2026 ICD-10-CM Diagnosis Code E70.311Autosomal recessive ocular albinism

ICD-10-CM CodesE00–E89E70-E88E70

ICD-10-CM E70.311
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

E70.311 is a billable ICD-10-CM diagnosis code for autosomal recessive ocular albinism. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026). In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified nutritional and metabolic disorders.

Code Identity

ICD-10-CM Code
E70.311
Billable Status
Yes — Valid for Submission
Code Describes
Autosomal recessive ocular albinism
Short Description
Autosomal recessive ocular albinism
Same as the full description in the CMS dataset.
Parent Code
Ocular albinism

Code Classification

ChapterE00–E89Endocrine, nutritional and metabolic diseases
SectionE70-E88Metabolic disorders
CategoryE70Disorders of aromatic amino-acid metabolism
This CodeE70.311Autosomal recessive ocular albinism

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Autosomal recessive ocular albinism
  • Ocular albinism

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Albinism, albino
      • ocular
        • autosomal recessive

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR END016
Other specified and unspecified nutritional and metabolic disorders
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Eye Diseases

Even if your eyes feel healthy, you could have a problem and not know it. That's why regular eye exams are so important. Refractive errors are the most common type of vision problem that makes it hard to see clearly. But some eye conditions or diseases don't have any symptoms and can lead to a permanent loss of vision.

The full article covers:

  • What diseases can affect the eye?
  • What are the symptoms of eye diseases?
  • Who is more likely to develop eye diseases?
  • What are the treatments for eye diseases?
  • Can eye diseases be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert E70.311 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
270.2 Arom amin-acid metab NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About E70.311Overview

Is E70.311 (Ocular albinism) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report autosomal recessive ocular albinism on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What is the ICD-9 equivalent of E70.311?

Under the General Equivalence Mappings, autosomal recessive ocular albinism converts to ICD-9-CM 270.2 (arom amin-acid metab NEC). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.