Valid for Submission
Chronic Condition Indicator [1]
Not chronic
Code Navigator:

Code Classification

  • Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
    • Aplastic and other anemias and other bone marrow failure syndromes
      • Other anemias

D64.3 is a billable diagnosis code used to specify a medical diagnosis of other sideroblastic anemias. The code is valid during the current fiscal year for the submission of HIPAA-covered transactions from October 01, 2023 through September 30, 2024.

Approximate Synonyms

The following clinical terms are approximate synonyms or lay terms that might be used to identify the correct diagnosis code:

  • Autosomal-linked pyridoxine refractory sideroblastic anemia
  • Fetal acidosis
  • Fetal anemia
  • Hydrops fetalis
  • Hydrops, lactic acidosis, sideroblastic anemia, multisystemic failure syndrome
  • Idiopathic sideroblastic anemia
  • Metabolic disorder of fetus
  • Pyridoxine-responsive sideroblastic anemia
  • Secondary acquired sideroblastic anemia
  • Sideroblastic anemia
  • X chromosome-linked pyridoxine responsive sideroblastic anemia
  • X chromosome-linked sideroblastic anemia

Clinical Classification

Clinical Category:
Aplastic anemia
CCSR Category Code:
Inpatient Default CCSR:
Y - Yes, default inpatient assignment for principal diagnosis or first-listed diagnosis.
Outpatient Default CCSR:
Y - Yes, default outpatient assignment for principal diagnosis or first-listed diagnosis.

Clinical Information

  • Hydrops Fetalis-. abnormal accumulation of serous fluid in two or more fetal compartments, such as skin; pleura; pericardium; placenta; peritoneum; amniotic fluid. general fetal edema may be of non-immunologic origin, or of immunologic origin as in the case of erythroblastosis fetalis.
  • Hydrops Fetalis-. a condition characterized by fluid accumulation in two or more anatomic compartments in the fetus.
  • Immune Hydrops Fetalis-. fluid accumulation in multiple fetal anatomic cavities attributable to a maternal immune response against fetal blood cell antigens.
  • Non-Immune Hydrops Fetalis-. fluid accumulation in multiple fetal anatomic cavities that is of non-immune origin.
  • Hereditary Sideroblastic Anemia-. an inherited form of sideroblastic anemia.
  • Myelodysplastic Syndrome with Ring Sideroblasts|MDS-RS|Pure Sideroblastic Anemia|RARS|RARS|Refractory Anemia with Ring Sideroblasts|Refractory Anemia with Ringed Sideroblasts|Refractory anemia with ring sideroblasts|Refractory anemia with ringed sideroblasts-. a myelodysplastic syndrome characterized by an anemia in which 15% or more of the erythroid precursors are ring sideroblasts. the ring sideroblast is an erythroid precursor in which one third or more of the nucleus is encircled by granules which are positive for iron stain. (who, 2001)
  • Sideroblastic Anemia-. anemia characterized by the production of ringed sideroblasts instead of healthy red blood cells.

Tabular List of Diseases and Injuries

The following annotation back-references are applicable to this diagnosis code. The Tabular List of Diseases and Injuries is a list of ICD-10-CM codes, organized "head to toe" into chapters and sections with coding notes and guidance for inclusions, exclusions, descriptions and more.

Inclusion Terms

Inclusion Terms
These terms are the conditions for which that code is to be used. The terms may be synonyms of the code title, or, in the case of "other specified" codes, the terms are a list of the various conditions assigned to that code. The inclusion terms are not necessarily exhaustive. Additional terms found only in the Alphabetic Index may also be assigned to a code.
  • Sideroblastic anemia NOS
  • Pyridoxine-responsive sideroblastic anemia NEC

Index to Diseases and Injuries References

The following annotation back-references for this diagnosis code are found in the injuries and diseases index. The Index to Diseases and Injuries is an alphabetical listing of medical terms, with each term mapped to one or more ICD-10-CM code(s).

Convert to ICD-9-CM Code

Source ICD-10-CM CodeTarget ICD-9-CM Code
D64.3285.0 - Sideroblastic anemia
Approximate Flag - The approximate mapping means there is not an exact match between the ICD-10 and ICD-9 codes and the mapped code is not a precise representation of the original code.

Patient Education


If you have anemia, your blood does not carry enough oxygen to the rest of your body. The most common cause of anemia is not having enough iron. Your body needs iron to make hemoglobin. Hemoglobin is an iron-rich protein that gives the red color to blood. It carries oxygen from the lungs to the rest of the body.

Anemia has three main causes: blood loss, lack of red blood cell production, and high rates of red blood cell destruction.

Conditions that may lead to anemia include:

  • Heavy periods
  • Pregnancy
  • Ulcers
  • Colon polyps or colon cancer
  • Inherited disorders
  • A diet that does not have enough iron, folic acid or vitamin B12
  • Blood disorders such as sickle cell anemia and thalassemia, or cancer
  • Aplastic anemia, a condition that can be inherited or acquired
  • G6PD deficiency, a metabolic disorder

Anemia can make you feel tired, cold, dizzy, and irritable. You may be short of breath or have a headache.

Your doctor will diagnose anemia with a physical exam and blood tests. Treatment depends on the kind of anemia you have.

NIH: National Heart, Lung, and Blood Institute

[Learn More in MedlinePlus]

Code History

  • FY 2024 - No Change, effective from 10/1/2023 through 9/30/2024
  • FY 2023 - No Change, effective from 10/1/2022 through 9/30/2023
  • FY 2022 - No Change, effective from 10/1/2021 through 9/30/2022
  • FY 2021 - No Change, effective from 10/1/2020 through 9/30/2021
  • FY 2020 - No Change, effective from 10/1/2019 through 9/30/2020
  • FY 2019 - No Change, effective from 10/1/2018 through 9/30/2019
  • FY 2018 - No Change, effective from 10/1/2017 through 9/30/2018
  • FY 2017 - No Change, effective from 10/1/2016 through 9/30/2017
  • FY 2016 - New Code, effective from 10/1/2015 through 9/30/2016. This was the first year ICD-10-CM was implemented into the HIPAA code set.


[1] Not chronic - A diagnosis code that does not fit the criteria for chronic condition (duration, ongoing medical treatment, and limitations) is considered not chronic. Some codes designated as not chronic are acute conditions. Other diagnosis codes that indicate a possible chronic condition, but for which the duration of the illness is not specified in the code description (i.e., we do not know the condition has lasted 12 months or longer) also are considered not chronic.