2027 ICD-10-CM Diagnosis Code Q76.1Klippel-Feil syndrome
ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q76
- Billable — Valid for Submission
- POA Exempt
- Chronic Condition
Q76.1 is a billable ICD-10-CM diagnosis code for Klippel-Feil syndrome. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. Coders also document this condition as Klippel-Feil anomaly, myopathy, facial dysmorphism syndrome. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.
Code Identity
Code Classification
Present on Admission (POA)Billing
Q76.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations and deformations of the musculoskeletal system (Q65-Q79).
Approximate SynonymsGuidance
Alternate terms and clinical phrases that map to this code.
- Klippel-Feil anomaly, myopathy, facial dysmorphism syndrome
- Klippel-Feil sequence
Instructional NotesGuidance
Instructions from the official ICD-10-CM Tabular List that apply to Q76.1: its own notes plus those printed at Q76 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.
Applicable To
Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.
- Cervical fusion syndrome
Excludes1
Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.
Excludes2
Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.
Notes
General instructions on how these codes are used.
- Codes from this chapter are not for use on maternal records
Source: CMS ICD-10-CM Tabular List. How to read instructional notes.
Referenced in Other NotesGuidance
Instructional notes printed at other codes that name Q76.1, its category, or a range that includes it.
Excludes1 1
These codes carry an Excludes1 note naming Q76.1: they are not reported together with it, unless the two conditions are unrelated.
- M43 Other deforming dorsopathiesKlippel-Feil syndrome (Q76.1)
Excludes2 1
These codes carry an Excludes2 note naming Q76.1: its condition is not part of those codes, and both may be reported when the patient has both.
- Block Q10-Q18 Congenital malformations of eye, ear, face and neck
Index to Diseases and InjuriesGuidance
Alphabetical index entries that point to this code.
Cervical See Also: condition;
fusion syndrome Q76.1
Disease, diseased See Also: Syndrome;
Clinical ClassificationClinical
AHRQ’s CCSR groups this code into broader clinical categories.
Clinical InformationClinical
Klippel-Feil Syndrome
a syndrome characterised by a low hairline and a shortened neck resulting from a reduced number of vertebrae or the fusion of multiple hemivertebrae into one osseous mass.
Patient EducationClinical
Birth Defects
A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.
The full article covers:
- What are birth defects?
- What causes birth defects?
- Who is at risk of having a baby with birth defects?
- How are birth defects diagnosed?
- What are the treatments for birth defects?
- Can birth defects be prevented?
Read the full article at MedlinePlus
Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.
Convert Q76.1 to ICD-9-CMHistory
The closest ICD-9-CM equivalents under the General Equivalence Mappings.
Code HistoryHistory
Questions About Q76.1Overview
What is the ICD-10 code for Klippel-Feil syndrome?
The ICD-10-CM code for Klippel-Feil syndrome is Q76.1 (sometimes written as Q761). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
Is Q76.1 (Congenital malformations of spine and bony thorax) a billable code?
Yes. This is a billable ICD-10-CM code, specific enough to report Klippel-Feil syndrome on HIPAA-covered claims from October 1, 2026 through September 30, 2027.
What MS-DRG does Q76.1 group to?
When Klippel-Feil syndrome is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 566, 565, with relative weights from 0.7374 to 1.4909 depending on complications. Higher weights mean higher Medicare reimbursement.
Is Q76.1 exempt from POA reporting?
Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for Klippel-Feil syndrome on inpatient claims. The code appears in the Congenital malformations and deformations of the musculoskeletal system (Q65-Q79) range of the CMS exempt list.
What is the ICD-9 equivalent of Q76.1?
Under the General Equivalence Mappings, Klippel-Feil syndrome converts to ICD-9-CM 756.16 (klippel-feil syndrome). The mapping is a direct match.
