2026 ICD-10-CM Diagnosis Code Q82.3Incontinentia pigmenti
ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q82
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q82.3 is a billable ICD-10-CM diagnosis code for incontinentia pigmenti. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 606 through 607. The code is exempt from POA reporting. Coders also document this condition as incontinentia pigmenti achromians syndrome. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q82.3 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Incontinentia pigmenti achromians syndrome
- Incontinentia pigmenti syndrome
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
- Bloch-Sulzberger disease or syndrome - Q82.3
- Incontinentia pigmenti - Q82.3
External Cause of Injuries IndexGuidance
References for this code in the External Cause of Injuries Index.
- Bloch-Sulzberger disease or syndrome
- Incontinentia pigmenti
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Incontinentia Pigmenti
a genodermatosis occurring mostly in females and characterized by skin changes in three phases - vesiculobullous, verrucous papillomatous, and macular melanodermic. hyperpigmentation is bizarre and irregular. sixty percent of patients have abnormalities of eyes, teeth, central nervous system, and skin appendages.Pigmentation Disorders
diseases affecting pigmentation, including skin pigmentation.
Patient EducationClinical
Skin Conditions
Your skin is your body's largest organ. It covers the entire outside of your body. There are many ways that your skin protects your body and helps keep you healthy. For example, it:
The full article covers:
- What does your skin do?
- What problems and conditions can affect your skin?
- How can I keep my skin healthy?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q82.3 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q82.3Overview
Is Q82.3 (Other congenital malformations of skin) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report incontinentia pigmenti on HIPAA-covered claims from October 1, 2025 through September 30, 2026.
What MS-DRG does Q82.3 group to?
When incontinentia pigmenti is the principal diagnosis on an inpatient stay, it groups to MS-DRG 606, 607, with relative weights from 0.9064 to 1.5132 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q82.3 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for incontinentia pigmenti on inpatient claims.
What is the ICD-9 equivalent of Q82.3?
Under the General Equivalence Mappings, incontinentia pigmenti converts to ICD-9-CM 757.33 (cong skin pigment anomal). The mapping is approximate, so confirm the match fits the documentation.
Footnotes
[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:
- The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
- The condition places limitations on self-care, independent living, and social interactions.
