2027 ICD-10-CM Diagnosis Code Q64.5Congenital absence of bladder and urethra

ICD-10-CM Codes›Q00-Q99›Q60-Q64›Q64

ICD-10-CM Q64.5
CMSSource: CMS FY 2027 ICD-10-CM dataset · Effective Oct 1, 2026 – Sep 30, 2027

Q64.5 is a billable ICD-10-CM diagnosis code for congenital absence of bladder and urethra. It is valid on HIPAA claims for fiscal year 2027 (October 1, 2026 through September 30, 2027) and groups to MS-DRG 698 through 700. The code is exempt from POA reporting. Coders also document this condition as agenesis of urinary bladder. In AHRQ's Clinical Classifications Software (CCSR), this diagnosis falls under Genitourinary congenital anomalies.

Code Identity

ICD-10-CM Code
Q64.5
Billable Status
Yes — Valid for Submission
Code Describes
Congenital absence of bladder and urethra
Short Description
Congenital absence of bladder and urethra
Same as the full description in the CMS dataset.
Parent Code
Q64
Other congenital malformations of urinary system

Code Classification

ChapterQ00-Q99Congenital malformations, deformations and chromosomal abnormalities
SectionQ60-Q64Congenital malformations of the urinary system
CategoryQ64Other congenital malformations of urinary system
This CodeQ64.5Congenital absence of bladder and urethra

Present on Admission (POA)Billing

Q64.5 is exempt from POA reporting on inpatient claims to general acute care hospitals. Review the other POA exempt codes in Congenital malformations of the urinary system (Q60-Q64).

Approximate SynonymsGuidance

Alternate terms and clinical phrases that map to this code.

  • Agenesis of urinary bladder
  • Aplasia of urinary bladder
  • Congenital absence of urethra
  • Congenital absence of urinary bladder
  • Congenital absence of urinary bladder and urethra
  • Congenital malformation of urinary bladder and urethra
  • Urinary bladder absent

Instructional NotesGuidance

Instructions from the official ICD-10-CM Tabular List that apply to Q64.5: its own notes plus those printed at Chapter 17. A note printed at a category, block or chapter applies to every code under it.

Excludes2

Not included here: the excluded condition is not part of this code, but a patient may have both, so both codes may be reported.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • inborn errors of metabolism (E70-E88)

Notes

General instructions on how these codes are used.

From Chapter 17 (Q00-QA1) Congenital malformations, deformations and chromosomal abnormalities applies to 900 codes
  • Codes from this chapter are not for use on maternal records

Source: CMS ICD-10-CM Tabular List. How to read instructional notes.

Index to Diseases and InjuriesGuidance

Alphabetical index entries that point to this code.

Clinical ClassificationClinical

AHRQ’s CCSR groups this code into broader clinical categories.

CCSR MAL003
Genitourinary congenital anomalies
Default principal diagnosis: inpatient Yes · outpatient Yes

Patient EducationClinical

Birth Defects

A birth defect is a problem that happens while a baby is developing in the mother's body. Most birth defects happen during the first 3 months of pregnancy. One out of every 33 babies in the United States is born with a birth defect.

The full article covers:

  • What are birth defects?
  • What causes birth defects?
  • Who is at risk of having a baby with birth defects?
  • How are birth defects diagnosed?
  • What are the treatments for birth defects?
  • Can birth defects be prevented?

Read the full article at MedlinePlus

Courtesy of MedlinePlus, a service of the U.S. National Library of Medicine.

Convert Q64.5 to ICD-9-CMHistory

The closest ICD-9-CM equivalents under the General Equivalence Mappings.

ICD-9-CM
753.8 Cystourethral anom NEC
Approximate The match is approximate rather than exact.

Code HistoryHistory

FY 2016AddedAdded to the ICD-10-CM code setEffective October 1, 2015, the first year of ICD-10-CM.
FY 2017–2026No changes
FY 2027CurrentCurrent code set, no changesEffective October 1, 2026 through September 30, 2027.

Questions About Q64.5Overview

What is the ICD-10 code for congenital absence of bladder and urethra?

The ICD-10-CM code for congenital absence of bladder and urethra is Q64.5 (sometimes written as Q645). It is billable on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

Is Q64.5 (Other congenital malformations of urinary system) a billable code?

Yes. This is a billable ICD-10-CM code, specific enough to report congenital absence of bladder and urethra on HIPAA-covered claims from October 1, 2026 through September 30, 2027.

What MS-DRG does Q64.5 group to?

When congenital absence of bladder and urethra is the principal diagnosis on an inpatient stay, it groups to MS-DRG 699, 698, 700, with relative weights from 0.6740 to 1.6400 depending on complications. Higher weights mean higher Medicare reimbursement.

Is Q64.5 exempt from POA reporting?

Yes. CMS lists this code among those exempt from present on admission reporting, so hospitals do not assign a POA indicator for congenital absence of bladder and urethra on inpatient claims. The code appears in the Congenital malformations of the urinary system (Q60-Q64) range of the CMS exempt list.

What is the ICD-9 equivalent of Q64.5?

Under the General Equivalence Mappings, congenital absence of bladder and urethra converts to ICD-9-CM 753.8 (cystourethral anom NEC). The mapping is approximate, so confirm the match fits the documentation.