2026 ICD-10-CM Diagnosis Code Q75.1Craniofacial dysostosis

ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q75

ICD-10-CM Q75.1
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q75.1 is a billable ICD-10-CM diagnosis code for craniofacial dysostosis. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q75.1
Billable Status
Yes — Valid for Submission
Code Describes
Craniofacial dysostosis
Short Description
Craniofacial dysostosis
Same as the full description in the CMS dataset.
Parent Code
Q75
Other congenital malformations of skull and face bones

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategoryQ75Other congenital malformations of skull and face bones
This CodeQ75.1Craniofacial dysostosis

Present on Admission (POA)Billing

Q75.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acanthosis nigricans
  • Acrocraniofacial dysostosis
  • Acrofacial dysostosis Catania type
  • Acrofacial dysostosis Kennedy Teebi type
  • Acrofacial dysostosis Palagonia type
  • Acrofacial dysostosis Rodriguez type
  • Acrofrontofacionasal dysostosis
  • Acrofrontofacionasal dysostosis type 2
  • Congenital anomaly of nasal bone
  • Crouzon syndrome
  • Crouzon syndrome with acanthosis nigricans
  • Dysostosis of bone of skull
  • Fibroblast growth factor receptor 3-related craniosynostosis
  • Frontal dysostosis
  • Fronto-frontal dysostosis
  • Fronto-naso-ethmoidal dysostosis
  • Hypomandibular faciocranial dysostosis
  • Internasal dysostosis
  • Maxillary dysostosis
  • Maxillo-zygomatic dysostosis
  • Naso-maxillary dysostosis
  • Spheno-frontal dysostosis
  • Sphenoidal dysostosis
  • Temporo-aural dysostosis

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Crouzon's disease

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Crouzon's disease
    • Dysostosis
      • craniofacial

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Craniofacial Dysostosis

    autosomal dominant craniosynostosis with shallow orbits; exophthalmos; and maxillary hypoplasia.

  • Acanthosis Nigricans

    a circumscribed melanosis consisting of a brown-pigmented, velvety verrucosity or fine papillomatosis appearing in the axillae and other body folds. it occurs in association with endocrine disorders, underlying malignancy, administration of certain drugs, or as in inherited disorder.

  • Acanthosis Nigricans

    a melanotic cutaneous lesion that develops in the axilla and other body folds. it may be idiopathic, drug-induced, or it may be associated with the presence of an endocrine disorder or malignancy.

  • Hyperandrogenism, Insulin Resistance, Acanthosis Nigricans Syndrome|HAIR-AN Syndrome

    a condition characterized by hyperandrogenism, insulin resistance, and acanthosis nigricans, typically associated with obesity in teenage girls. it is considered to be a subtype of polycystic ovarian syndrome, but may occur in male individuals. etiology is unclear, but some cases may be associated with mutations affecting the tyrosine kinase domain of the insulin receptor.

  • Insulin Resistant Diabetes Mellitus with Acanthosis Nigricans and Hyperandrogenism|Type A Insulin Resistance Syndrome

    a syndrome of insulin resistance caused by mutation(s) in the insr gene, encoding the insulin receptor. this condition is characterized by a clinical triad of hyperinsulinemia, acanthosis nigricans, and hyperandrogenism without lipodystrophy. this is the least severe of a spectrum of disorders; the other two conditions are rabson-mendenhall syndrome and donohoe syndrome.

Patient EducationClinical

Craniofacial Abnormalities

Craniofacial is a medical term that relates to the bones of the skull and face. Craniofacial abnormalities are birth defects of the face or head. Some, like cleft lip and palate, are among the most common of all birth defects. Others are very rare. Most of them affect how a person's face or head looks.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q75.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
756.0 Anomal skull/face bones
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q75.1Overview

Is Q75.1 (Other congenital malformations of skull and face bones) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report craniofacial dysostosis on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q75.1 group to?

When craniofacial dysostosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 565, 566, with relative weights from 0.7493 to 1.5436 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q75.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for craniofacial dysostosis on inpatient claims.

What is the ICD-9 equivalent of Q75.1?

Under the General Equivalence Mappings, craniofacial dysostosis converts to ICD-9-CM 756.0 (anomal skull/face bones). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.