2026 ICD-10-CM Diagnosis Code Q64.9Congenital malformation of urinary system, unspecified

ICD-10-CM Codes›Q00-Q99›Q60-Q64›Q64

ICD-10-CM Q64.9
CMSSource: CMS FY 2026 ICD-10-CM dataset · Effective Oct 1, 2025 – Sep 30, 2026

Q64.9 is a billable ICD-10-CM diagnosis code for congenital malformation of urinary system, unspecified. It is valid on HIPAA claims for fiscal year 2026 (October 1, 2025 through September 30, 2026) and groups to MS-DRG 698 through 700. The code is exempt from POA reporting. Coders also document this condition as anal atresia. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q64.9
Billable Status
Yes — Valid for Submission
Code Describes
Congenital malformation of urinary system, unspecified
Short Description
Congenital malformation of urinary system, unspecified
Same as the full description in the CMS dataset.
Parent Code
Q64
Other congenital malformations of urinary system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ60-Q64Congenital malformations of the urinary system
CategoryQ64Other congenital malformations of urinary system
This CodeQ64.9Congenital malformation of urinary system, unspecified

Present on Admission (POA)Billing

Q64.9 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review other POA exempt codes.

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Anal atresia
  • Cardiac urogenital syndrome
  • Congenital anomaly of male urogenital tract
  • Congenital anomaly of the urinary tract proper
  • Congenital female urogenital anomaly
  • Congenital malformation of the urinary system
  • Cutis laxa with severe pulmonary, gastrointestinal and urinary anomalies
  • Cutis laxa, autosomal recessive
  • Karandikar Maria Kamble syndrome
  • Nephrosis, deafness, urinary tract, digital malformation syndrome

Tabular List NotesGuidance

Coding notes and annotation back-references applicable to this code.

Inclusion Terms

  • Congenital anomaly NOS of urinary system
  • Congenital deformity NOS of urinary system

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

External Cause of Injuries IndexGuidance

References for this code in the External Cause of Injuries Index.

    • Anomaly, anomalous(congenital) (unspecified type)
      • urinary tract
    • Deformity
      • urinary tract (congenital)
    • Malformation(congenital)
      • urinary system

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q64.9 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
753.9 Urinary anomaly NOS
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2025No changes
FY 2026CurrentCurrent code set, no changesEffective October 1, 2025 through September 30, 2026.

Questions About Q64.9Overview

Is Q64.9 (Other congenital malformations of urinary system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital malformation of urinary system, unspecified on HIPAA-covered claims from October 1, 2025 through September 30, 2026.

What MS-DRG does Q64.9 group to?

When congenital malformation of urinary system, unspecified is the principal diagnosis on an inpatient stay, it groups to MS-DRG 698, 699, 700, with relative weights from 0.6899 to 1.6544 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q64.9 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital malformation of urinary system, unspecified on inpatient claims.

What is the ICD-9 equivalent of Q64.9?

Under the General Equivalence Mappings, congenital malformation of urinary system, unspecified converts to ICD-9-CM 753.9 (urinary anomaly NOS). The mapping is approximate, so confirm the match fits the documentation.

Footnotes

[1] Chronic - a chronic condition code indicates a condition lasting 12 months or longer and its effect on the patient based on one or both of the following criteria:

  • The condition results in the need for ongoing intervention with medical products,treatment, services, and special equipment
  • The condition places limitations on self-care, independent living, and social interactions.