2026 ICD-10-CM Diagnosis Code C88.40Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission

ICD-10-CM Codes›C00–D49›C81-C96›C88

ICD-10-CM C88.40
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

C88.40 is a billable ICD-10-CM diagnosis code for extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 820 through 825, 840 through 842, 974 through 976. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Non-Hodgkin lymphoma.

Code Identity

ICD-10-CM Code
C88.40
Billable Status
Yes — Valid for Submission
Code Describes
Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission
Short Description
Extrnod mrgnl B-cell lymph mucosa-assoc lym tiss not remis
Parent Code
C88.4
Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]

Code Classification

ChapterC00–D49Neoplasms
SectionC81-C96Malignant neoplasms of lymphoid, hematopoietic and related tissue
CategoryC88Malignant immunoproliferative diseases and certain other B-cell lymphomas
This CodeC88.40Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Diffuse low grade B-cell lymphoma
  • Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue
  • Malignant lymphoma of the eye region
  • Mucosa-associated lymphoid tissue lymphoma of orbit
  • Mucosa-associated lymphoid tissue lymphoma of stomach
  • Mucosa-associated lymphoma
  • Non-Hodgkin's lymphoma of stomach
  • Orbital lymphoma
  • Primary cutaneous B-cell lymphoma
  • Primary cutaneous marginal zone B-cell lymphoma

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue MALT-lymphoma NOS
  • Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue MALT-lymphoma with failed remission
  • Lymphoma of bronchial-associated lymphoid tissue BALT-lymphoma NOS
  • Lymphoma of bronchial-associated lymphoid tissue BALT-lymphoma not having achieved remission
  • Lymphoma of bronchial-associated lymphoid tissue BALT-lymphoma with failed remission
  • Lymphoma of skin-associated lymphoid tissue SALT-lymphoma NOS
  • Lymphoma of skin-associated lymphoid tissue SALT-lymphoma not having achieved remission
  • Lymphoma of skin-associated lymphoid tissue SALT-lymphoma with failed remission

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR NEO058
Non-Hodgkin lymphoma
Default principal diagnosis: inpatient Yes · outpatient Yes

Code History & ChangesHistory

Replacement C88.40 replaces the following previously assigned code(s):

  • C88.4 - Extrnod mrgnl zn B-cell lymph of mucosa-assoc lymphoid tiss
FY 2025AddedAdded to the ICD-10-CM code setEffective October 1, 2024.
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About C88.40Overview

Is C88.40 a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does C88.40 group to?

When extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission is the principal diagnosis on an inpatient stay, it groups to MS-DRG 820, 821, 822, 823, 824, 825, 840, 841, 842, 974, 975, 976, with relative weights from 0.8945 to 5.8648 depending on complications. Higher weights mean higher Medicare reimbursement.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.