2026 ICD-10-CM Diagnosis Code Q80.2Lamellar ichthyosis

ICD-10-CM Codes›Q00-Q99›Q80-Q89›Q80

ICD-10-CM Q80.2
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q80.2 is a billable ICD-10-CM diagnosis code for lamellar ichthyosis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 606 through 607. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Other specified and unspecified congenital anomalies.

Code Identity

ICD-10-CM Code
Q80.2
Billable Status
Yes — Valid for Submission
Code Describes
Lamellar ichthyosis
Short Description
Lamellar ichthyosis
Same as the full description in the CMS dataset.
Parent Code
Q80
Congenital ichthyosis

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ80-Q89Other congenital malformations
CategoryQ80Congenital ichthyosis
This CodeQ80.2Lamellar ichthyosis

Present on Admission (POA)Billing

Q80.2 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acral self-healing collodion baby
  • Autosomal dominant ichthyosis
  • Autosomal dominant lamellar ichthyosis
  • Congenital non bullous ichthyosiform erythroderma
  • Erythrodermic lamellar ichthyosis
  • Lamellar ichthyosis
  • Non-erythrodermic lamellar ichthyosis
  • Self-healing collodion baby

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Collodion baby

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Collodion baby
    • Ichthyosis(congenital)
      • lamellar

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL010
Other specified and unspecified congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • ABCA12 wt Allele|ABC12|ARCI4A|ARCI4B|ATP Binding Cassette Subfamily A Member 12 wt Allele|ATP-Binding Cassette, Sub-Family A (ABC1), Member 12 Gene|ATP-Binding Cassette, Subfamily A, Member 12 Gene|DKFZP434G232|ICR2B|Ichthyosis Congenita II, Lamellar Ichthyosis B Gene|LI2

    human abca12 wild-type allele is located in the vicinity of 2q35 and is approximately 207 kb in length. this allele, which encodes glucosylceramide transporter abca12 protein, plays a role in both the membrane localization of glucosylceramide and other lipids in lamellar granules and in cholesterol transport. mutation of the gene is associated with autosomal recessive congenital ichthyosis (arci) types 4a and 4b (harlequin).

  • Lamellar Ichthyosis

    a very rare, autosomal recessive inherited skin disorder present at birth. it is characterized by the presence of a transparent membrane encasing the newborn. this membrane sheds in about two weeks after birth to reveal generalized scaling and skin erythema.

Patient EducationClinical

Skin Conditions

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Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q80.2 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
757.1 Ichthyosis congenita
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q80.2Overview

Is Q80.2 (Congenital ichthyosis) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report lamellar ichthyosis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q80.2 group to?

When lamellar ichthyosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 606, 607, with relative weights from 0.9064 to 1.5132 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q80.2 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for lamellar ichthyosis on inpatient claims.

What is the ICD-9 equivalent of Q80.2?

Under the General Equivalence Mappings, lamellar ichthyosis converts to ICD-9-CM 757.1 (ichthyosis congenita). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.