2027 ICD-10-CM Diagnosis Code Q82.4Ectodermal dysplasia (anhidrotic)
ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q82
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q82.4 is a billable ICD-10-CM diagnosis code for ectodermal dysplasia (anhidrotic). It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 606 through 607. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q82.4 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Other congenital malformations (Q80-Q89).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Acanthosis nigricans
- Ackerman syndrome
- Acrorenal field defect, ectodermal dysplasia, and lipoatrophic diabetes
- Alopecia, onychodysplasia, hypohidrosis, deafness ectodermal dysplasia
- Amelo-onycho-hypohidrotic syndrome
- Anhidrotic ectodermal dysplasia with immune deficiency
- Anhidrotic ectodermal dysplasia with immune deficiency due to IKBA gain of function mutation
- Anhidrotic ectodermal dysplasia with immune deficiency due to IKBKB GOF mutation
- Anhidrotic ectodermal dysplasia, immunodeficiency, osteopetrosis, lymphedema syndrome
- Anonychia
- Anonychia with bizarre flexural pigmentation
- Arthrogryposis and ectodermal dysplasia syndrome
- Autosomal dominant hypohidrotic ectodermal dysplasia syndrome
- Autosomal dominant ichthyosis
- Basan syndrome
- Berlin syndrome
- Blepharocheilodontic syndrome
- Book syndrome
- BRESEK syndrome
- Cerebellar ataxia and ectodermal dysplasia
- Congenital anomaly of macula
- Congenital hypoplasia of breast
- Congenital hypoplasia of nail unit
- Congenital hypotrichia
- Contracture with ectodermal dysplasia and orofacial cleft syndrome
- Cranioectodermal dysplasia
- Curly hair, ankyloblepharon, nail dysplasia syndrome
- Curry-Hall syndrome
- Cutaneous syndrome with ichthyosis
- Dermo-odonto dysplasia
- Dermotrichic syndrome
- Dominant autosomal hereditary disorder, incomplete penetrance
- Ectodermal dysplasia
- Ectodermal dysplasia and sensorineural deafness syndrome
- Ectodermal dysplasia syndactyly syndrome
- Ectodermal dysplasia trichoodontoonychial type
- Ectodermal dysplasia with blindness syndrome
- Ectodermal dysplasia with ectrodactyly and macular dystrophy syndrome
- Ectodermal dysplasia with hair-nail defect
- Ectodermal dysplasia with hair-tooth defects
- Ectodermal dysplasia with hair-tooth-nail defects
- Ectodermal dysplasia with hair-tooth-nail-sweating defect
- Ectodermal dysplasia with nail defect
- Ectodermal dysplasia with natal teeth Turnpenny type
- Ectodermal dysplasia with sweating defect
- Ectodermal dysplasia with tooth-nail defects
- Ectodermal dysplasia with tooth-nail-sweating defect
- Ectodermal dysplasia with tooth-sweating defect
- Ectodermal dysplasia, hyperhidrosis, cutaneous syndactyly syndrome
- Ectodermal dysplasia, intellectual disability, central nervous system malformation syndrome
- Ectodermal dysplasia, syndactyly and pili torti
- Ectodermal dysplasia-ocular malformation syndrome
- Ectodermal syndrome with hair-sweating defects
- Ectodermal syndrome with hair-tooth-sweating defects
- Focal facial dermal dysplasia
- Focal facial dermal dysplasia type I
- Focal facial dermal dysplasia type II
- Focal facial dermal dysplasia type III
- Focal facial dermal dysplasia type IV
- Fried's tooth and nail syndrome
- Greither type of ectodermal dysplasia
- Hay-Wells syndrome of ectodermal dysplasia
- Hypohidrosis
- Hypohidrosis-diabetes insipidus syndrome
- Hypohidrotic X-linked ectodermal dysplasia
- Johanson-Blizzard syndrome
- KID syndrome
- Kirman syndrome
- Lelis syndrome
- Limb mammary syndrome
- Linear hypopigmentation and craniofacial asymmetry with acral, ocular and brain anomalies
- Marshall syndrome
- Melanin pigmentation of oral mucosa
- Melanosis of mucosa of body orifice
- Nail and tooth abnormalities, marginal palmoplantar keratoderma, oral hyperpigmentation syndrome
- Neonatal tooth
- Oculoosteocutaneous syndrome
- Odonto onycho dysplasia with alopecia syndrome
- Odontomicronychial ectodermal dysplasia
- Odonto-onychial dysplasia with alopecia
- Odonto-onycho-dermal dysplasia
- Odonto-tricho-ungual-digito-palmar syndrome
- Onycho-tricho-dysplasia neutropenia syndrome
- Pilodental dysplasia, refractive errors syndrome
- Premature tooth eruption
- Robinson nail dystrophy-deafness syndrome
- Roselli-Gulienetti ectodermal dysplasia
- Sabinas brittle hair syndrome
- Salamon's syndrome
- Sandman-Andra syndrome
- Schinzel-Giedion syndrome
- Senter syndrome
- Tricho-dento-osseous syndrome
- Trichodermodysplasia and dental alterations syndrome
- Trichodysplasia with amelogenesis imperfecta syndrome
- Tricho-oculodermovertebral syndrome
- Trichoodontoonychial dysplasia
- Tricho-onychodental dysplasia
- Trichothiodystrophy
- Zlotogora Ogur syndrome
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q82.4: its own notes plus those printed at Q82 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
- Ellis-van Creveld syndrome (Q77.6)
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q82.4, its category, or a range that includes it.
Index to Diseases and InjuriesGuidance
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Ectodermal Dysplasia
a group of hereditary disorders involving tissues and structures derived from the embryonic ectoderm. they are characterized by the presence of abnormalities at birth and involvement of both the epidermis and skin appendages. they are generally nonprogressive and diffuse. various forms exist, including anhidrotic and hidrotic dysplasias, focal dermal hypoplasia, and aplasia cutis congenita.
Patient EducationClinical
Skin Conditions
Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:
The full article covers:
- What does your skin do?
- What problems and conditions can affect your skin?
- How can I keep my skin healthy?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q82.4 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q82.4Overview
What is the ICD-10 code for ectodermal dysplasia (anhidrotic)?
The ICD-10-CM code for ectodermal dysplasia (anhidrotic) is Q82.4 (sometimes written as Q824). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q82.4 (Other congenital malformations of skin) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report ectodermal dysplasia (anhidrotic) on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q82.4 group to?
When ectodermal dysplasia (anhidrotic) is the principal diagnosis on an inpatient stay, it groups to MS-DRG 607, 606, with relative weights from 0.8772 to 1.5721 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q82.4 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for ectodermal dysplasia (anhidrotic) on inpatient claims. The code appears in the Other congenital malformations (Q80-Q89) range of the CMS exempt list.
Can Q82.4 be reported with Q77.6?
Not as a rule. The Excludes1 note on Q82.4 lists "Ellis-van Creveld syndrome (Q77.6)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).
