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  5. Other specified types of T/NK-cell lymphoma (C86)

Other specified types of T/NK-cell lymphoma (C86)

The ICD-10 code C86 covers various specified types of T-cell and natural killer (NK)-cell lymphomas, including conditions like extranodal NK/T-cell lymphoma, hepatosplenic T-cell lymphoma, and others. These codes help classify specific lymphomas that affect the immune system’s T and NK cells, providing distinctions based on location and remission status.

This section is used for coding less common T/NK-cell lymphomas such as extranodal NK/T-cell lymphoma, nasal type (C86.0), sometimes called angiocentric NK/T-cell malignant lymphoma involving skin. It also includes hepatosplenic T-cell lymphoma (C86.1), known as hepatosplenic gamma-delta cell lymphoma, and enteropathy-type (intestinal) T-cell lymphoma (C86.2), known as enteropathy-associated T-cell lymphoma or gastrointestinal lymphoma. Other entries include subcutaneous panniculitis-like T-cell lymphoma (C86.3), blastic NK-cell lymphoma (C86.4) which may be called NK-lymphoblastic leukemia/lymphoma, and angioimmunoblastic T-cell lymphoma (C86.5). Primary cutaneous CD30-positive T-cell proliferations (C86.6) embrace conditions like lymphomatoid papulosis and primary cutaneous anaplastic large cell lymphoma. Each subtype has codes to specify whether the disease is in remission or not, which is useful for treatment tracking and documentation. Use the ICD-10 code for [specific condition] to accurately capture precise diagnoses in clinical records.

  • Neoplasms (C00–D49)

    • Malignant neoplasms of lymphoid, hematopoietic and related tissue (C81-C96)

        • Other specified types of T/NK-cell lymphoma (C86)

        • C86 Other specified types of T/NK-cell lymphoma
        • C86.0 Extranodal NK/T-cell lymphoma, nasal type DELETED CODE
        • C86.00 Extranodal NK/T-cell lymphoma, nasal type not having achieved remission NEW CODE
        • C86.01 Extranodal NK/T-cell lymphoma, nasal type, in remission NEW CODE
        • C86.1 Hepatosplenic T-cell lymphoma DELETED CODE
        • C86.10 Hepatosplenic T-cell lymphoma not having achieved remission NEW CODE
        • C86.11 Hepatosplenic T-cell lymphoma, in remission NEW CODE
        • C86.2 Enteropathy-type (intestinal) T-cell lymphoma DELETED CODE
        • C86.20 Enteropathy-type (intestinal) T-cell lymphoma not having achieved remission NEW CODE
        • C86.21 Enteropathy-type (intestinal) T-cell lymphoma, in remission NEW CODE
        • C86.3 Subcutaneous panniculitis-like T-cell lymphoma DELETED CODE
        • C86.30 Subcutaneous panniculitis-like T-cell lymphoma not having achieved remission NEW CODE
        • C86.31 Subcutaneous panniculitis-like T-cell lymphoma, in remission NEW CODE
        • C86.4 Blastic NK-cell lymphoma DELETED CODE
        • C86.40 Blastic NK-cell lymphoma not having achieved remission NEW CODE
        • C86.41 Blastic NK-cell lymphoma, in remission NEW CODE
        • C86.5 Angioimmunoblastic T-cell lymphoma DELETED CODE
        • C86.50 Angioimmunoblastic T-cell lymphoma not having achieved remission NEW CODE
        • C86.51 Angioimmunoblastic T-cell lymphoma, in remission NEW CODE
        • C86.6 Primary cutaneous CD30-positive T-cell proliferations DELETED CODE
        • C86.60 Primary cutaneous CD30-positive T-cell proliferations not having achieved remission NEW CODE
        • C86.61 Primary cutaneous CD30-positive T-cell proliferations, in remission NEW CODE

Instructional Notations

Type 1 Excludes

A type 1 excludes note is a pure excludes note. It means "NOT CODED HERE!" An Excludes1 note indicates that the code excluded should never be used at the same time as the code above the Excludes1 note. An Excludes1 is used when two conditions cannot occur together, such as a congenital form versus an acquired form of the same condition.

  • anaplastic large cell lymphoma, ALK negative C84.7
  • anaplastic large cell lymphoma, ALK positive C84.6
  • mature T/NK-cell lymphomas C84
  • other specified types of non-Hodgkin lymphoma C85.8

Clinical Terms

The following clinical terms provide additional context, helping users better understand the clinical background and common associations for each diagnosis listed in this section. Including related terms alongside ICD-10-CM codes supports coders, billers, and healthcare professionals in improving accuracy, enhancing documentation, and facilitating research or patient education.

Blastic Plasmacytoid Dendritic Cell Neoplasm

A rare and aggressive hematologic malignancy derived from the precursors of PLASMACYTOID DENDRITIC CELLS. Blastic plasmacytoid dendritic cell neoplasms affect bone marrow and blood in addition to the lymph nodes, spleen, central nervous system, and skin.

Lymphomatoid Papulosis

Clinically benign, histologically malignant, recurrent cutaneous T-cell lymphoproliferative disorder characterized by an infiltration of large atypical cells surrounded by inflammatory cells. The atypical cells resemble REED-STERNBERG CELLS of HODGKIN DISEASE or the malignant cells of CUTANEOUS T-CELL LYMPHOMA. In some cases, lymphomatoid papulosis progresses to lymphomatous conditions including MYCOSIS FUNGOIDES; HODGKIN DISEASE; CUTANEOUS T-CELL LYMPHOMA; or ANAPLASTIC LARGE-CELL LYMPHOMA.