2027 ICD-10-CM Diagnosis Code Q75.1Craniofacial dysostosis

ICD-10-CM Codes›Q00-Q99›Q65-Q79›Q75

ICD-10-CM Q75.1
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q75.1 is a billable ICD-10-CM diagnosis code for craniofacial dysostosis. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 564 through 566. The code is exempt from POA reporting. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Musculoskeletal congenital conditions.

Code Identity

ICD-10-CM Code
Q75.1
Billable Status
Yes — Valid for Submission
Code Describes
Craniofacial dysostosis
Short Description
Craniofacial dysostosis
Same as the full description in the CMS dataset.
Parent Code
Q75
Other congenital malformations of skull and face bones

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ65-Q79Congenital malformations and deformations of the musculoskeletal system
CategoryQ75Other congenital malformations of skull and face bones
This CodeQ75.1Craniofacial dysostosis

Present on Admission (POA)Billing

Q75.1 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations and deformations of the musculoskeletal system (Q65-Q79).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Acanthosis nigricans
  • Acrocraniofacial dysostosis
  • Acrofacial dysostosis Catania type
  • Acrofacial dysostosis Kennedy Teebi type
  • Acrofacial dysostosis Palagonia type
  • Acrofacial dysostosis Rodriguez type
  • Acrofrontofacionasal dysostosis
  • Acrofrontofacionasal dysostosis type 2
  • Congenital anomaly of nasal bone
  • Crouzon syndrome
  • Crouzon syndrome with acanthosis nigricans
  • Dysostosis of bone of skull
  • Fibroblast growth factor receptor 3-related craniosynostosis
  • Frontal dysostosis
  • Fronto-frontal dysostosis
  • Fronto-naso-ethmoidal dysostosis
  • Hypomandibular faciocranial dysostosis
  • Internasal dysostosis
  • Maxillary dysostosis
  • Maxillo-zygomatic dysostosis
  • Naso-maxillary dysostosis
  • Spheno-frontal dysostosis
  • Sphenoidal dysostosis
  • Temporo-aural dysostosis

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q75.1: its own notes plus those printed at Q75 and Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Applicable To

Conditions this code is used for: synonyms of the title or, for "other specified" codes, the conditions assigned to it. The list is not exhaustive.

  • Crouzon's disease

Excludes1

Not coded here: the excluded code is never reported together with this one, unless the two conditions are unrelated.

From Q75 Other congenital malformations of skull and face bones applies to 22 codes
  • congenital malformation of face NOS (Q18.-)
  • congenital malformation syndromes classified to Q87.-
  • dentofacial anomalies [including malocclusion] (M26.-)
  • musculoskeletal deformities of head and face (Q67.0-Q67.4)
  • skull defects associated with congenital anomalies of brain such as:
  • anencephaly (Q00.0)
  • encephalocele (Q01.-)
  • hydrocephalus (Q03.-)
  • microcephaly (Q02)

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Referenced in Other NotesGuidance

Instructional notes printed at other codes that name Q75.1, its category, or a range that includes it.

Excludes1 1

These codes carry an Excludes1 note naming Q75.1: they are not reported together with it, unless the two conditions are unrelated.

  • Q18 Other congenital malformations of face and neck
    congenital malformations of skull and face bones (Q75.-) names Q75.-, which includes this code

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL008
Musculoskeletal congenital conditions
Default principal diagnosis: inpatient Yes · outpatient Yes

Clinical InformationClinical

  • Craniofacial Dysostosis

    autosomal dominant craniosynostosis with shallow orbits; exophthalmos; and maxillary hypoplasia.

Patient EducationClinical

Craniofacial Abnormalities

Craniofacial is a medical term that relates to the bones of the skull and face. Craniofacial abnormalities are birth defects of the face or head. Some, like cleft lip and palate, are among the most common of all birth defects. Others are very rare. Most of them affect how a person's face or head looks.

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q75.1 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
756.0 Anomal skull/face bones
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q75.1Overview

What is the ICD-10 code for craniofacial dysostosis?

The ICD-10-CM code for craniofacial dysostosis is Q75.1 (sometimes written as Q751). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q75.1 (Other congenital malformations of skull and face bones) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report craniofacial dysostosis on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q75.1 group to?

When craniofacial dysostosis is the principal diagnosis on an inpatient stay, it groups to MS-DRG 564, 566, 565, with relative weights from 0.7374 to 1.4909 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q75.1 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for craniofacial dysostosis on inpatient claims. The code appears in the Congenital malformations and deformations of the musculoskeletal system (Q65-Q79) range of the CMS exempt list.

Can Q75.1 be reported with a code from Q18?

Not as a rule. The Excludes1 note at Q75, which applies to Q75.1, lists "congenital malformation of face NOS (Q18.-)". An Excludes1 note means the excluded code is never reported together with this one; the only exception is when the two conditions are unrelated to each other (Official Guidelines, Section I.A.12.a).